Results 71 to 80 of about 23,822 (250)

Phenotypic and Genotypic Analysis of Two Rare Cases of ‐‐SEA/‐α4.3 HbH Disease

Journal of Clinical Laboratory Analysis, EarlyView.
We report two unrelated adult patients with rare deletional HbH disease (genotype ‐‐SEA/‐α4.3). This novel 4.3 kb deletion covering the HBA1 gene is accompanied by X‐Y‐Z segment recombination, which was identified by CycloneSEQ long‐read nanopore sequencing.
Weijia Yang, Xiaoyan Huang, Li Zhang, Xiaoqin Yang, Yaya Guo, Qingping Kang, Min Dou, Guijun Huang   +7 more
wiley   +1 more source

Cirrose biliar secundária em doente com histiocitose X.

Acta Médica Portuguesa, 2002
Histiocitose X or Histiocytosis of the Langerhans cells represents a complex spectrum of clinical alterations, resulting from infiltration by anomalous histiocytes of various organs, including the skin, bones, lungs, lymphatic ganglia and liver.
Zita Romão, J Pontes, P Andrade, M C Leitão, A Donato, Diniz Freitas   +5 more
doaj   +1 more source

Clinical Evaluation of the Effectiveness of Digital Peroral Cholangioscopy‐Guided Lithotripsy for Difficult Bile Duct Stones

Journal of Hepato-Biliary-Pancreatic Sciences, EarlyView.
ABSTRACT Background and Aims Peroral cholangioscopy‐guided lithotripsy (POCS‐L) has emerged as a treatment option for difficult bile duct stones (DBDSs), but detailed evidence remains limited. This study evaluated its effectiveness, safety, and risk factors for adverse events (AEs).
Hirohito Minami, Shuntaro Mukai, Takayoshi Tsuchiya, Reina Tanaka, Ryosuke Tonozuka, Kazumasa Nagai, Hiroyuki Kojima, Noriyuki Hirakawa, Kyoko Asano, Takao Itoi   +9 more
wiley   +1 more source

Biliary Cast Syndrome and Secondary Sclerosing Cholangitis in Critically Ill Patient after Long-Term Treatment in the Intensive Care Unit

Case Reports in Gastroenterology
Introduction: Secondary sclerosing cholangitis in critically ill patients (SSC-CIP) is a rare but underdiagnosed entity that occurs after life-threatening events and treatment in the intensive care unit (ICU).
Adnan Alkurdi, Johannes Herrmann, Damir Bikmukhametov, Rebecca Tschöpe   +3 more
doaj   +1 more source

Sclerosing Cholangitis in Behçet’s Disease

Case Reports in Medicine, 2013
Introduction. Sclerosing cholangitis is characterized by an inflammatory and fibrotic lesion of intra- and/or extrahepatic bile ducts. When a causal mechanism of a bile duct lesion is identified, the sclerosing cholangitis is considered secondary.
Aida Ben Slama Trabelsi, Dhilel Issaoui, Mehdi Ksiaa, Ahlem Souguir, Nadia Mama, Ahlem Brahem, Ali Jmaa, Salem Ajmi   +7 more
doaj   +1 more source

Hospital Volume and Operative Mortality in Pancreaticoduodenectomy and Hepatectomy: Analysis of the National Clinical Database in Japan

Journal of Hepato-Biliary-Pancreatic Sciences, EarlyView.
ABSTRACT Background/Purpose This study evaluated the association between institutional advanced hepatobiliary‐pancreatic (HBP) surgical volume and operative mortality for pancreaticoduodenectomy (PD) and advanced hepatectomy using data from the Japanese National Clinical Database.
Yoshitaro Shindo, Hideki Endo, Hiroyuki Yamamoto, Hidenori Takahashi, Shigeru Marubashi, Atsushi Nanashima, Itaru Endo, Hideki Ueno, Ken Shirabe, Masafumi Nakamura, Hiroaki Nagano, Masayuki Ohtsuka   +11 more
wiley   +1 more source

The Clinicopathological Characteristics and Prognosis of Cholangiolocarcinoma: A Multicenter Study With a Central Pathology Review

Journal of Hepato-Biliary-Pancreatic Sciences, EarlyView.
ABSTRACT Background Cholangiolocarcinoma (CLC) is a rare liver cancer with ≥ 80% ductular configuration (DC). Given its rarity, its clinicopathological characteristics remain poorly understood, and its status as a distinct disease entity remains controversial.
Takamichi Ishii, Kenta Makino, Etsuro Hatano, Mina Komuta, Jun Akiba, Yoshihiro Sakamoto, Shun‐Ichi Ariizumi, Goro Honda, Toru Hisaka, Yutaka Takeda, Akira Shimizu, Kentaro Yasuchika, Takashi Mizuno, Daisuke Asano, Atsushi Fujio, Naoto Gotohda, Chie Kitami, Koji Amaya, Hiroshi Sadamori, Manabu Kawai, Akiyoshi Nakakura, Masafumi Nakamura, Itaru Endo   +22 more
wiley   +1 more source

Pre‐Scan Breathing Pattern and Image Quality in Respiratory‐Triggered T2‐Weighted Liver MRI: Radial Versus Cartesian Fast Spin Echo

Journal of Magnetic Resonance Imaging, EarlyView.
ABSTRACT Background Respiratory‐triggered T2‐weighted imaging (T2WI) may use rectilinear sampling (respiratory‐triggered fast recovery fast spin echo [RT‐FRFSE]) or radial sampling (periodically rotated overlapping parallel lines with enhanced reconstruction [PROPELLER]). Their relative performance across breathing patterns is unclear.
Ho Sung Park, Jimi Huh, Kyungmin Lee, Hyun Seung Lee, Hyesun Park, Kyung Won Kim, Jai Keun Kim   +6 more
wiley   +1 more source

Cholecystoduodenal Fistula, Gallstone Ileus, and Choledocholithiasis: A Case Report and Literature Review. [PDF]

Clin Case Rep
ABSTRACT Prompt diagnosis using CT is critical in gallstone ileus, as symptoms are often nonspecific. A combined surgical approach—comprising enterolithotomy, cholecystectomy, and fistula repair—effectively addresses both the obstruction and its underlying source, achieving favorable outcomes even in complex presentations.
Ji J, Huang Y, Tang D, Wulamu W.
europepmc   +2 more sources

Portal vein peak systolic velocity is a useful noninvasive predictor of high‐risk varices in biliary atresia

Journal of Pediatric Gastroenterology and Nutrition, EarlyView.
Abstract Objectives Portal vein (PV) flow velocity is considered an indicator of portal hypertension. However, few studies have evaluated the predictive performance of PV flow velocity for high‐risk varices (HRV) in children with biliary atresia (BA). In this study, we evaluated the predictive performance of PV peak systolic velocity (PSV) for HRV in ...
Tomoya Fukuoka, Hiroyo Ishii, Emi Ito, Yuki Matsuoka, Yoshikazu Miura, Takeshi Kimura, Kazuhiko Bessho, Takehisa Ueno, Yasuji Kitabatake   +8 more
wiley   +1 more source