Results 41 to 50 of about 311 (135)

Haploinsufficiency of Col5a1 causes intrinsic lung and respiratory changes in a mouse model of classical Ehlers‐Danlos syndrome

open access: yesPhysiological Reports, Volume 10, Issue 8, April 2022., 2022
We used mice that are haploinsufficient for Col5a1 (Col5a1+/−), a well‐accepted model of classical EDS type, and demonstrated the presence of primary changes in the lung parenchyma that are reminiscent of emphysema. We then performed a detailed analysis of the respiratory mechanics, lung volumes, and flow–volume curves and show that both male and ...
Jordan Fett   +3 more
wiley   +1 more source

Difficulties in the Differential Diagnosis of Tracheobronchomegaly in Children

open access: yesВестник рентгенологии и радиологии, 2020
Tracheobronchomegaly is a rare developmental defect in children, which is characterized by the expansion of the trachea and large bronchi, the diagnosis and treatment of which are made more often in adult practice, when the clinical diagnostic picture ...
N. A. Il’ina   +3 more
doaj   +1 more source

A case of tracheobronchomegaly [PDF]

open access: yesEuropean Journal of Internal Medicine, 2017
Tracheobronchomegaly (Mounier-Kuhn syndrome) is a rare condition characterized by an abnormally enlarged trachea and main bronchi. Herein, we present a case of 79-year-old male with idiopathic pulmonary fibrosis and acute hypoxemic respiratory failure due to multilobar pneumonia. Computed tomography of the chest demonstrated a markedly dilated trachea,
Jirat Chenbhanich   +2 more
openaire   +2 more sources

Anesthetic experience of a patient with tracheomegaly -A case report- [PDF]

open access: yesKorean Journal of Anesthesiology, 2010
Tracheomegaly or tracheobronchomegaly is a rare syndrome that consists of marked dilatation of the trachea and the major bronchi, and this is usually due to a congenital defect of the elastic and muscle fibers of the tracheobroncheal tree.
Mi Young Kim   +5 more
doaj   +1 more source

A 46-year-old man with tracheomegaly, tracheal diverticulosis, and bronchiectasis: Mounier-Kuhn syndrome

open access: yesLung India, 2012
Lower respiratory tract infection is one of the common causes of morbidity in India which is occasionally undiagnosed. In this regard tracheobronchomegaly is one of those conditions which masquerade as chronic bronchitis and bronchiectasis and are ...
Ashish K Jaiswal   +4 more
doaj   +1 more source

Mounier-Kuhn syndrome [PDF]

open access: yesVojnosanitetski Pregled, 2011
Background. Mounier-Kuhn syndrome or tracheobronchomegaly is a rare disorder characterized by marked dilatation of the trachea and main bronchi, bronchiectasis, and recurrent respiratory tract infections.
Pešut Dragica   +4 more
doaj   +1 more source

The Mounier-Kuhn syndrome [PDF]

open access: yesVojnosanitetski Pregled, 2010
Background. The Mounier-Kuhn syndrome (MKS) or tracheobronchomegaly (TBM) is a rare condition of unknown frequency, up to now about 100 cases have been reported.
Milić Rade   +4 more
doaj   +1 more source

Síndrome de Mounier-Kühn Mounier-Kuhn syndrome

open access: yesJornal Brasileiro de Pneumologia, 2006
A síndrome de Mounier-Kühn, ou traqueobroncomegalia congênita, é uma entidade clínica rara caracterizada pela dilatação anormal de traquéia e brônquios principais. O diagnóstico geralmente pode ser realizado através da mensuração do diâmetro traqueal. Os
Fabrício Piccoli Fortuna   +3 more
doaj   +1 more source

Mounier-Kuhn syndrome masquerading pulmonary thromboembolism in an elderly male

open access: yesLung India, 2014
Mounier-Kuhn syndrome, also referred to as tracheobronchomegaly, is a rare idiopathic clinical and radiologic disorder characterized by significant tracheobronchial dilation.
Pankaj Gupta   +3 more
doaj   +1 more source

A case report of Mounier-Kuhn syndrome

open access: yesThe Journal of Association of Chest Physicians, 2017
Mounier-Kuhn syndrome is a congenital abnormality characterized by tracheobronchomegaly as a result of atrophy or absence of elastic fibers and thinning of smooth muscle layer in trachea and main bronchi.
Keerthivasan Sivanmani
doaj   +1 more source

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