Agrin-induced acetylcholine receptor clustering in mammalian muscle requires tyrosine phosphorylation. [PDF]
, 1996 Agrin is thought to be the nerve-derived factor that initiates acetylcholine receptor (AChR) clustering at the developing neuromuscularjunction. We have investigated the signaling pathway in mouse C2 myotubes and report that agrin induces a rapid but ...
Deiner, M, Ferns, M, Hall, Z
core
Employment of Microencapsulated Sertoli Cells as a New Tool to Treat Duchenne Muscular Dystrophy
Journal of Functional Morphology and Kinesiology, 2017 Duchenne muscular dystrophy (DMD) is a lethal X-linked pathology due to lack of dystrophin and characterized by progressive muscle degeneration, impaired locomotion and premature death.
Sara Chiappalupi +6 more
doaj +1 more source
A nitric oxide synthase transgene ameliorates muscular dystrophy in mdx mice. [PDF]
, 2001 Dystrophin-deficient muscles experience large reductions in expression of nitric oxide synthase (NOS), which suggests that NO deficiency may influence the dystrophic pathology.
Spencer, MJ, Tidball, JG, Wehling, M
core
The spectrin family of proteins: a unique coiled-coil fold for various molecular surface properties
, 2014 International audienceThe spectrin superfamily is composed of proteins involved in cytolinker functions. Their main structural feature is a large central subdomain with numerous repeats folded in triple helical coiled-coils.
Delalande, Olivier +3 more
core +2 more sources
A gliovascularis lamina basalis funkcionális állapotainak immunhisztokémiai jellemzése = Immunohistochemical characterisation of functional stages of the gliovascular basal lamina [PDF]
, 2011 A gliovaszkuláris kapcsolatban lényeges disztroglikán-disztrofin komplex (DGC) komponenseit vizsgáltuk immunhisztokémiai módsrerekkel patkányban Intakt, kifejlett állatban a tobozmirigy ereinek festődése inkább hasonlított a piában futó erekre, mint az ...
Dénes, László +3 more
core
Activation of p38 signaling increases utrophin A expression in skeletal muscle via the RNA-binding protein KSRP and inhibition of AU-rich element-mediated mRNA decay: implications for novel DMD therapeutics [PDF]
, 2013 Adel Amirouche +5 more
openalex +1 more source
Prevention of pathology in mdx mice by expression of utrophin: analysis using an inducible transgenic expression system [PDF]
, 2002 Sarah Squire
openalex +1 more source
, 2009 International audienceThe dystrophin-glycoprotein complex (DGC) is a large trans-sarcolemmal complex that provides a linkage between the subsarcolemmal cytoskeleton and the extracellular matrix.
Cherel, Yan +3 more
core +2 more sources
Arquivos de Neuro-PsiquiatriaSignificant advances in the understanding and management of Duchenne muscular dystrophy (DMD) took place since international guidelines were published in 2010.
Alexandra P. Q. C. Araujo +15 more
doaj +1 more source
Expression and function of utrophin associated protein complex in stretched endothelial cells: dissociation and activation of eNOS [PDF]
, 2006 Israel Ramírez‐Sánchez
openalex +1 more source