Results 31 to 40 of about 3,525 (192)
Supravalvular Aortic Stenosis [PDF]
Circulation, 1958 A case of supravalvular aortic stenosis is described. The diagnosis was suspected from pressure curves obtained at retrograde catheterization of the left ventricle. At operation a circular narrowing of the aorta 2 cm. above the valvular ring was seen. No attempt at surgical correction was made; the patient died at the end of the operation.
J J, DENIE, A P, VERHEUGT
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Research in Cardiovascular Medicine, 2022 We report an extremely rare case of Williams–Beuren (WB) syndrome in a 10-year-old boy with supravalvular aortic stenosis (SVAS) secondary to a large fibrocalcific eccentric shelf in the ascending aorta with fibrocalcific severe supravalvular pulmonary ...
Debasish Das +5 more
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Isolated Diffuse Supravalvular Aortic Stenosis with Severe Aortic Narrowing in a 41-Year-Old Man. [PDF]
Tex Heart Inst J, 2017 Namana V +4 more
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Incomplete Shone’s Complex with BAV and VSD in Adult Diagnosed by Echocardiography [PDF]
Advanced Ultrasound in Diagnosis and Therapy, 2021 : The Shone’s complex, defined as a constellation of parachute mitral valve (PMV), supravalvular ring of the left atrium, subaortic stenosis, and aorta coarctation, is a rare entity, which more commonly occurs in its incomplete form.
Yichen Qu, MD, Ya Yang, MD, Jinjie Xie, MD, Rongjuan Li, MD, Han Zhang, MD, Li Song, MD, Yueli Wang, MD, Jing Li, MD
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Supravalvular Aortic Stenosis [PDF]
Circulation: Cardiovascular Genetics, 2012 Supravalvular aortic stenosis is a systemic elastin (ELN) arteriopathy that disproportionately affects the supravalvular aorta. ELN arteriopathy may be present in a nonsyndromic condition or in syndromic conditions such as Williams–Beuren syndrome.
Giuseppe, Merla +4 more
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Annals of Pediatric Cardiology, 2022 Bicuspid aortic valve (BAV) is the most common congenital cardiac defect, commonly associated with valve dysfunction and coarctation of aorta. Rarely, BAV can be associated with abnormalities of the coronary arteries, the most common of which are ectopic
Amad Chohan +6 more
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Annals of Cardiac Anaesthesia, 2023 Williams-Beuren syndrome is a rare genetic malformation with predilection for supravalvular aortic stenosis. Apart from cardiovascular malformation, hypocalcemia, developmental delay, and elfin facies, challenging airway make perioperative management ...
Devishree Das, Neeti Makhija
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Successful percutaneous balloon dilatation of supravalvular aortic membrane
Heart Views, 2019 Supravalvular aortic stenosis is the least common type of left ventricular outflow tract obstruction. Primary balloon dilatation of membranous supravalvular aortic stenosis was performed in a 10-year-old male child with a remarkable reduction in systolic
Gurkirat Singh +3 more
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Annals of Vascular Surgery - Brief Reports and Innovations, 2022 Objective: This case highlights the clinical consequences of elastin (ELN) arteriopathy, which affects the supravalvular aorta, the branches of the arch and pulmonary arterial branches.
Pradeep Pravinkumar Mistry +5 more
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Arquivos Brasileiros de Cardiologia, 2003 OBJECTIVE: To evaluate the cardiovascular findings and clinical follow-up of patients with Williams-Beuren syndrome. METHODS: We studied 20 patients (11 males, mean age at diagnosis: 5.9 years old), assessed for cardiovascular abnormalities with ...
Sofia Mizuho Miura Sugayama +8 more
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