Results 121 to 130 of about 516,930 (293)

Super‐Refractory Status Epilepticus (SRSE) in a Patient With Compound Heterozygous OPA1 Variants: Case Report and Literature Review

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Super‐Refractory Status Epilepticus (SRSE) is a rare, life‐threatening neurological emergency with unclear etiology in many cases. Mitochondrial dysfunction, often due to disease‐causing genetic variants, is increasingly recognized as a cause, with each gene producing distinct pathophysiological mechanisms.
Pouria Mohammadi, Lara Basovic, Christopher Michael McGraw   +2 more
wiley   +1 more source

Input-to-state stability of nonlinear systems with delayed impulse based on event-triggered impulse control

AIMS Mathematics
This paper investigates input-to-state stability (ISS) of nonlinear systems with delayed impulse under event-triggered impulse control, where external inputs are different in continuous and impulse dynamics.
Linni Li, Jin-E Zhang
doaj   +1 more source

Predicting Loss of Ambulation in Limb Girdle Muscular Dystrophy R9

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Background Limb girdle muscular dystrophy type R9 (LGMDR9) results from biallelic variants in FKRP. There is limited data to predict loss of ambulation (LOA) among those with LGMDR9. Methods Participants in an ongoing dystroglycanopathy natural history study (NCT00313677) with FKRP variants who had achieved ambulation and were more than 3 ...
Chandra L. Miller, Lauren N. Coffey, Shelley R. H. Mockler, Katie M. Laubscher, Carrie M. Stephan, M. Bridget Zimmerman, Katherine D. Mathews   +6 more
wiley   +1 more source

Applying an Ethical Lens to the Treatment of People With Multiple Sclerosis

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT The practice of neurology requires an understanding of clinical ethics for decision‐making. In multiple sclerosis (MS) care, there are a wide range of ethical considerations that may arise. These involve shared decision‐making around selection of a disease‐modifying therapy (DMT), risks and benefits of well‐studied medications in comparison to
Methma Udawatta, Farrah J. Mateen
wiley   +1 more source

Scramjet sidewall burning: Preliminary shock tunnel results [PDF]

Experiments performed with a two dimensional model scramjet with particular emphasis on the effect of fuel injection from a wall are reported. Air low with a nominal Mach number of 3.5 and varied enthalpies was produced.
Morgan, R. G., Morris, N., Paull, A., Stalker, R. J.   +3 more
core   +1 more source

Characterization of Clinical Phenotype to Glial Fibrillary Acidic Protein Concentrations in Alexander Disease

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective To determine the concentration of glial fibrillary acidic protein (GFAP) in cerebrospinal fluid (CSF) and plasma in Alexander disease (AxD) and whether GFAP levels are predictive of disease phenotypes. Methods CSF and plasma were collected (longitudinally when available) from AxD participants and non‐AxD controls.
Amy T. Waldman, Asako Takanohashi, Joshua Y. Joung, Geraldine W. Liu, Kaley Arnold, Amy Pizzino, Walter Faig, Sarah Woidill, Sona Narula, Adeline L. Vanderver   +9 more
wiley   +1 more source

Ultrasonic regeneration of activated carbon with the addition of gas flushing

Desalination and Water Treatment
In this study, we investigated the effects of four operating parameters; frequency, power, gas impulse intensity, and regeneration time, on the regeneration of activated carbon.
Zhiwei Wang, Bingjie Zhou, Zhendong Liu, Lu Li, Kemei Zhou, Tian Tian, Binbin Wu, Wanting Feng, Yuanxiang Shan, Hongqin Xue, Zheng Wang   +10 more
doaj   +1 more source

Clinically Relevant Outcome Measures in Women With Adrenoleukodystrophy

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Adrenoleukodystrophy is a rare inherited peroxisomal disease caused by pathogenic variants in the ABCD1 gene located on the X chromosome. Although the most severe central nervous system and adrenal complications typically affect only men with adrenoleukodystrophy, the majority of women develop myeloneuropathy symptoms in adulthood.
Chenwei Yan, Elizabeth I. Pierpont, Amena S. Fine, Reena V. Kartha   +3 more
wiley   +1 more source

High-power hydrogen arcjet performance [PDF]

A hydrogen arcjet was operated at power levels ranging from 5 to 30 kW with three different nozzle geometries. Test results using all three nozzle geometries are reported and include variations of specific impulse with flow rate, and thrust with power ...
Curran, Francis M., Haag, Thomas W.
core   +1 more source

Ring-cusp ion thruster with shell anode [PDF]

, 1984
An improved ion thruster for low specific impulse operation in the 1500 sec to 6000 sec range has a multicusp boundary field provided by high strength magnets on an iron anode shell which lengthens the paths of electrons from a hollow cathode assembly. A
Rawlin, V. K., Roman, R. F., Sovey, J. S.   +2 more
core   +1 more source