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Arrhythmogenic Cardiomyopathy [PDF]
Circulation Research, 2017 Arrhythmogenic cardiomyopathy is an inherited heart muscle disorder, predisposing to sudden cardiac death, particularly in young patients and athletes. Pathological features include loss of myocytes and fibrofatty replacement of right ventricular myocardium; biventricular involvement is often observed.
Cristina Basso
exaly +9 more sources
Zdravniški Vestnik, 2019 Arrhythmogenic cardiomyopathy (AC) is a genetic disease of the myocardium characterized by fibro-fatty replacement of the apoptotic myocardium. It primarily affects the right ventricle, however in advanced stages of the disease the left ventricle can ...
Blaž Podgoršek +4 more
doaj +3 more sources
Natural History of Arrhythmogenic Cardiomyopathy [PDF]
Journal of Clinical Medicine, 2020 Arrhythmogenic cardiomyopathy (AC) is a heart muscle disease characterized by a scarred ventricular myocardium with a distinctive propensity to ventricular arrhythmias (VAs) and sudden cardiac death, especially in young athletes. Arrhythmogenic right ventricular cardiomyopathy (ARVC) represents the best characterized variant of AC, with a peculiar ...
Alberto Cipriani
exaly +3 more sources
Arrhythmogenic Cardiomyopathy [PDF]
European Heart Journal, 2020 Electrocardiography (ECG) is a critically important modality in the investigation of patients with cardiomyopathy of any kind, including arrhythmogenic cardiomyopathies. In some specific arrhythmogenic cardiomyopathies, the ECG is to some extent diagnostic, e.g.
Proost, Virginnio M. +1 more
+8 more sources
Arrhythmogenic Cardiomyopathy [PDF]
Circulation, 2018 Arrhythmogenic cardiomyopathy (AC) is a genetic disorder characterized by high risk of life-threatening ventricular arrhythmias, sudden cardiac death, and progressive heart failure. Currently, there is evidence that AC includes a spectrum of cardiomyopathy phenotypes, ranging from the classical form of arrhythmogenic right ventricular cardiomyopathy ...
Pilichou K. +3 more
+9 more sources
Multimodality imaging in arrhythmogenic cardiomyopathy [PDF]
Romanian Journal of Cardiology, 2021 Arrhythmogenic cardiomyopathy, as it has been recently redefined, is characterized by progressive myocyte loss with fibrosis and fat infiltration of the myocardium, which finally leads to a broad clinical spectrum ranging from heart failure symptoms to ...
Laura Tapoi +3 more
doaj +1 more source
Pregnancy in arrhythmogenic cardiomyopathy [PDF]
Herzschrittmachertherapie + Elektrophysiologie, 2021 AbstractArrhythmogenic cardiomyopathy (AC) is a rare heart muscle disease with a genetic background and autosomal dominant mode of transmission. The clinical manifestation is characterized by ventricular arrhythmias (VA), heart failure (HF) and the risk of sudden cardiac death (SCD).
Wichter, Thomas +3 more
openaire +2 more sources
Metabolic Signature of Arrhythmogenic Cardiomyopathy [PDF]
Metabolites, 2021 Arrhythmogenic cardiomyopathy (ACM) is a genetic-based cardiac disease accompanied by severe ventricular arrhythmias and a progressive substitution of the myocardium with fibro-fatty tissue. ACM is often associated with sudden cardiac death. Due to the reduced penetrance and variable expressivity, the presence of a genetic defect is not conclusive ...
Chiara Volani +10 more
openaire +4 more sources
Radiology Case Reports, 2023 Arrhythmogenic cardiomyopathy is a genetic heart muscle disease that typically affects the right ventricle. However, 2 other phenotypes affecting the left ventricle were recently discovered.
Hajar El Ouartassi, MD +6 more
doaj +1 more source
Scarring/arrhythmogenic cardiomyopathy
European Heart Journal Supplements, 2023 Abstract The designation of ‘arrhythmogenic cardiomyopathy’ reflects the evolving concept of a heart muscle disease affecting not only the right ventricle (ARVC) but also the left ventricle (LV), with phenotypic variants characterized by a biventricular (BIV) or predominant LV involvement (ALVC).
Corrado, Domenico +15 more
openaire +2 more sources