Long-term surgical outcomes of congenital supravalvular aortic stenosis: a systematic review, meta-analysis and microsimulation study. [PDF]
OBJECTIVES: Congenital supravalvular aortic stenosis (SVAS) is a rare form of congenital outflow tract obstruction and long-term outcomes are scarcely reported. This study aims to provide an overview of outcomes after surgical repair for congenital SVAS.
Meccanici F+9 more
europepmc +4 more sources
A 3D scaling law for supravalvular aortic stenosis suited for stethoscopic auscultations [PDF]
In this study a frequency scaling law for 3D anatomically representative supravalvular aortic stenosis (SVAS) cases is proposed. The law is uncovered for stethoscopy's preferred auscultation range (70-120 Hz).
Ahmed M. Ali+4 more
doaj +3 more sources
Clinical Results of a Modified Doty's Technique for Supravalvular Aortic Stenosis. [PDF]
This study aimed to assess the early and mid-term results of the modified Doty’s technique compared with the traditional Doty’s technique in patients with congenital supravalvular aortic stenosis (SVAS).
Lv L+5 more
europepmc +4 more sources
H-repair in supravalvular aortic stenosis. [PDF]
Luo S, Haller C, Deng MX, Honjo O.
europepmc +6 more sources
A successful surgical repair for supravalvular aortic stenosis with a bicuspid valve and malpositioned coronary orifices by partial Brom's technique: a case report. [PDF]
Background Supravalvular aortic stenosis (SVAS) is a relatively rare form of left ventricular outflow tract obstruction, often accompanied by other cardiac conditions.
Hara M+4 more
europepmc +3 more sources
Coronary artery lesions are associated with adverse cardiac events in children undergoing supravalvular aortic stenosis repair. [PDF]
OBJECTIVES The aim of this study was to identify the prevalence and anatomic characteristics of coronary artery lesions and their associated postoperative risk in patients undergoing supravalvular aortic stenosis repair.
Luo S+5 more
europepmc +4 more sources
We report an extremely rare case of Williams–Beuren (WB) syndrome in a 10-year-old boy with supravalvular aortic stenosis (SVAS) secondary to a large fibrocalcific eccentric shelf in the ascending aorta with fibrocalcific severe supravalvular pulmonary ...
Debasish Das+5 more
doaj +2 more sources
Anesthetic considerations in supravalvular aortic stenosis: A case series
Supravalvular aortic stenosis (SVAS), characterized by elastin arteriopathy, presents either as a localized narrowing at the sinotubular junction or as a diffuse form with additional involvement of the ascending aorta, aortic arch, and its branches ...
Virendra Kumar +3 more
doaj +2 more sources
Supravalvular aortic stenosis in William′s syndrome
We report supravalvular aortic stenosis in a 12 year old patient who presented with mental retardation, malformed teeth, broad lower lips, pectus carinatum, clinodactyly, kyphoscoliosis with symptoms of shortness of breath.
Bishav Mohan, Chander Mohan Mittal
doaj +4 more sources
Familial hypercholesterolemia supravalvular aortic stenosis and extensive atherosclerosis [PDF]
Familial hypercholesterolemia is an autosomally dominant disorder caused by various mutations in low-density lipoprotein receptor genes. This can lead to premature coronary atherosclerosis and cardiac-related death.
Rajpal Prajapati, Vikas Agrawal
doaj +2 more sources