Results 51 to 60 of about 19,725 (236)
Embryonic Biliary Atresia in a Very-low-birth-weight Premature Infant
Journal of the Formosan Medical Association, 2007 Two major forms of biliary atresia, the embryonic and perinatal type, are considered to have different pathogeneses and distinct prognoses. Embryonic biliary atresia is associated with worse prognosis.
Hung-Wen Chen +6 more
doaj +1 more source
Seminars in Pediatric Surgery, 2000 Although the prognosis of biliary atresia has been dramatically improved in the era of liver transplantation, the Kasai operation is still the first line of surgical treatment. Successful hepatic portoenterostomy depends on early diagnosis and surgery, adequate surgical technique, prevention of cholangitis, and precise postoperative management.
M, Nio, R, Ohi
openaire +2 more sources
Biliary Atresia - Clinical Series [PDF]
GE - Portuguese Journal of Gastroenterology, 2017 <b><i>Introduction:</i></b> Biliary atresia is the main cause of death by hepatic failure and the main indication for liver transplant in children. This study aims to analyze the population with this diagnosis, treated between 2000 and 2015 at Hospital de São João.
Neto, Bárbara +4 more
openaire +4 more sources
American Journal of Medical Genetics Part A, EarlyView.ABSTRACT The rare X‐linked female‐restricted Hardikar syndrome (HDKR, OMIM # 301068) is characterized by multiple congenital anomalies including orofacial clefts, gastrointestinal, genitourinary, and cardiac anomalies, but cognitive and neurobehavioral development is rarely impaired.
Tinne Warmoeskerken +4 more
wiley +1 more source
American Journal of Medical Genetics Part A, EarlyView.ABSTRACT The ciliopathies are a group of genetic disorders caused by defective function of either the primary cilia (a large number) or the motile cilia (a much smaller number). These have been defined as diseases with mutations in genes encoding individual ciliary or cilia‐associated proteins.
Robert P. Erickson +1 more
wiley +1 more source
Journal of Zoonotic Diseases, 2023 Here we present a case of an infant with biliary atresia with bacteremia caused by Ciprofloxacin resistant C. jejuni. An eight-month-old boy - previously diagnosed with inoperable biliary atresia, was referred with fever.
Daniel Edbert +3 more
doaj +1 more source
Emergencies in neonatal management: jaundice and biliary atresia [PDF]
, 2016 Biliary atresia is a severe and progressive inflammatory process of unknown cause, which initially involves the extrahepatic bile ducts but which quickly proceeds towards the intrahepatic bile tree leading rapidly to biliary cirrhosis. Biliary atresia is
Clemente, Maria Grazia +1 more
core
Paediatric development of radiopharmaceutical imaging agents and radioligand therapeutics
British Journal of Clinical Pharmacology, EarlyView.Abstract This review focuses on the development of radiopharmaceutical imaging agents and radioligand therapeutics for paediatric use. Nuclear medicine plays an important role in the diagnosis and treatment of various childhood conditions, including cancers, infections and brain disorders.
Justin L. Hay +5 more
wiley +1 more source
Maternal regulation of biliary disease in neonates via gut microbial metabolites
Nature Communications, 2022 The pathogenesis of biliary atresia remains poorly understood. Here, the authors report that maternal butyrate treatment alters the gut microbiome and glutamine/hypoxanthine metabolites similar to human subjects, and suppresses biliary atresia in newborn
Jai Junbae Jee +23 more
doaj +1 more source
Diagnosis and treatment of biliary atresia in children
Медицина болю, 2022 . There are relatively few severe liver diseases in childhood. Biliary atresia is one of the most difficult. Early diagnosis of this disease is the basis of the subsequent treatment algorithm.
K Dmytriieva +3 more
doaj +1 more source