Juvenile Xanthogranuloma With Hydrocephalus
Indian Journal of Dermatology, 2004 Juvenile xanthogranuloma (JXG) is a rare, benign, self-healing tumor of unknown etiology arising from non-Langerhans†cell histiocytes.
Ghosh Arghyaprasun +4 more
doaj
Necrobiotic xanthogranuloma: A case report of successful treatment with intravenous immunoglobulins
JEADV Clinical Practice, Volume 3, Issue 4, Page 1248-1252, September 2024.Abstract Necrobiotic xanthogranuloma (NXG) is a rare non‐Langerhans cell histiocytosis associated with paraproteinemia. Skin lesions of NXG are difficult to treat and various therapies have been evaluated with inconsistent results. A therapeutic standard has not been established.
Julia K. Winkler +4 more
wiley +1 more source
An Atypical Presentation of a Rare Disease [PDF]
, 2019 A 76-year-old white woman presented for evaluation of asymptomatic skin lesions on her right shin, right buttock, and left arm. All lesions initially underwent slow growth and plateaued and then remained stable in size.
Connolly, Deirdre +3 more
core +1 more source
A 7-Year History of Necrobiotic Xanthogranuloma following Asymptomatic Multiple Myeloma: A Case Report [PDF]
, 2011 Necrobiotic xanthogranuloma (NXG) is a rare destructive xanthomatous granuloma with chronic, indolent, and progressive course. The morbidity and mortality are the results from wound complications and associated disorders.
Inthasotti, Siriluk +2 more
core +4 more sources
Pilomatricoma in the infraorbital region
Clinical Case Reports, Volume 12, Issue 8, August 2024.Key Clinical Message Pilomatricoma, a rare benign skin tumor arising from hair follicle matrix cells, warrants consideration in the evaluation of subcutaneous nodules or masses, especially when presenting as painless and firm lesions. Accurate diagnosis hinges on histopathological examination, underscoring the significance of clinician vigilance and ...
Dilasha Dhungel +3 more
wiley +1 more source
Necrobiotic xanthogranuloma successfully treated with autologous stem cell transplantation [PDF]
, 2018 Paraproteinemia can be complicated by necrobiotic xanthogranuloma. Therapeutic options for this progressive disease are limited, and there is no agreement on a single best strategy.
Dispenzieri, Angela +7 more
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Cutaneous crystal storing histiocytosis: A case series with review of literature
Journal of Cutaneous Pathology, Volume 51, Issue 7, Page 506-512, July 2024.Abstract Crystal‐storing histiocytosis (CSH) is a rare condition in which crystals accumulate in the cytoplasm of histiocytes and is usually associated with a lymphoplasmacytic neoplasm. Cutaneous CSH is extraordinarily rare and limited to case reports in the literature. We report two cases of this disease with cutaneous involvement.
Haya A. Homsi +6 more
wiley +1 more source
Recurrent CLTC::SYK fusions and CSF1R mutations in juvenile xanthogranuloma of soft tissue [PDF]
Juvenile xanthogranuloma (JXG) is a histiocytic neoplasm that usually presents in the skin. Rarely, extracutaneous localizations occur; the genetic drivers of this clinical variant of JXG remain incompletely characterized.
Al-Hussaini, Maysa +25 more
core +1 more source
Erdheim-Chester Disease: a comprehensive review of the literature [PDF]
, 2013 Erdheim-Chester Disease (ECD) is a rare form of non Langerhans' cell histiocytosis. Individuals affected by this disease are typically adults between their 5th and 7th decades of life. Males and females are almost equally affected.
Mirra Manevich-Mazor +2 more
core +1 more source
Cutaneous necrobiotic xanthogranuloma (NXG)--successfully treated with low dose chlorambucil. [PDF]
, 2001 Eur J Dermatol. 2001 Sep-Oct;11(5):458-62. Cutaneous necrobiotic xanthogranuloma (NXG)--successfully treated with low dose chlorambucil. Machado S, Alves R, Lima M, Leal I, Massa A.
Alves, R. +4 more
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