Results 31 to 40 of about 10,425 (178)
Nature Reviews Disease PrimersBiliary atresia (BA) is a progressive inflammatory fibrosclerosing disease of the biliary system and a major cause of neonatal cholestasis. It affects 1:5,000-20,000 live births, with the highest incidence in Asia. The pathogenesis is still unknown, but emerging research suggests a role for ciliary dysfunction, redox stress and hypoxia.
Siddiqui AI, Desai H, Ahmad T.
europepmc +3 more sources
Alagille Syndrome Mimicking Biliary Atresia in Early Infancy.
PLoS ONE, 2015 Alagille syndrome may mimic biliary atresia in early infancy. Since mutations in JAG1 typical for Alagille syndrome type 1 have also been found in biliary atresia, we aimed to identify JAG1 mutations in newborns with proven biliary atresia (n = 72). Five
Tomáš Dědič +5 more
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Diagnostic Imaging of Biliary Atresia
대한영상의학회지, 2022 Biliary atresia is a rare but significant cause of neonatal cholestasis. An early and accurate diagnosis is important for proper management and prognosis.
Haesung Yoon +3 more
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Majalah Kedokteran Andalas, 2009 AbstrakAtresia bilier merupakan penyakit yang jarang terjadi dan penyababnya belum diketahui secara pasti. Karakteristik dari penyakit ini adalah terjadinya inflamasi progresif pada duktus bilier sehingga terjadi obstruksi ekstrahepatal yang akhirnya ...
Julinar Julinar +2 more
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Correctable biliary atresia and cholangiocarcinoma: a case report of a 63-year-old patient
Surgical Case Reports, 2019 Background Although cancer occurrence following surgery for biliary atresia has gradually increased, the development of cholangiocarcinoma in a native liver survivor of biliary atresia is extremely rare.
Masaki Nio +5 more
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Hepatolithiasis in a 52-year-old native liver survivor with postoperative biliary atresia
Journal of Pediatric Surgery Case Reports, 2023 Hepatolithiasis is well known to be a late complication after biliary reconstruction. However, there were few reports regarding hepatolithiasis in late complications of long-term, native liver survivors in postoperative patients of biliary atresia. Here,
Kazuki Shirane +5 more
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What to measure in biliary atresia research: study protocol for developing a core outcome set
BMJ Open, 2021 Aim Extrahepatic biliary atresia is a rare disorder. This creates challenges in the quality and quantity of research conducted. This issue is exacerbated by the potential heterogeneity in the reported outcomes in research examining the management of ...
Roy M Kimble +6 more
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Differential diagnosis of neonatal cholestasis by genetic testing: A case report
Journal of Pediatric Surgery Case Reports, 2023 Introduction: Alagille syndrome (ALGS) is a cholestasis disorder with multiple organ dysfunction, including heart and kidney. The causative genes of ALGS are JAG1 and NOTCH2.
Sakura Kawahara +9 more
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Seminars in Pediatric Surgery, 2000 Although the prognosis of biliary atresia has been dramatically improved in the era of liver transplantation, the Kasai operation is still the first line of surgical treatment. Successful hepatic portoenterostomy depends on early diagnosis and surgery, adequate surgical technique, prevention of cholangitis, and precise postoperative management.
M, Nio, R, Ohi
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Surgery of Biliary Atresia [PDF]
Scandinavian Journal of Surgery, 2011 Biliary atresia (BA) is a progressive fibro-obliterative cholangiopathy of unclear etiology affecting varying degrees of both extra- and intrahepatic biliary tree resulting in obstructive bile flow and cholestasis in neonates. The diagnostic work-up is designed to diagnose or rule out BA without any unnecessary delay.
M P, Pakarinen, R J, Rintala
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