Results 71 to 80 of about 1,234,995 (195)
ABSTRACT Background and Aims The polymerization of deoxygenated hemoglobin S, resulting from a genetic mutation in sickle cell disease (SCD), leads to damage in multiple organs, including renal, cardiopulmonary, and cerebrovascular systems. The liver is also commonly affected, resulting in “sickle cell liver disease,” which may lead to progressive ...
Josué Louokdom Simo +6 more
wiley +1 more source
Functional Asplenia and Microscopic (Collagenous) Colitis
A 54-year-old female presented with a pulmonary infection that resolved completely with antibiotic treatment. Peripheral blood films showed features characteristic of splenic hypofunction, and radiolabelling studies confirmed an absence of splenic ...
Hugh James Freeman
core +1 more source
Congenital asplenia (Ivemark syndrome) is usually associated with major cardiac malformations, which determine the clinical presentation and often result in death before 6 months of age.
Morel, Philippe +7 more
core +1 more source
Esophageal Varices in Congenital Heart Disease with Total Anomalous Pulmonary Venous Connection
Total anomalous pulmonary venous connection (TAPVC) is an uncommon congenital anomaly in which the anatomical presentations vary widely among patients.
李瑤華;吳美環;陳世杰 +1 more
core
Purpura fulminans – meningococcal infection or postsplenectomy sepsis
The article presents two clinical cases with description of peculiarities of septic infection occurred after splenectomy and due to congenital splenic hypoplasia.Decreased immune defense resulted from splenectomy leads to severe infections with a high ...
O. V. Samodova +4 more
doaj +1 more source
Splenic infarction may be the first sign of granulomatosis with polyangiitis: case reports
Granulamatous polyangiitis (GPA) is a rare systemic vasculitis that makes up most of the antineutrophilic cytoplasmic antibody (ANCA)-associated vasculitis (AAV). The disease is more likely to affect the upper and lower respiratory tract, kidney and skin.
D. Üsküdar Cansu +2 more
doaj +1 more source
Surgical Treatment for Asplenia Syndrome.
無脾症候群24例に対する外科治療の成績と Fontan 型手術 (以下F手術) に至る問題点について検討した. 24例中F手術の適応となったのは5例 (20.8%) であった. 11例に総肺静脈環流異常を合併しており, うち6例が肺静脈閉塞を呈していた. 4例に対して総肺静脈幹-心房吻合を施行したが, 手術成績は不良で, 4例中2例は手術死亡, 1例は遠隔死亡, 現在, 1例が生存中である.
Miyaji, Kagami +2 more
openaire +2 more sources
Heterotaxy syndrome, analysis of 13 cases and review of the literature
INTRODUCTION: Heterotaxy syndrome (Ivemark syndrome, or asplenia-polysplenia syndrome) is a heterogeneous group of disease with disturbed body symmetry and malposition of internal organs. Heterotaxy syndrome is caused by the disturbance of the left/right
Marton, Tamas +4 more
core +4 more sources
Pheochromocytoma in a patient with heterotaxy syndrome: a case report
Background Heterotaxy syndrome is a rare congenital condition characterized by abnormal arrangement of thoracoabdominal organs, often associated with complex cardiac and splenic anomalies. Pheochromocytoma is a rare neuroendocrine tumor that overproduces
Farid Farahani Rad +3 more
doaj +1 more source
Demonstration of presence of a sling between anterior and posterior bundle branch during tachycardia using twin atrioventricular nodes: A case of asplenia syndrome. [PDF]
Kinjo T +4 more
europepmc +1 more source

