Results 31 to 40 of about 11,711 (254)

Developmental and Epileptic Encephalopathy due to Biallelic Pathogenic Variants in PIGM

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective PIGM encodes a critical enzyme in the glycosylphosphatidylinositol (GPI)‐anchor biosynthesis pathway. While promoter‐region mutations in PIGM have been associated with a relatively mild phenotype characterized by portal vein thrombosis and absence seizures, recent evidence suggests that coding‐region mutations result in a more severe
Júlia Sala‐Coromina, Anna Marcé‐Grau, Barbara Masotto, Marta Codina, Lamia BenJemaa, Yasmina Elaribi, Mónica Martinez‐Gallo, Roger Colobran, Angel Sanchez‐Montañez, Irene Valenzuela, Yoshiko Murakami, Alfons Macaya   +11 more
wiley   +1 more source

JUSTIFICATION OF THE POSSIBILITY OF BUILDING AN INTEGRATED ULTRASONIC MEASURING TRANSDUCER OF NATURAL GAS CONSUMPTION

Informatyka, Automatyka, Pomiary w Gospodarce i Ochronie Środowiska
The paper establishes the feasibility of constructing an integrated ultrasonic measuring transducer for measuring natural gas consumption. Various schemes for combining ultrasonic transducers with flow conditioning devices, along with several natural ...
Yosyp Bilynsky, Аndrii Stetsenko, Konstantin Ogorodnik   +2 more
doaj   +1 more source

Neurovascular Contacts in the Pathophysiology of Neuralgic Amyotrophy: An Observational Study

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Neuralgic amyotrophy (NA) is a prevalent, monophasic, multifocal immune‐mediated neuropathy. A distinctive characteristic of the disease is the occurrence of nerve or fascicle constrictions and torsions (NA‐associated focal nerve lesions, NAFL). The pathophysiology underlying this phenomenon remains to be fully elucidated.
Johannes Fabian Holle, Andreas Leha, Volker Limmroth, Wolfram Windisch, Maximilian Zimmermann   +4 more
wiley   +1 more source

Anorectal Dysfunction in Systemic Sclerosis: Clinical Phenotypes and Functional Patterns

Arthritis Care &Research, EarlyView.
Objective The aim of this study was to characterize specific physiologic defects in anorectal dysfunction in systemic sclerosis (SSc) using anorectal manometry (ARM), evaluate associations with gastrointestinal (GI) and extraintestinal clinical phenotypes, and explore potential serologic markers for risk stratification.
Timothy Kaniecki, Alireza Amindarolzarbi, Tsion Abdi, John Clarke, Michael Hughes, Ami A. Shah, Zsuzsanna H. McMahan   +6 more
wiley   +1 more source

Damage Detection Using d15 Piezoelectric Sensors in a Laminate Beam Undergoing Three-Point Bending

Actuators, 2019
A major inhibition to the widespread use of laminate structures is the inability of nondestructive testing techniques to effectively evaluate the bondline integrity.
Hussain Altammar, Anoop Dhingra, Nathan Salowitz   +2 more
doaj   +1 more source

Elastic Properties and Thermal Expansion Behavior of a Polycrystalline VMnFeCoNi High‐Entropy Alloy

Advanced Engineering Materials, EarlyView.
The high‐entropy alloy (HEA) V20Mn20Fe20Co20Ni20 (composition in at.%) can be made single‐phase face‐centered cubic (FCC) when annealed above 1338 K followed by water quenching. In this state, the alloy exhibits the greatest strength‐ductility combination of any quinary single‐phase FCC HEA.
Guillaume Laplanche, Marie Münchhalfen, Aditya Srinivasan Tirunilai, Jürgen Schreuer   +3 more
wiley   +1 more source

High Performance Relaxor-Based Ferroelectric Single Crystals for Ultrasonic Transducer Applications

Sensors, 2014
Relaxor-based ferroelectric single crystals Pb(Mg1/3Nb2/3)O3-PbTiO3 (PMN-PT) have drawn much attention in the ferroelectric field because of their excellent piezoelectric properties and high electromechanical coupling coefficients (d33~2000 pC/N, kt~60%)
Yan Chen, Kwok-Ho Lam, Dan Zhou, Qingwen Yue, Yanxiong Yu, Jinchuan Wu, Weibao Qiu, Lei Sun, Chao Zhang, Haosu Luo, Helen L. W. Chan, Jiyan Dai   +11 more
doaj   +1 more source

Optimum Driving of Ultrasonic Cleaner Using Impedance and FFT Analysis with Validation of Image Processing of Perforated Foils

Applied Sciences, 2023
Over the past decade, ultrasonic cleaners have been widely used in many industries. Now, this technology is finding its way into homes for vegetable, fruit, and clothes cleaning.
Muhammad Usman Khan, Faisal Rehman, Mohsin Saleem, Hassan Elahi, Tae Hyun Sung, Hamid Jabbar   +5 more
doaj   +1 more source

Enhanced Ultrasound Transmission Through Aberration Layers Using Space‐Coiling Acoustic Metamaterials

Advanced Engineering Materials, EarlyView.
Enhancing ultrasound transmission through an aberration layer exhibiting mismatched impedance with the surrounding medium possesses great implications in imaging and treatment. In this study, we show that a space‐coiling acoustic metamaterial with judiciously tailored structural profile can help improve impedance matching.
Maral Ghanami, Hengzhe Ren, Erqian Dong, Ashkan Ghanbarzadeh‐Dagheyan, Chen Shen   +4 more
wiley   +1 more source

Advances in Langevin Piezoelectric Transducer Designs for Broadband Ultrasonic Transmitter Applications

Actuators
Langevin ultrasonic transducers, also known as Tonpilz transducers, are widely used in high-power ultrasonic applications, including underwater sonar arrays, ultrasonic cleaning, and sonication devices.
Jinwook Kim, Jinwoo Kim, Juwon Kang
doaj   +1 more source