Results 101 to 110 of about 113,935,104 (175)

Arylsulfatase activity in human urine: quantitative studies on patients with lysosomal disorders including metachromatic leukodystrophy

, 1972
A rapid and simple quantitative assay has been employed to measure the arylsulfatase A activity in urine samples from 173 individuals. This group includes three patients with late infantile metachromatic leukodystrophy (MLD), three patients with the ...
Thomas, G.H, Howell, R.R
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Effect of Pseudomonas Fluorescens on Isofetamid Dissipation and Soil Microbial Activity

Applied Sciences
The aim of this study was to assess the effect of Pseudomonas fluorescens (P) application on isofetamid (IS) dissipation; the number of specific genes of archaea, bacteria and ammonia-oxidizing bacteria (AOB); and the activity of β-Glucosidase ...
Urszula Wydro, Agata Jabłońska-Trypuć, Juraj Medo, Gabriel Borowski, Piotr Kaczyński, Bożena Łozowicka, Elżbieta Wołejko   +6 more
doaj   +1 more source

Identification of two novel arylsulfatase A mutations with a polymorphism as a cause of metachromatic leukodystrophy

, 2009
Objective: Metachromatic leukodystrophy is a lysosomal storage disorder caused by the deficiency of arylsulfatase A or saposin B.
Sinici, Incilay, Oezkara, H. Asuman, Oezkara, HATİCE ASUMAN, Soenmez, F. Muejgan, Oender, Evren, TOPÇU, MERAL   +5 more
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A study on enzyme activities of some sphingolipidoses

The Turkish Journal of Pediatrics, 1994
Enzyme activities were determined in fibroblast cell cultures of eight patients suspected of having a type of sphingolipidosis. The patients were 0 to 4 years of age; four were female and four were male.
H A Ozkara, M C Arikan, M Topçu, S Emre, Y Renda   +4 more
doaj  

Activity of urine arylsulfatase A in brain-dead graft donors is a predictor of early and late graft function

, 2017
<b>Objective:</b> Human lysosomal arylsulfatase A (ASA) is a member of the sulfatase family. Arylsulfatase A is required to degrade sulfatides. Sulfatides occur in the myelin sheets of the central and peripheral nervous system.
Kazimierz Ciechanowski, Krzysztof Safranow, Joanna Bober, Andrzej Pawlik, Leszek Domanski, Ewa Kwiatkowska   +5 more
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A systematic review on the birth prevalence of metachromatic leukodystrophy

Orphanet Journal of Rare Diseases
Background Metachromatic leukodystrophy (MLD) is an autosomal recessive lysosomal storage disease caused by deficiency in arylsulfatase A (ASA) activity arising primarily from ASA gene (ARSA) variants. Late-infantile, juvenile and adult clinical subtypes
Shun-Chiao Chang, Aurore Bergamasco, Mélanie Bonnin, Teigna Arredondo Bisonó, Yola Moride   +4 more
doaj   +1 more source

Arylsulfatase K, a Novel Lysosomal Sulfatase

, 2013
Wiegmann E, Westendorf E, Kalus I, Pringle TH, Lübke T, Dierks T. Arylsulfatase K, a Novel Lysosomal Sulfatase. Journal of Biological Chemistry. 2013;288(42):30019-30028.The human sulfatase family has 17 members, 13 of which have been characterized ...
Lübke, Torben ; https://orcid.org/, Westendorf, Eva, Kalus, Ina, Dierks, Thomas, Wiegmann, Elena, Pringle, Thomas H.   +5 more
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Biotechnological valorization of rice waste from Trichoderma production through the development of a streptomyces-based biological soil conditioner. [PDF]

Braz J Microbiol
Melo N, Nazari MT, Schommer VA, Ferrari V, Moraes CAM, Modolo RCE, Scariot FJ, Delamare APL, Brehm FA.   +8 more
europepmc   +1 more source

Understanding the Role of Deconjugation of Phase II Metabolites in Wastewater: Implications for Wastewater-Based Epidemiology. [PDF]

Environ Sci Technol
Elliss H, Hricova K, Griffiths E, Byrnes NA, Faill B, Hawkins E, Proctor K, Robertson M, Bagnall J, Kasprzyk-Hordern B.   +9 more
europepmc   +1 more source

The relationship of arylsulfatase C and the steroid sulfatases in mammals

, 1990
Arylsulfatases (arylsulfate sulfohydrolase, EC 3.1.6.1) catalyze the hydrolysis of the O-S bond of sulfate esters. Two types of arylsulfatases have been described based on their subcellular distribution and biochemical properties. Arylsulfatase C, a Type
Ruoff, Berthie Marie
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