Results 41 to 50 of about 979 (102)

Arrhythmogenic right ventricular cardiomyopathy: diverse substrate characteristics and ablation outcome

Reviews in Cardiovascular Medicine, 2021
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited cardiomyopathy caused by defective desmosomal proteins. The typical histopathological finding of ARVC is characterized by progressive fibrofatty infiltration of the right ventricle
Wen-Han Cheng, Fa-Po Chung, Yenn-Jiang Lin, Li-Wei Lo, Shih-Lin Chang, Yu-Feng Hu, Ta-Chuan Tuan, Tze-Fan Chao, Jo-Nan Liao, Chin-Yu Lin, Ting-Yung Chang, Ling Kuo, Cheng-I Wu, Chih-Min Liu, Shin-Huei Liu, Shih-Ann Chen   +15 more
doaj   +1 more source

A Crossroads Junction That Leads to Heart Failure (Arrhythmogenic Cardiomyopathy): Hope for Future Therapeutics

Cardiogenetics, 2023
Arrhythmogenic cardiomyopathy (ACM) is an inherited multifaceted cardiac disease that causes sudden cardiac death, especially in young adults and athletes [...]
Kadiam C. Venkata Subbaiah
doaj   +1 more source

Emergency department extracorporeal membrane oxygenation as a rescue therapy for ventricular tachycardia electrical storm: a case report

Journal of the American College of Emergency Physicians Open, 2020
Arrhythmogenic right ventricular cardiomyopathy is a cause of sudden cardiac death in often otherwise healthy young adults. Cardiac arrest following an unstable tachydysrhythmia may be the primary presenting symptom.
Andrew Pugh, Joseph E. Tonna, Scott Youngquist, John J. Ryan, Graham Brant‐Zawadzki   +4 more
doaj   +1 more source

Wide Complex Tachycardia in Arrhythmogenic Right Ventricular Cardiomyopathy: Electrocardiogramand Intracardiac Electrogram Features

Indian Journal of Clinical Cardiology, 2022
Case of an arrhythmogenic right ventricular cardiomyopathy with associated arrhythmias discussing classical electrocardiogram and intracardiac electrogram findings.
Rangadham Nagarakanti, Kavin Raj
doaj   +1 more source

Cardiovascular Characteristics of Patients with Genetic Variation in Desmoplakin (DSP)

Cardiogenetics, 2022
Background: Variants in the desmoplakin (DSP) gene have been recognized in association with the pathogenesis of arrhythmogenic right ventricular cardiomyopathy (ARVC) for nearly 20 years.
Nosheen Reza, Alejandro de Feria, Jessica L. Chowns, Lily Hoffman-Andrews, Laura Vann, Jessica Kim, Amy Marzolf, Anjali Tiku Owens   +7 more
doaj   +1 more source

Molecular mechanisms of arrhythmogenic cardiomyopathy [PDF]

Nature Reviews Cardiology, 2019
Arrhythmogenic cardiomyopathy is a genetic disorder characterized by the risk of life-threatening arrhythmias, myocardial dysfunction and fibrofatty replacement of myocardial tissue. Mutations in genes that encode components of desmosomes, the adhesive junctions that connect cardiomyocytes, are the predominant cause of arrhythmogenic cardiomyopathy and
Karyn M. Austin, Michael A. Trembley, Stephanie F. Chandler, Stephen P. Sanders, Jeffrey E. Saffitz, Dominic J. Abrams, William T. Pu   +6 more
openaire   +2 more sources

High resolution systematic digital histological quantification of cardiac fibrosis and adipose tissue in phospholamban p.Arg14del mutation associated cardiomyopathy.

PLoS ONE, 2014
Myocardial fibrosis can lead to heart failure and act as a substrate for cardiac arrhythmias. In dilated cardiomyopathy diffuse interstitial reactive fibrosis can be observed, whereas arrhythmogenic cardiomyopathy is characterized by fibrofatty ...
Johannes M I H Gho, René van Es, Nikolas Stathonikos, Magdalena Harakalova, Wouter P te Rijdt, Albert J H Suurmeijer, Jeroen F van der Heijden, Nicolaas de Jonge, Steven A J Chamuleau, Roel A de Weger, Folkert W Asselbergs, Aryan Vink   +11 more
doaj   +1 more source

Impact of Exercise Restriction on Arrhythmic Risk Among Patients With Arrhythmogenic Right Ventricular Cardiomyopathy

Journal of the American Heart Association: Cardiovascular and Cerebrovascular Disease, 2018
Background Prior studies have shown a close link between exercise and development of arrhythmogenic right ventricular cardiomyopathy. How much exercise restriction reduces ventricular arrhythmia (VA), how genotype modifies its benefit, and whether it ...
Weijia Wang, Gabriela Orgeron, Crystal Tichnell, Brittney Murray, Jane Crosson, Oliver Monfredi, Julia Cadrin‐Tourigny, Harikrishna Tandri, Hugh Calkins, Cynthia A. James   +9 more
doaj   +1 more source

Intercalated Discs and Arrhythmogenic Cardiomyopathy [PDF]

Circulation: Cardiovascular Genetics, 2014
Heart tissue is subjected to high mechanical stress. Different junctional complexes exist within the intercalated disc (ID) at the site of end-to-end contacts between cardiomyocytes. These junctions are essential for adhesive integrity, morphogenesis, differentiation, and maintenance of cardiac tissue.
RAMPAZZO, ALESSANDRA, CALORE, MARTINA, van Hengel J, van Roy F.   +3 more
openaire   +4 more sources

Arrhythmogenic Right Ventricular Cardiomyopathy and Cor Triatriatum Dexter: An Unreported Association

Clinical Case Reports
We present a 74‐year‐old patient with a previous diagnosis of arrhythmogenic right ventricular cardiomyopathy manifesting as heart failure where a concomitant cor triatriatum dexter has accidentally been diagnosed by echocardiography.
Erica Franco, Chiara Rovera, Claudio Moretti, Pier Paolo Bassareo   +3 more
doaj   +1 more source