Results 111 to 120 of about 85,651 (308)
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective To delineate specific in vivo white matter pathology in neuronal intranuclear inclusion disease (NIID) using diffusion spectrum imaging (DSI) and define its clinical relevance. Methods DSI was performed on 42 NIID patients and 38 matched controls.
Kaiyan Jiang +10 more
wiley +1 more source
166 kW Liquid-Insulated Medium-Frequency Transformer With Hybrid Foil-Litz Windings
IEEE Open Journal of Power ElectronicsThe safe operation of high-power solid-state transformers (SSTs) in medium-voltage grid-connected applications relies on medium-frequency transformers (MFTs).
Andrea Cremasco +4 more
doaj +1 more source
Energies, 2018 Solid State Transformers (SST) are attracting considerable attention due to their great application potential in future smart grids. It is an essential technology capable of promoting the modernization of the electric power distribution system and it is ...
Welbert A. Rodrigues +3 more
doaj +1 more source
Value of MRI Outcomes for Preventive and Early‐Stage Trials in Spinocerebellar Ataxias 1 and 3
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective To examine the value of MRI outcomes as endpoints for preventive and early‐stage trials of two polyglutamine spinocerebellar ataxias (SCAs). Methods A cohort of 100 participants (23 SCA1, 63 SCA3, median Scale for the Assessment and Rating of Ataxia (SARA) score = 5, 42% preataxic, and 14 gene‐negative controls) was scanned at 3T up ...
Thiago J. R. Rezende +26 more
wiley +1 more source
, 2013 The partial discharge (PD) process in liquid dielectrics is influenced by several factors. Although the PD current contains the information representing the discharge process during the PD event, it is difficult to determine the detailed dynamics of what
Chilong Jiang +6 more
core +2 more sources
Solid state phase transformation kinetics
, 2001 Solid state phase transformations determine the microstructure, and thus the material properties in many materials of technological interest. Industrial adjustment of material properties by controlling phase transformations is mainly achieved empirically.
openaire +2 more sources
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective Onasemnogene abeparvovec (OA) is an AAV9‐based gene therapy for spinal muscular atrophy type I (SMA I). Real‐world outcomes show increased response variability compared to clinical trials, and follow‐up data beyond 12–18 months are limited.
Marika Pane +43 more
wiley +1 more source
Variable electrostatic transformer: controllable coupling of two charge qubits
, 2003 We propose and investigate a novel method for the controlled coupling of two Josephson charge qubits by means of a variable electrostatic transformer. The value of the coupling capacitance is given by the discretized curvature of the lowest energy band ...
C. Bruder +4 more
core +1 more source
CSF Monoamine Metabolites and Cognitive Trajectory in Early Parkinson's Disease
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Background Imaging and postmortem studies indicate that abnormalities in monoaminergic neurotransmission contribute to cognitive impairment in Parkinson's disease (PD). However, it remains uncertain if cerebrospinal fluid (CSF) monoamine metabolites can serve as biomarkers of cognitive decline in early PD.
Jing‐Yu Shao +7 more
wiley +1 more source
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Background X‐linked adrenoleukodystrophy (X‐ALD) is a neurometabolic disorder caused by pathogenic variants in ABCD1, leading to slowly progressive spinal cord disease in nearly all affected men. Sensitive biomarkers to quantify disease severity and predict progression are needed for clinical care and trial design.
Eda G. Kabak +4 more
wiley +1 more source