Results 151 to 160 of about 1,234,995 (195)
Some of the next articles are maybe not open access.
Ivemark syndrome with asplenia in siblings
The Journal of Pediatrics, 1997We describe two siblings with Ivemark syndrome. In both cases, absent spleen, symmetric liver, and lungs with three lobes were associated with complex cardiac malformation. The syndrome was diagnosed prenatally in the second case by fetal echocardiography at the twentieth week of pregnancy.
I, Cesko +5 more
openaire +2 more sources
Immunologic study of the asplenia syndrome
The Pediatric Infectious Disease Journal, 1991Asplenia syndrome is usually associated with complex congenital cardiovascular defects. These patients often succumb to overwhelming infections. A complete immunological evaluation was therefore conducted on 13 consecutive patients with asplenia syndrome and 12 age-matched patients with congenital heart disease but without evident splenic problems. IgG,
Wang, Jou-Kou, Hsieh, Kue-Hsiung
openaire +2 more sources
Functional Asplenia in Sezary Syndrome
Clinical Nuclear Medicine, 1980A case of functional asplenia revealed by radiocolloid scanning is reported in a patient suffering from Sezary syndrome, a lymphoma of cutaneous origin. Heavy, diffuse sinusoidal infiltration of the spleen by the Sezary cells appears to be responsible for the functional asplenia in this case.
S, Balachandran, R, Kumar, T T, Kuo
openaire +2 more sources
Prophylactic gastropexy in the asplenia syndrome
Pediatric Surgery International, 1996The asplenia [Ivemark] syndrome (AS) is the association of congenital absence of the spleen with a variety of visceral abnormalities, predominantly of the cardiovascular system. Varying degrees of malrotation and malfixation of the bowel are common in this condition, and the occurrence of catastrophic gastric volvulus due to malfixation of the bowel ...
B O, Okoye +3 more
openaire +2 more sources
Acute Gastric Volvulus in a Child With Asplenia Syndrome
Pediatrics International, 2004Yen-Hsuan Ni, Ming-Tai Lin, Jou-Kou Wang
exaly +3 more sources
Southern Medical Journal, 1989
Congenital heart defects as a group represent a significant proportion of congenital malformations. Most are isolated and multifactorially determined; a relatively small proportion are due to a single gene defect, and result in an increased risk of recurrence among first-degree relatives. We have reported the cases of three male siblings with Ivemark's
R H, McChane +3 more
openaire +2 more sources
Congenital heart defects as a group represent a significant proportion of congenital malformations. Most are isolated and multifactorially determined; a relatively small proportion are due to a single gene defect, and result in an increased risk of recurrence among first-degree relatives. We have reported the cases of three male siblings with Ivemark's
R H, McChane +3 more
openaire +2 more sources
Prolonged and functional survival with the asplenia syndrome
The American Journal of Medicine, 1986Asplenia syndrome is a rare congenital complex of splenic agenesis, cardiac malformation, and malposition of the abdominal viscera. Prolonged functional survival is very uncommon, with death usually caused by severe infection or congestive heart failure.
M W, Wolfe +3 more
openaire +2 more sources
Radiographic Visceral Patterns in the Asplenia Syndrome
Radiology, 1973Abstract The postero-anterior chest and abdominal radiographs of 32 patients were evaluated; in each the asplenia syndrome had been proved at autopsy. Three basic visceral patterns are described: situs solitus, situs inversus, and situs ambiguus. The cardiovascular manifestations of symmetry are diagnosed only by angiocardiography or at necropsy.
R M, Freedom, K E, Fellows
openaire +2 more sources
Prenatal diagnosis of asplenia/polysplenia syndrome
American Journal of Obstetrics and Gynecology, 1988Complex congenital heart disease with atrioventricular block was detected prenatally in two fetuses at 34 and 28 weeks' gestation. The spleen was not seen on ultrasonographic examination in either fetus, suggesting polysplenia/asplenia syndrome. Both infants died shortly after delivery and the autopsies confirmed this diagnosis.
D, Chitayat +4 more
openaire +2 more sources
Extracardiac malformations in asplenia syndrome
Cardiology in the Young, 1992SummaryThe incidence and spectrum of extracardiac malformations in congenital asplenia syndrome were determined by review of43 cases (40 live-births) identified in the province of British Columbia over a 21 year period. Major extracardiac anomalies (excluding those of abnormal arrangement of the organs) were identified in nine cases (21%), and minor ...
Steven A. Webber +4 more
openaire +1 more source