Results 121 to 130 of about 1,254,731 (295)

SPG4 and Dementia: Expanding the Clinical Spectrum

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Hereditary spastic paraplegia (HSP) is a group of disorders characterized by progressive spasticity and lower limb weakness, with mutations in SPG4/SPAST being the most common cause. Detailed studies and clinical and molecular comparisons across different populations are missing.
Emanuele Panza, Arun Meyyazhagan, Eliseo Picchi, Gustavo Ribas, Ingrid Faber, Ryosuke Miyamoto, Preethi Basavaraju, Paolo Eusebi, Haripriya Kuchi Bhotla, Mario Stasi, Fabrizio Gaudiello, Francesco Patti, Filippo Maria Santorelli, Marcondes Cavalcante França Jr, José Luiz Pedroso, Orlando Graziani Povoas Barsottini, Hélio Afonso Ghizoni Teive, Peter Henry St George‐Hyslop, Toshitaka Kawarai, Antonio Orlacchio   +19 more
wiley   +1 more source

The structural architecture of international industry networks in the global economy. [PDF]

PLoS One, 2021
Sigler T, Martinus K, Iacopini I, Derudder B, Loginova J.   +4 more
europepmc   +1 more source

Seismic vulnerability of Modern Architecture building's: Le Corbusier style: a case study [PDF]

, 2005
In Portugal, at the end of the World War II, a new generation of architects emerged, influenced by the Modern Movement Architecture, born in Central-Europe in the early twenties but now influenced also by the Modern Brazilian Architecture. They worked
Costa, A., Fonseca, J., Rodrigues, H., Tostões, A., Varum, H.   +4 more
core   +1 more source

Characterization of Defect Distribution in an Additively Manufactured AlSi10Mg as a Function of Processing Parameters and Correlations with Extreme Value Statistics

Advanced Engineering Materials, EarlyView.
Predicting extreme defects in additive manufacturing remains a key challenge limiting its structural reliability. This study proposes a statistical framework that integrates Extreme Value Theory with advanced process indicators to explore defect–process relationships and improve the estimation of critical defect sizes. The approach provides a basis for
Muhammad Muteeb Butt, Varma Kvvssn, Hossein Laieghi, Zia Uddin, Peyman Ansari, E. Kıvanç Sadak, Can Barış Toprak, Hüseyin Kızıl, Enrico Salvati   +8 more
wiley   +1 more source

The l,d-Transpeptidase Ldt_Ab from Acinetobacter baumannii Is Poorly Inhibited by Carbapenems and Has a Unique Structural Architecture. [PDF]

ACS Infect Dis, 2022
Toth M, Stewart NK, Smith CA, Lee M, Vakulenko SB.   +4 more
europepmc   +1 more source

Seven Pillars of Wisdom [PDF]

The persistence of financial instability calls into question the adequacy of the current regulatory regime. A critical review of the three pillars at the core of current financial regulation exposes some structural flaws.
Giovanni Barone-Adesi
core  

A Concept of a Digital and Traceable Manufacturing Documentation Based on Formalized Process Description Applied on Composite Aircraft Moveable

Advanced Engineering Materials, EarlyView.
The documentation of component manufacture has become an essential part of today's production processes, especially for the analysis and optimization of production or component design with regard to structural performance, economic efficiency, and sustainability.
Björn Denker, Dominik Delisle, Christian Krombholz, Martin Rädel, Frank Dressel   +4 more
wiley   +1 more source

Harnessing Fungal Biowelding for Constructing Mycelium‐Engineered Materials

Advanced Engineering Materials, EarlyView.
Mycelium‐bound composites (MBCs) offer low‐carbon alternatives for construction, yet interfacial bonding remains a critical challenge. This review examines fungal biowelding as a biocompatible adhesive, elucidating mycelium‐mediated interfacial mechanisms and their role in material assembly. Strategies to optimize biowelding are discussed, highlighting
Xue Brenda Bai, Xinrui Sarah Niu, Zhao Qin   +2 more
wiley   +1 more source

Structural architecture of the Middle Niger Basin, Nigeria based on aeromagnetic data: An example of a non-volcanic basin. [PDF]

Heliyon, 2021
Salawu NB, Dada SS, Fatoba JO, Ojo OJ, Adebiyi LS, Sunday AJ, Abdulraheem TY.   +6 more
europepmc   +1 more source

Optimization Alternatives of Information Systems for Risk Management [PDF]

The focus of this article lies on synthesizing the requirements a risk management information system should meet in order to ensure an efficient risk management within a company, but also on presenting the architecture of the information system proposed ...
Iulia APOSTOL-MAURER
core