Results 171 to 180 of about 1,915,528 (208)

Contemporary management of vascular Ehlers–Danlos syndrome

Current Opinion in Cardiology, 2011
Vascular Ehlers-Danlos syndrome (EDS) results from mutations in the formation of type III collagen. This leads to various potentially lethal complications including rupture of the arterial vessels, intestinal organs, and the uterus. This review summarizes recent cohort studies that have improved our medical and surgical management of complications ...
Ying Wei, Lum, Benjamin S, Brooke, James H, Black   +2 more
openaire   +2 more sources

Vascular Ehlers-Danlos Syndrome: Imaging Findings

American Journal of Roentgenology, 2007
Vascular Ehlers-Danlos syndrome (EDS), formerly known as EDS type IV, is an autosomal dominant disorder characterized by fragility of medium and large arteries due to type III procollagen deficiency. Our purpose was to review the imaging findings in a cohort of patients with a diagnosis of vascular EDS.The radiologic, surgical, and genetic databases at
Massimo, Zilocchi, Thanila A, Macedo, Gustavo S, Oderich, Terri J, Vrtiska, Pietro R, Biondetti, Anthony W, Stanson   +5 more
openaire   +2 more sources

Treatment of Vascular Ehlers-Danlos Syndrome

Annals of Surgery, 2013
To provide the collected evidence from all literature reports.Vascular Ehlers-Danlos syndrome (EDS) is a rare connective tissue disorder with serious hemorrhagic consequences. Most experience on treatment is based on case reports and small case series.A systematic literature review was performed.
David, Bergqvist, Martin, Björck, Anders, Wanhainen   +2 more
openaire   +2 more sources

Two vascular complications of the Ehlers—Danlos syndrome

European Journal of Vascular Surgery, 1993
Patients with Ehlers-Danlos syndrome type IV have thin walled, friable arteries and veins and are prone to spontaneous arterial rupture. We present a patient who suffered severe damage to the common femoral vein during surgery for varicose veins and who subsequently suffered a spontaneous rupture of the right external carotid artery, treated by ...
S, Brearley, J, Fowler, J D, Hamer
openaire   +2 more sources

Successful multidisciplinary management of vascular Ehlers–Danlos syndrome

Clinical Journal of Gastroenterology, 2021
Vascular Ehlers-Danlos syndrome is a rare connective tissue disease with a high risk of severe complications. Because of these complications, the median life expectancy for patients with vascular Ehlers-Danlos syndrome is estimated at 48 years. However, the optimal management of these complications remains unclear. A 25-year-old man with abdominal pain
Shintaro Kanaka, Takeshi Yamada, Akihisa Matsuda, Goro Takahashi, Masatoku Arai, Toru Takiguchi, Hideki Tayama, Hiroshi Yoshida   +7 more
openaire   +2 more sources

Stroke in vascular Ehlers-Danlos syndrome

Practical Neurology, 2023
Rebecca Ranzani Martins, Mauricio Leonardo da Silva Paiva, Weverton Carlos da Silva Teixeira, Rachel Sayuri Honjo Kawahira, Fernando Freua, Matheus Augusto Araujo Castro, Chong Ae Kim, Fernando Kok   +7 more
openaire   +2 more sources

[Vascular Ehlers-Danlos syndrome].

Presse medicale (Paris, France : 1983), 2007
The vascular type of Ehlers-Danlos syndrome (EDS) is a rare genetic disease transmitted as an autosomal dominant trait. It is distinguished from other forms of EDS by its unstable acrogeric morphotype and by vascular, gastrointestinal, and obstetrical complications.
Jérôme, Perdu, Pierre, Boutouyrie, Khadija, Lahlou-Laforêt, Philippe, Khau Van Kien, Nicolas, Denarié, Elie, Mousseaux, Marc, Sapoval, Pierre, Julia, Frank, Zinzindohoué, Philippe, Touraine, Yves, Dumez, Denis, Trystram, Catherine, Vignal-Clermont, Anne-Paule, Gimenez-Roqueplo, Xavier, Jeunemaitre, Jean-Noël, Fiessinger   +15 more
openaire   +1 more source

Anaesthetic Implications of Vascular Type Ehlers-Danlos Syndrome [PDF]

Anaesthesia and Intensive Care, 2006
Vascular type Ehlers-Danlos syndrome is an inherited connective tissue disease, which is typified by tissue fragility, joint hypermobility, a tendency to bleed excessively and rupture of the uterus, the bowel and arteries. Two case reports are presented which describe the anaesthetic management of patients with spontaneous bowel perforations due to ...
exaly   +3 more sources

Changing Patterns in the Vascular Form of Ehlers-Danlos Syndrome

Archives of Surgery, 1986
We report and analyze two cases of Ehlers-Danlos syndrome (EDS) type 4. The first manifestation of the disease was a spontaneous perforation of the colon in a 47-year-old man; he was successfully reoperated on five years later for the rupture of an abdominal aortic aneurysm.
P, Gertsch, P W, Loup, A, Lochman, P, Anani   +3 more
openaire   +2 more sources

Vascular Ehlers-Danlos Syndrome

Cardiology in Review, 2012
The Ehlers-Danlos syndrome consists of a group of inherited connective tissue disorders caused by defects in the synthesis of collagen. The vascular type 4 form of Ehlers-Danlos syndrome (VEDS) is associated with serious vascular complications in young adults, such as the spontaneous rupture of large-caliber and medium-caliber arteries, often without ...
Natalia, Beridze, William H, Frishman
openaire   +2 more sources