Clinical features and arrhythmic complications of patients with pediatric-onset arrhythmogenic right ventricular dysplasia [PDF]
Objective: Arrhythmogenic right ventricular dysplasia (ARVD) is a myocardial genetic disease that occurs primarily in the right ventricle. Patients with ARVD may present with severe ventricular arrhythmias, syncope, and cardiac arrest.
Fatma Sevinç Şengül +6 more
doaj +3 more sources
Implantable Cardioverter‐Defibrillator Therapy in Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy: Predictors of Appropriate Therapy, Outcomes, and Complications [PDF]
BackgroundArrhythmogenic right ventricular dysplasia/cardiomyopathy is characterized by ventricular arrhythmias and sudden cardiac death. Once the diagnosis is established, risk stratification to determine whether implantable cardioverter‐defibrillator ...
Gabriela M. Orgeron +11 more
doaj +3 more sources
Ventricular Arrhythmias in Arrhythmogenic Right Ventricular Dysplasia [PDF]
In this issue of 'EP Update' we summarize the recent literature on arrhythmogenic right ventricular dysplasia (ARVD). The articles have been hand picked and reviewed by the editors of IPEJ for the benefit of readers.
Johnson Francis, MD, DM, FACC, FRCP Edin, FRCP London +1 more
doaj +4 more sources
Desmosomal COP9 regulates proteome degradation in arrhythmogenic right ventricular dysplasia/cardiomyopathy. [PDF]
Dysregulated protein degradative pathways are increasingly recognized as mediators of human disease. This mechanism may have particular relevance to desmosomal proteins that play critical structural roles in both tissue architecture and cell‐cell ...
Liang Y +15 more
europepmc +2 more sources
Left ventricular fibro-fatty replacement in arrhythmogenic right ventricular dysplasia/cardiomyopathy: prevalence, patterns, and association with arrhythmias. [PDF]
Background Left ventricular (LV) fibrofatty infiltration in arrhythmogenic right ventricular (RV) dysplasia/cardiomyopathy (ARVD/C) has been reported, however, detailed cardiovascular magnetic resonance (CMR) characteristics and association with outcomes
Zghaib T +11 more
europepmc +2 more sources
Transesophageal and intracardiac ultrasound in arrhythmogenic right ventricular dysplasia/cardiomyopathy: Two case reports. [PDF]
Rationale: Two-dimensional echocardiography (2D echo) is a major tool for the diagnosis of Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C). However 2D echo can skip regional localized anomalies of the right ventricular wall.
Cismaru G +8 more
europepmc +2 more sources
Arrhythmogenic right ventricular cardiomyopathy/dysplasia [PDF]
Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a heart muscle disease clinically characterized by life-threatening ventricular arrhythmias. Its prevalence has been estimated to vary from 1:2,500 to 1:5,000.
Basso Cristina +2 more
doaj +3 more sources
Physical exercise and arrhythmogenic right ventricular cardiomyopathy/dysplasia: An overview
Arrhythmogenic right ventricular cardiomyopathy/dysplasia is inherited cardiomyopathy that has a propensity for ventricular arrhythmia, ventricular dysfunction, and sudden cardiac death.
Rasha Kaddoura, Hassan Al-Tamimi
doaj +2 more sources
Diagnostic and therapeutic strategies for arrhythmogenic right ventricular dysplasia/cardiomyopathy patient. [PDF]
Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a rare inherited heart muscle disease characterized by ventricular tachyarrhythmia, predominant right ventricular dysfunction, and sudden cardiac death.
Wang W, James CA, Calkins H.
europepmc +2 more sources
Arrhythmogenic Right Ventricular Dysplasia in Neuromuscular Disorders [PDF]
Objectives Arrhythmogenic right ventricular dysplasia (ARVD) is a rare, genetic disorder predominantly affecting the right ventricle. There is increasing evidence that in some cases, ARVD is due to mutations in genes, which have also been implicated in ...
Josef Finsterer, Claudia Stöllberger
doaj +3 more sources

