Results 91 to 100 of about 6,792 (211)
Efficacy of low-dose Bevacizumab in Hereditary Hemorrhagic Telangiectasia
not ...
Lastella P. +5 more
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BACKGROUND: Hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber disease) is an autosomal dominant vascular disorder characterized by severe and recurrent nosebleeds, muco-cutaneous telangiectasias, and, in some cases, life-threatening visceral ...
Porcellini A +12 more
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of Definite hereditary hemorrhagic telangiectasia in a 60-year-old black Kenyan woman: a case report
of Definite hereditary hemorrhagic telangiectasia in a 60-year-old black Kenyan woman: a case ...
Cornelius Koech (3491222) +3 more
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Hereditary Hemorrhagic Telangiectasia - a literature review
Introduction and purpose: Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome, is a rare and complex vascular disorder characterized by abnormal blood vessel formation.
Marcel Stodolak +10 more
doaj +1 more source
Hereditary hemorrhagic telangiectasia: diagnosis and management from the hematologist’s perspective
Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome, is an autosomal dominant disorder that causes abnormal blood vessel formation. The diagnosis of hereditary hemorrhagic telangiectasia is clinical, based on the Curaçao
Athena Kritharis +2 more
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Pericardial Involvement in Hereditary Hemorrhagic Telangiectasia
Hereditary haemorrhagic telangiectasia is a rare disease characterized by cutaneo-mucous and visceral arteriovenous malformations. Cardiac involvement is uncommon and was presented primarily by hyper-output heart failure.
Abir Derbel +7 more
doaj +1 more source
Gastrointestinal bleeding in patients with hereditary hemorrhagic telangiectasia
Gastrointestinal bleeding occurs in a number of patients with hereditary hemorrhagic telangiectasia (HHT) and may lead to a high transfusion need.
Kjeldsen, A D; id_orcid +1 more
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As malformações arteriovenosas pulmonares (MAVP) estão associadas a telangiectasia hemorrágica hereditária em cerca de 70% dos casos, podendo cursar com complicações neurológicas graves decorrentes do embolismo paradoxal potencial.
Cláudia Sofia Santos +6 more
doaj
Hereditary hemorrhagic telangiectasia as a cause of severe iron deficiency anemia of obscure origin
Introducción: la telangiectasia hemorrágica hereditaria o enfermedad de Osler-Weber-Rendu es una entidad autosómica dominante rara, con una frecuencia que oscila entre 1 por cada 5000 habitantes a 1 por cada 1331 dependiendo de la población y ...
Puello Ramos, Walter +5 more
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