Results 31 to 40 of about 5,479,866 (221)

Temperature-Dependence of Weibel-Palade Body Exocytosis and Cell Surface Dispersal of von Willebrand Factor and Its Propolypeptide [PDF]

, 2011
Background: Weibel-Palade bodies (WPB) are endothelial cell (EC) specific secretory organelles containing Von Willebrand factor (VWF). The temperature-dependence of Ca2+-driven WPB exocytosis is not known, although indirect evidence suggests that WPB ...
Hewlett, L, Matthew J. Hannah, Carter, T, David Ogden, Hannah, MJ, Matthew J Hannah, Mashanov, G, Gregory Mashanov, Zupančič, G, Knipe, L, Tom Carter, Laura Knipe, Gregor Zupančič, Ogden, D, Lindsay Hewlett, Zupančič Gregor, Hannah, Matthew J., Ogden, David, Hewlett, Lindsay, Carter Tom, Hannah Matthew J., Knipe, Laura, Mashanov, Gregory, Ogden David, Zupančič, Gregor, Hewlett Lindsay, Carter, Tom D., Mashanov Gregory, Knipe Laura   +28 more
core   +1 more source

Lack of multimer organization of von Willebrand factor in an acquired von Willebrand syndrome [PDF]

British Journal of Haematology, 2002
Summary. We report a case of acquired von Willebrand syndrome (AVWS) in a 20‐year‐old‐woman with systemic lupus erythematosus, in whom severe bleeding complications followed kidney biopsy. Coagulation studies demonstrated undetectable levels of ristocetin‐induced platelet aggregation (RIPA), von Willebrand factor antigen (VWF:Ag) and VWF ristocetin ...
CASONATO, SANDRA, PONTARA, ELENA, DORIA, ANDREA, BERTOMORO, ANTONELLA, Cattini MG, GAMBARI, PIERFRANCA, GIROLAMI, ANTONIO   +6 more
openaire   +3 more sources

Clinical practice guidelines for the management of atypical haemolytic uraemic syndrome in the United Kingdom [PDF]

, 2010
Atypical haemolytic uraemic syndrome (aHUS) is associated with a poor prognosis with regard to survival at presentation, recovery of renal function and transplantation.
Sam Machin, ?, ?, Machin, Sam, Tim H. J. Goodship, Goodship, Tim H J, Stephen J. Wigmore, Taylor, C Mark, Wigmore, Stephen J, C. Mark Taylor   +8 more
core   +1 more source

Acquired von Willebrand syndrome associated with plasma cell myeloma – a rare histopathological bone marrow image

Polish Journal of Pathology, 2020
Acquired von Willebrand syndrome (AVWS) is a rare bleeding disorder that is associated with a variety of underlying diseases. We report a case of AVWS associated with plasma cell myeloma.
Maria Chraszczewska, Kamil Sokół, Olga Kuczkiewicz-Siemion, Monika Prochorec-Sobieszek, Anna Szumera-Cieækiewicz   +4 more
doaj   +1 more source

Impact of the Severity of Acquired von Willebrand Syndrome on the Short-Term Prognosis in Patients with Temporary Mechanical Circulatory Support

Medicina, 2022
Background and Objectives: Acquired von Willebrand syndrome (AVWS) develops not only in patients with durable ventricular assist devices but also in patients receiving temporary mechanical circulatory support (MCS).
Makiko Nakamura, Teruhiko Imamura, Hiroshi Ueno, Koichiro Kinugawa   +3 more
doaj   +1 more source

The role of von Willebrand factor and its cleaving protease, ADAMTS13, in young patients with HIV-related stroke. [PDF]

, 2013
Includes abstract.Includes bibliographical references.The Human Immunodeficiency Virus (HIV) is neuro-invasive and neurological complications of HIV infection occur frequently through a variety of possible mechanisms.
Allie, Sameera
core   +1 more source

Reappraising the spectrum of bleeding gastrointestinal angioectasia in a degenerative calcific aortic valve stenosis: Heyde’s syndrome

The Egyptian Journal of Internal Medicine, 2021
Background The occurrence of bleeding gastrointestinal angioectasia in elderly patients with degenerative calcific aortic stenosis is one of the most challenging clinical scenarios. A number of studies have shown that this clinical phenomenon is known as
Nelson Musilanga, Zhou Hongli, Cai Hongyu   +2 more
doaj   +1 more source

Successful treatment of acquired von Willebrand syndrome in multiple myeloma

Thrombosis Update, 2022
Acquired von Willebrand syndrome (AVWS) is a rare bleeding disorder characterized by quantitative or qualitative defects of the von Willebrand factor (vWF) with laboratory findings and clinical presentations similar to those of inherited von Willebrand ...
Sandra Marten, Raphael Teipel, Oliver Tiebel, Karolin Trautmann-Grill   +3 more
doaj   +1 more source

Bleeding from gastrointestinal angioectasias is not related to bleeding disorders - a case control study

BMC Gastroenterology, 2010
Background Angioectasias in the gastrointestinal tract can be found in up to 3% of the population. They are typically asymptomatic but may sometimes result in severe bleeding. The reasons for why some patients bleed from their angioectasias are not fully
Lärfars Gerd, Hillarp Andreas, Lindahl Tomas L, Broström Olle, Höög Charlotte M, Sjöqvist Urban   +5 more
doaj   +1 more source

Administration of plasma-derived coagulation factor VIII during the perioperative period of mastectomy for breast cancer with acquired von Willebrand syndrome

Surgical Case Reports, 2018
Background Acquired von Willebrand syndrome (aVWS) is a rare bleeding disorder with laboratory findings similar to those of congenital von Willebrand disease (VWD).
Ritsuko Sasaki, Yoshiya Horimoto, Ju Mizuno, Yoko Edahiro, Tsukasa Ohmori, Norio Komatsu, Mitsue Saito   +6 more
doaj   +1 more source