Results 51 to 60 of about 838,557 (301)

A study on the safety and efficacy of reveglucosidase alfa in patients with late-onset Pompe disease. [PDF]

, 2017
BackgroundLate-onset Pompe disease is a rare genetic neuromuscular disorder caused by lysosomal acid alpha-glucosidase (GAA) deficiency that ultimately results in mobility loss and respiratory failure.
Barohn, Richard, Barshop, Bruce A, Bratkovic, Drago, Byrne, Barry J, Desnuelle, Claude, Geberhiwot, Tarekegn, Haroldsen, Peter, Hughes, Derralynn, Jayaram, Kala, Laforet, Pascal, Mengel, Eugen, POM-001/002 Investigators, Reilley, Kristin, Roberts, Mark, Walsh, Liron, Yang, Ke   +15 more
core   +2 more sources

Real‐Time, Label‐Free Monitoring of Cell Behavior on a Bioelectronic Scaffold

Advanced Functional Materials, EarlyView.
A bioelectronic nanofibrous scaffold is introduced that supports cell growth while enabling real‐time, label‐free monitoring of cellular behavior through impedance measurements. The system correlates electrical signals with cell viability and surface coverage, offering an integrated platform for studying dynamic biological processes and advancing next ...
Dana Cohen‐Gerassi, Offir Loboda, Aakash Jog, Or Messer, Dor Aaron Goldstein, Tomer Reuveni, Moran Aviv, Amit Sitt, Yosi Shacham‐Diamand, Maxim Sokol, Lihi Adler‐Abramovich   +10 more
wiley   +1 more source

Infrared Nanocrystals for Space Application: Hardness to Irradiations

Advanced Functional Materials, EarlyView.
This article investigates infrared HgTe nanocrystals under X‐ray and ion irradiation, revealing remarkable radiation hardness. It uncovers distinct degradation mechanisms and shows that the nanomaterial outperforms integrated electronics. The results position colloidal nanocrystals as promising candidates for resilient space and harsh‐environment ...
Alexandre Neyret, Dario Mastrippolito, Bingbing Xia, Adrien Khalili, Maxime Lebreton, Giorgia Strobbia, Albin Colle, Marco Paye, Mariarosa Cavallo, Erwan Bossavit, Claire Abadie, Yoann Prado, Debora Pierucci, Victor Parahyba, Francois Coursaget, David Darson, Emrick Briand, Ian Vickridge, Stephane Demiguel, Sebastien Massenot, Jean‐Marc Belloir, Vincent Goiffon, Emmanuel Lhuillier   +22 more
wiley   +1 more source

The Arecibo L-band Feed Array Zone of Avoidance Survey I: Precursor Observations through the Inner and Outer Galaxy

, 2010
The Arecibo L-band Feed Array (ALFA) is being used to conduct a low-Galactic latitude survey, to map the distribution of galaxies and large-scale structures behind the Milky Way through detection of galaxies' neutral hydrogen (HI) 21-cm emission.
Catinella, B., Day, F., Henning, P. A., Koribalski, B., McIntyre, T., Minchin, R. F., Momjian, E., Muller, E., Rosenberg, J. L., Schneider, S., Springob, C. M., Staveley-Smith, L., van Driel, W.   +12 more
core   +1 more source

Surface Diffusion in SnTe‐PbTe Monolayer Lateral Heterostructures

Advanced Functional Materials, EarlyView.
The lateral heterostructures between 2D materials often suffer from the interdiffusion at the interfaces. Here, a surface diffusion mechanism is found to be dominating at the interfaces between semiconducting SnTe and PbTe monolayers. Atomically sharp interfaces can be achieved by suppressing this diffusion process. ABSTRACT The construction of complex
Jing‐Rong Ji, Zi'Ang Gao, Shiva Prasad Poudel, Rui‐Qi Cao, Tianzhe Chen, Luxin Li, Chong Liu, Salvador Barraza‐Lopez, Stuart S. P. Parkin, Kai Chang   +9 more
wiley   +1 more source

Novel management of pseudomonas biofilm-like structure in a post-pneumonectomy empyema

Frontiers in Cellular and Infection Microbiology
We present a patient with a post-pneumonectomy empyema refractory to surgical debridement and systemic antibiotics. The patient initially presented with a bronchopleural fistula and pneumothorax secondary to tuberculosis (TB) destroyed lung, which ...
Alexandra M. Gustafson, Carolina M. Larrain, Lindsay R. Friedman, Rachel Repkorwich, Ifeanyichukwu U. Anidi, Karen M. Forrest, Kevin P. Fennelly, Shamus R. Carr   +7 more
doaj   +1 more source

The Project Activities of the Renewable Energy Resources Use in the Republic of Serbia

Journal of Sustainable Development of Energy, Water and Environment Systems, 2014
With the ratification of the Energy Community of Southeast Europe countries (14th July 2006) the Republic of Serbia, among other things, accepted the obligation to adopt and implement a plan of applying the Directive 2001/77/EC about promoting the ...
Larisa Jovanović, Lazar Cvijić
doaj   +1 more source

Active Microrheology of Networks Composed of Semiflexible Polymers. II. Theory and comparison with simulations

, 2005
Building on the results of our computer simulation (ArXiv cond-mat/0503573)we develop a theoretical description of the motion of a bead, embedded in a network of semiflexible polymers, and responding to an applied force.
A. Boulbitch, A. J. Levine, B. Alberts, D. A. Pink, F. G. Schmidt, F. Gittes, H. C. Brinkman, L. D. Landau, L. D. Landau, N. Ter-Oganessian, N. W. Tschoegl, W. Helfrich   +11 more
core   +1 more source

High Entropy Wide‐Bandgap Borates with Broadband Luminescence and Large Nonlinear Optical properties

Advanced Functional Materials, EarlyView.
High‐entropy rare‐earth borates exhibit excellent nonlinear optical and broadband luminescence properties arising from multi‐component doping, chemical disorder, increased configurational entropy, and increased lattice and electronic anharmonicity. This formulation enabled us to obtain a large, environmentally stable single crystal with 3X higher laser‐
Saugata Sarker, Yu Wang, Yongwen Sun, Caeli Benyacko, Saeed S.I. Almishal, Tao Zhou, Zhiyu Zhang, Jadupati Nag, Himirkanti Sarkar, Jeffrey Shallenberger, Hemant Yennawar, Yang Yang, Jon‐Paul Maria, Zhiqiang Mao, Venkatraman Gopalan   +14 more
wiley   +1 more source

Local Governments' Policies of Investments in Environmental Protection

Industrija, 2013
The present paper tries to investigate the impact of the decrease of local governments' budgets on the local government environmental investment policies.
Jozefina J. Beke-Trivunac, Larisa Jovanović   +1 more
doaj   +1 more source