Results 51 to 60 of about 222,722 (307)
Correctable biliary atresia and cholangiocarcinoma: a case report of a 63-year-old patient
Surgical Case Reports, 2019 Background Although cancer occurrence following surgery for biliary atresia has gradually increased, the development of cholangiocarcinoma in a native liver survivor of biliary atresia is extremely rare.
Masaki Nio +5 more
doaj +1 more source
What to measure in biliary atresia research: study protocol for developing a core outcome set
BMJ Open, 2021 Aim Extrahepatic biliary atresia is a rare disorder. This creates challenges in the quality and quantity of research conducted. This issue is exacerbated by the potential heterogeneity in the reported outcomes in research examining the management of ...
Roy M Kimble +6 more
doaj +1 more source
Current Concepts of Biliary Atresia and Matrix Metalloproteinase-7: A Review of Literature
Frontiers in Medicine, 2020 Biliary atresia (BA) is a rare cholangiopathy of infancy in which the bile ducts obliterate, leading to profound cholestasis and liver fibrosis. BA is hypothesized to be caused by a viral insult that leads to over-activation of the immune system ...
M. Nomden +4 more
semanticscholar +1 more source
A genome-wide association study identifies a susceptibility locus for biliary atresia on 2p16.1 within the gene EFEMP1 [PDF]
, 2018 Biliary atresia (BA) is a rare pediatric cholangiopathy characterized by fibrosclerosing obliteration of the extrahepatic bile ducts, leading to cholestasis, fibrosis, cirrhosis, and eventual liver failure.
Bailey-Wilson, Joan E +12 more
core +2 more sources
대한영상의학회지, 2022 Biliary atresia is a progressive, idiopathic, obliterative disease of the extrahepatic biliary tree that presents with biliary obstruction in the neonatal period. It is the most common indication for liver transplantation in children.
Tae Yeon Jeon
doaj +1 more source
Mayo Clinic Proceedings, 1998 Extrahepatic biliary atresia is an obliterative cholangiopathy that involves all or part of the extrahepatic biliary tree and, in many cases, the intrahepatic bile ducts. In the United States, from 400 to 600 new cases of biliary atresia are encountered annually.
openaire +2 more sources
Novel NIR-II fluorescent probes for biliary atresia imaging
Acta Pharmaceutica Sinica B, 2023 Biliary atresia is a rare infant disease that predisposes patients to liver transplantation and death if not treated in time. However, early diagnosis is challenging because the clinical manifestations and laboratory tests of biliary atresia overlap with
Xiaodong Zeng +9 more
doaj
BMC Pediatrics, 2018 Background In biliary atresia, the disease process of obliterative cholangiopathy may begin in the perinatal period; however, no chronological evidence exists on how the cholangiopathy progresses to biliary obliteration.
Tsugumichi Koshinaga +4 more
doaj +1 more source
Embryonic Biliary Atresia in a Very-low-birth-weight Premature Infant
Journal of the Formosan Medical Association, 2007 Two major forms of biliary atresia, the embryonic and perinatal type, are considered to have different pathogeneses and distinct prognoses. Embryonic biliary atresia is associated with worse prognosis.
Hung-Wen Chen +6 more
doaj +1 more source
American Journal of Medical Genetics Part A, EarlyView.ABSTRACT Gastrointestinal defects and immunodeficiency syndrome 1 (GIDID1) is a rare autosomal recessive disorder caused by biallelic variants in TTC7A. GIDID1 is characterized by a broad clinical spectrum ranging from very early‐onset inflammatory bowel disease (VEOIBD) to multiple intestinal atresia (MIA) with or without immunological manifestations.
Julia Imhoff +8 more
wiley +1 more source