The synaptic Muscle-Specific Kinase (MuSK) complex: new partners, new functions. [PDF]
, 2005 The muscle-specific kinase MuSK is part of an agrin receptor complex which stimulates tyrosine phosphorylation and drives clustering of acetylcholine receptors (AChRs) in the postsynaptic membrane at the vertebrate neuromuscular junction.
Cartaud, Annie +2 more
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l-arginine improves dystrophic phenotype in mdx mice
Neurobiology of Disease, 2005 A possible treatment for Duchenne muscular dystrophies would be to compensate for dystrophin loss by increasing the expression of utrophin, another cytoskeletal protein of the muscle membrane. We previously found that l-arginine, the substrate for nitric
Vincent Voisin +7 more
doaj
Dystrophin and utrophin influence fiber type composition and post-synaptic membrane structure [PDF]
, 2000 Jill A. Rafael
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Arquivos de Neuro-PsiquiatriaSignificant advances in the understanding and management of Duchenne muscular dystrophy (DMD) took place since international guidelines were published in 2010.
Alexandra P. Q. C. Araujo +15 more
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Adhesion-dependent tyrosine phosphorylation of β-dystroglycan regulates its interaction with utrophin [PDF]
, 2000 Marian James +6 more
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Regulation and functional significance of utrophin expression at the mammalian neuromuscular synapse [PDF]
, 2000 Anthony O. Gramolini +2 more
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Distinct regions in the 3′ untranslated region are responsible for targeting and stabilizing utrophin transcripts in skeletal muscle cells [PDF]
, 2001 Anthony O. Gramolini +2 more
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Subcutaneous injection, from birth, of epigallocatechin-3-gallate, a component of green tea, limits the onset of muscular dystrophy in mdx mice: a quantitative histological, immunohistochemical and electrophysiological study [PDF]
, 2018 Dystrophic muscles suffer from enhanced oxidative stress. We have investigated whether administration of an antioxidant, epigallocatechin-3-gallate (EGCG), a component of green tea, reduces their oxidative stress and pathophysiology in mdx mice, a mild ...
Goto, Junpei +6 more
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Utrophin, MHC and M1/M2 macrophages in GRMD dogs
Ciência Animal Brasileira, 2020 Muscular dystrophies are hereditary diseases that lead to progressive degeneration of the skeletal musculature. Golden Retriever dogs are used as animal models because they show a hereditary muscle disease similar to muscular dystrophy in humans.
Gabriela Noronha de Toledo +1 more
doaj
The role of basal and myogenic factors in the transcriptional activation of utrophin promoter A: implications for therapeutic up-regulation in Duchenne muscular dystrophy [PDF]
, 2001 Kathleen J. Perkins
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