Results 41 to 50 of about 10,531,467 (204)

Congenital Neutropenia in Children: Evaluation of Infectious Complications, Treatment Results and Long-Term Outcome

Journal of Behçet Uz Children's Hospital, 2021
Objective: Infections are an important cause of morbidity and mortality for patients with congenital neutropenia. In the present study, we report on the incidence, type, localization of documented infections, as well as the clinical features and long ...
Işık Odaman Al, Yeşim Oymak, Tuba Hilkay Karapınar, Melek Erdem, Salih Gözmen, Neryal Tahta, Sultan Okur Acar, ilknur Çağlar, Nuri Bayram, İlker Devrim   +9 more
doaj   +1 more source

Behçet’s Disease, Pathogenesis, Clinical Features, and Treatment Approaches: A Comprehensive Review

Medicina
Behçet’s disease is a systemic inflammatory disorder of unknown etiology. The disease manifests with diverse clinical symptoms, most commonly recurrent oral and genital ulcers, skin lesions, and uveitis, though it can affect multiple organ systems ...
S. Lavalle, Sebastiano Caruso, R. Foti, Caterina Gagliano, S. Cocuzza, L. La Via, F. Parisi, Christian Calvo-Henríquez, A. Maniaci   +8 more
semanticscholar   +1 more source

Multidetector Computed Tomographic Evaluation of the Normal Characteristics of the Thymus in the Pediatric Population

Journal of the Belgian Society of Radiology, 2022
Objectives: The objective of the present study was to determine the morphologic features and measurements of the normal thymus on contrast-enhanced multi-detector computed tomography (MDCT) in subjects from the newborn period up to 18 years of age ...
Edis Çolak, Behzat Özkan
doaj   +1 more source

Clinical features and long-term follow-up of patients with West syndrome: 5-year developmental outcomes

Trends in Pediatrics
Objectives: West syndrome (WS) is an early childhood epileptic encephalopathy characterized by spasms, typically occurring within the first year of life.
Yiğithan Güzin, Serdar Pekuz, Pakize Karaoğlu, İpek Burcu Parlak İbiş, Hatice Hilal Kırkgöz, Merve Yavuz, Aycan Ünalp, Ünsal Yılmaz   +7 more
doaj   +1 more source

Factors Associated with Neurodevelopmental Retardation in Preterm Infants: A Single-center Experience

Forbes Tıp Dergisi, 2022
Objective: Today, the survival rate of low-birth-weight infants has increased thanks to supportive care. However, various permanent health problems, especially neurodevelopmental retardation, can be seen in these infants. This study investigates the risk
Rüya ÇOLAK, Meltem KIVILCIM, Senem ALKAN ÖZDEMİR, Ezgi YANGIN ERGON, Sebnem ÇALKAVUR, Tülin GÖKMEN YILDIRIM   +5 more
doaj   +1 more source

Retractions in Rheumatology: Trends, Causes, and Implications for Research Integrity

Arthritis Care &Research, EarlyView.
Objective We aimed to describe the trends and main reasons for study retraction in rheumatology literature. Methods We reviewed the Retraction Watch database to identify retracted articles in rheumatology. We recorded the main study characteristics, authors’ countries, reasons for retraction, time from publication to retraction, and trends over time ...
Anna Maria Vettori, Michele Iudici
wiley   +1 more source

Discordance Between Patient and Physician Global Assessments in Early Systemic Sclerosis

Arthritis Care &Research, EarlyView.
Objective This study aims to identify factors associated with patient global assessment (PtGA) and physician global assessment (PhGA) and discordance between them in systemic sclerosis (SSc). Methods Data from adults with early SSc (<5 years) from the Collaborative National Quality and Efficacy Registry were included.
Ellen Romich, Alexis Ogdie, Alisa Stephens Shields, Peter A. Merkel, Shervin Assassi, Elana J. Bernstein, Andreea Bujor, Flavia V. Castelino, Lorinda Chung, Luke B. Evnin, Tracy M. Frech, Jessica K. Gordon, Melissa Griffith, Faye N. Hant, Monica L. Harding, Laura K. Hummers, Dinesh Khanna, Kimberly S. Lakin, Dorota J. Lebiedz‐Odrobina, Yiming Luo, Ashima Makol, Maureen D. Mayes, Zsuzsanna H. McMahan, Jerry Molitor, Duncan F. Moore, Julie Paik, Carrie Richardson, Brian Skaug, Ami A. Shah, Ankoor Shah, Virginia Steen, John M. VanBuren, Elizabeth R. Volkmann, Carleigh Zahn, Nora Sandorfi, for the CONQUER Investigators   +35 more
wiley   +1 more source

Common genetic susceptibility loci link PFAPA syndrome, Behçet’s disease, and recurrent aphthous stomatitis

Proceedings of the National Academy of Sciences of the United States of America, 2020
Significance In this report we identify genetic susceptibility variants for periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome, the most common periodic fever syndrome in children.
K. Manthiram, Silvia Preite, F. Dedeoğlu, S. Demir, S. Ozen, K. Edwards, S. Lapidus, Alexander E. Katz, H. Feder, M. Lawton, G. Licameli, P. Wright, J. Le, K. Barron, A. Ombrello, B. Barham, T. Romeo, Anne Jones, Hemalatha Srinivasalu, P. Mudd, R. DeBiasi, A. Gül, G. Marshall, O. Jones, S. Chandrasekharappa, Yuriy Stepanovskiy, P. Ferguson, P. Schwartzberg, E. Remmers, D. Kastner   +29 more
semanticscholar   +1 more source

Comparison of Sociodemographic Features Between Behçet Uveitis and Other Non-infectious Uveitis

Türk Oftalmoloji Dergisi, 2021
Objectives:To analyze and compare sociodemographic features between Behçet uveitis and other non-infectious uveitis.Materials and Methods:The data of adults with non-infectious uveitis in the nationwide uveitis database were analyzed and the ...
F. Nilüfer Yalçındağ, Pınar Çakar Özdal, Yılmaz Özyazgan, Figen Batıoğlu, İlknur Tugal-Tutkun   +4 more
doaj   +1 more source

An Aggregation‐Induced Polymerization Poly(Disulfide)‐Drug Nanoplatform for Autoimmune Uveitis Therapy via Inhibiting the cGAS‐STING Pathway

Advanced Science, EarlyView.
A cationic poly(disulfide)‐drug nanoplatform (LA/DexP) was developed to treat experimental autoimmune uveitis (EAU). With potent blood‐retinal barrier penetrability, LA/DexP releases DSP in response to high ROS and scavenges cfDNA to inhibit the cGAS‐STING signaling pathway.
Yuelan Wu, Wenbo Geng, Qinjin Dai, Wanyun Zhang, Yuxian Lai, Pei Zhang, Chunjiang Zhou, Yinuo Wang, Qingfeng Cao, Xiang Luo, Yujie Lai, Changwei Huang, Peizeng Yang   +12 more
wiley   +1 more source