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Pediatrics In Review, 1989
Biliary atresia is a pathologic entity in which there is obliteration of some portion of the extrahepatic bile ducts. In the past, occlusion of the proximal ducts (at the liver hilus) was referred to as "noncorrectable" (Fig 1). If only the distal duct is occluded (and the proximal duct is patent), the lesion was referred to as "correctable." The ...
E A, Wanek +3 more
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Biliary atresia is a pathologic entity in which there is obliteration of some portion of the extrahepatic bile ducts. In the past, occlusion of the proximal ducts (at the liver hilus) was referred to as "noncorrectable" (Fig 1). If only the distal duct is occluded (and the proximal duct is patent), the lesion was referred to as "correctable." The ...
E A, Wanek +3 more
openaire +5 more sources
2021
Biliary Atresia (BA) affects approximately 1:20,000 babies and is the most frequent cause of surgical jaundice in children. BA presents in the first few weeks of life with pale stools and dark urine in otherwise healthy infants. It is the end result of a destructive inflammatory process of the bile ducts, with unclear origins.
Betalli P., Cheli M., D'Antiga L.
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Biliary Atresia (BA) affects approximately 1:20,000 babies and is the most frequent cause of surgical jaundice in children. BA presents in the first few weeks of life with pale stools and dark urine in otherwise healthy infants. It is the end result of a destructive inflammatory process of the bile ducts, with unclear origins.
Betalli P., Cheli M., D'Antiga L.
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Current Opinion in Pediatrics, 1997
Biliary atresia, a progressive obliterative process involving the bile ducts, has its onset in the newborn period. It is characterized by worsening cholestasis, hepatic fibrosis, and cirrhosis, which lead to portal hypertension and a decline in hepatic synthetic function. Untreated, the outcome is uniformly fatal.
W, Middlesworth, R P, Altman
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Biliary atresia, a progressive obliterative process involving the bile ducts, has its onset in the newborn period. It is characterized by worsening cholestasis, hepatic fibrosis, and cirrhosis, which lead to portal hypertension and a decline in hepatic synthetic function. Untreated, the outcome is uniformly fatal.
W, Middlesworth, R P, Altman
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Clinics and Research in Hepatology and Gastroenterology, 2012
Biliary atresia is an obliterative cholangiopathy with progressive hepatobiliary disease, starting from the perinatal period. With a frequency of 1/15-18,000 live births, biliary atresia is the commonest cause of life-threatening liver disease in infants, and fatal if untreated.
Ulrich, Baumann, Benno, Ure
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Biliary atresia is an obliterative cholangiopathy with progressive hepatobiliary disease, starting from the perinatal period. With a frequency of 1/15-18,000 live births, biliary atresia is the commonest cause of life-threatening liver disease in infants, and fatal if untreated.
Ulrich, Baumann, Benno, Ure
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Biliary atresia and biliary cysts
Baillière's Clinical Gastroenterology, 1997The authors present a review of the classification, aetiology, presentation, treatment and long-term outcome of children and adults with biliary atresia and choledochal cyst disease. Biliary atresia should be suspected in any infant with jaundice beyond the second week of life.
P A, Lipsett, D L, Segev, P M, Colombani
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Pediatrics, 1975
It is difficult for me to find fault with Dr. Lilly's presentation, especially since he refers to me as a fair-minded, clear-thinking man! Dr. Thaler and I concluded in 1968 that the chance of encountering a patient with operable atresia of the extrahepatic biliary ducts was so small that our primary obligation was to protect the infant ...
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It is difficult for me to find fault with Dr. Lilly's presentation, especially since he refers to me as a fair-minded, clear-thinking man! Dr. Thaler and I concluded in 1968 that the chance of encountering a patient with operable atresia of the extrahepatic biliary ducts was so small that our primary obligation was to protect the infant ...
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Etiopathogenesis of Biliary Atresia
Seminars in Liver Disease, 2001Biliary atresia, a progressive sclerosis of the extrahepatic biliary tree that occurs only within the first 3 months of life, is one of the most common causes of neonatal cholestasis and accounts for over half of children who undergo liver transplantation.
R J, Sokol, C, Mack
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Biliary atresia in the newborn
Journal of Pediatric Surgery, 1986A prenatal sonographic diagnosis of extrahepatic biliary atresia was made and, 76 hours after birth, operatively confirmed. A standard Kasai operation was performed, with the exception of the use of an ancillary appendiceal conduit to provide biliary drainage of an independent bile duct draining the right anterior hepatic segment.
S K, Greenholz +3 more
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Current Opinion in Gastroenterology, 2019
Biliary atresia is a poorly understood deadly disease. Genetic predisposition factors are suspected albeit not firmly established. This review summarizes recent evidence of genetic alterations in biliary atresia.Whole-genome association studies in biliary atresia patients identified four distinct predisposition loci with four different genes ...
Muriel, Girard, Ganna, Panasyuk
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Biliary atresia is a poorly understood deadly disease. Genetic predisposition factors are suspected albeit not firmly established. This review summarizes recent evidence of genetic alterations in biliary atresia.Whole-genome association studies in biliary atresia patients identified four distinct predisposition loci with four different genes ...
Muriel, Girard, Ganna, Panasyuk
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