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[Clinical characteristics and prognosis of primary immune thrombocytopenia complicated with diffuse alveolar hemorrhage]. [PDF]

open access: yesZhonghua Xue Ye Xue Za Zhi
An ZY   +8 more
europepmc   +1 more source

支气管肺泡灌洗液涂片辅助诊断嗜酸性肉芽肿性多血管炎1例

open access: yesZhongguo shiyan zhenduanxue
嗜酸性肉芽肿性多血管炎(eosinophilic granulomatosis with polyangiitis, EGPA)是一种系统性坏死性血管炎,临床上罕见,常被误诊。目前国内外对 EGPA 的发病机制、病理改变、基因组学等认识不足,大多数研究是关于临床特征、实验室检查、影像学检查和病理学检查[1-3]。EGPA患者突出的实验室检查特征是外周血嗜酸性粒细胞比值和计数显著升高,受累组织活检结果可见血管炎和血管周围嗜酸性粒细胞浸润。
王春苗   +4 more
doaj  

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