Results 21 to 30 of about 94,453 (216)
An investigation of the Ciliary Protein PKHD1 in Cyst development in liver disease: clues to the pathogenesis of Biliary Atresia [PDF]
, 2010 Biliary atresia is a common form of paediatric liver disease, with progressive, inflammatory obliteration of the biliary tree, leading to liver failure early in life.
Blair-Reid, Sarah Alexandra
core +7 more sources
Journal of Indian Association of Pediatric Surgeons, 2008 Biliary atresia (BA) is a cholangiodestructive disease affecting biliary tract, which ultimately leads to cirrhosis, liver failure and death if not treated. The incidence is higher in Asian countries than in Europe. Up to 10% of cases have other congenital anomalies, such as polysplenia, asplenia, situs inversus, absence of inferior vena cava and pre ...
Sinha, C.K., Davenport, Mark
openaire +5 more sources
Zdravniški Vestnik, 2013 Backg round: The objective of this study was to investigate the history, clinical, laboratory, imaging data and outcome of children with biliary atresia in Slovenia.
Petja Fister +4 more
doaj +1 more source
Long-term outcomes of the partial splenectomy for hypersplenism after portoenterostomy of patients with biliary atresia [PDF]
, 2021 Massive splenomegaly and hypersplenism in patients with biliary atresia after Kasai portoenterostomy were treated with partial splenic embolization or total splenectomy.
Makita, Satoshi +11 more
core +1 more source
Serum bile acids as a prognostic biomarker in biliary atresia following Kasai portoenterostomy
Hepatology, EarlyView., 2022 Serum bile acid levels predict outcomes in patients with biliary atresia who achieve normalized bilirubin levels after Kasai portoenterostomy. Abstract Background and Aims In biliary atresia, serum bilirubin is commonly used to predict outcomes after Kasai portoenterostomy (KP).
Sanjiv Harpavat +22 more
wiley +1 more source
Archives of Pediatric Gastroenterology, Hepatology, and Nutrition, 2022 Background: Biliary atresia (BA) is a progressive fibrosing obstructive cholangiopathy involving both the intrahepatic and extrahepatic biliary system; resulting in obstruction of bile flow and neonatal jaundice.
Ninung RD Kusumawati +5 more
doaj +1 more source
Pediatrics In Review, 2006 Biliary atresia (BA) is a rare disease characterised by a biliary obstruction of unknown origin that presents in the neonatal period. It is the most frequent surgical cause of cholestatic jaundice in this age group. BA occurs in approximately 1/18,000 live births in Western Europe.
Garret S, Zallen +4 more
openaire +7 more sources
Impacts of Early Kasai Portoenterostomy on Short‐Term and Long‐Term Outcomes of Biliary Atresia
Hepatology Communications, 2021 There are discrepancies regarding the clinical impact of age at Kasai portoenterostomy (KP) on surgical outcomes. Hence, we re‐assessed the clinical significance of age at KP.
Ryuji Okubo +3 more
doaj +1 more source
Current and emerging adjuvant therapies in biliary atresia
Frontiers in Pediatrics, 2022 Following Kasai hepatic portoenterostomy (HPE), most patients with biliary atresia will eventually require liver transplantation due to progressive cirrhosis and liver failure.
Scott C. Fligor +4 more
doaj +1 more source
Prognosis of Biliary Atresia Associated With Cytomegalovirus: A Meta-Analysis
Frontiers in Pediatrics, 2021 Objective: The etiology of biliary atresia is unclear, but viral infection has been implicated. The aim of the current meta-analysis was to investigate relationships between cytomegalovirus (CMV) and the prognosis of biliary atresia.Methods: PubMed ...
Yilin Zhao +8 more
doaj +1 more source