Caroli syndrome, which is characterized by saccular and fusiform dilatation of the biliary ducts, is usually observed in association with autosomal recessive polycystic kidney disease (ARPKD).
Amanda Rivas +4 more
doaj +4 more sources
Caroli Disease (Clinical Observation) [PDF]
The incidence of Caroli disease is estimated to be 1 case per 1 million people; as a result, there are very few available clinical observations. At the moment, the treatment of Caroli disease is limited to symptomatic therapy and the prevention of ...
I. G. Nikitin +8 more
doaj +2 more sources
Pediatric segmental Caroli disease: A case report and review of the literature
Introduction: Caroli disease is a rare congenital disorder causing nonobstructive segmental dilatation of intrahepatic bile ducts. Caroli disease can affect the liver diffusely or be confined to a single segment or lobe, although localized Caroli disease
Donna C. Koo +7 more
doaj +2 more sources
Open resection of gastroduodenal artery aneurysm with fistulization into the duodenum 17 years after coil embolization in a patient with Caroli disease [PDF]
Gastroduodenal artery aneurysm (GDAA) is a very rare vascular condition with a high risk of fatal rupture. Coil embolization is the recommended treatment for GDAA.
Shreef Said, MD +5 more
doaj +2 more sources
Caroli disease combined with Banti syndrome in a woman: a case report [PDF]
Caroli disease is a rare congenital malformation that predisposes to segmental cystic dilatation of the intrahepatic bile ducts. Banti syndrome is characterized by persistent splenomegaly due to chronic congestion, resulting in a low hematocrit and ...
Shian Yu, Hang Yuan, Yong Cao
doaj +2 more sources
Caroli disease incidentally discovered in a 23-years old male: A case report [PDF]
This case report describes a 23-year-old male who was incidentally diagnosed with Caroli disease while investigating symptoms of recurrent upper quadrant pain and fever.
Luis F. Bonilla Larrama +4 more
doaj +2 more sources
Imaging diagnosis of Caroli-like disease with concurrent extrahepatic biliary obstruction in a young small-breed dog: case report [PDF]
Caroli-like disease is a rare congenital ductal plate malformation characterized by intrahepatic bile duct dilatation and has only rarely been reported in veterinary medicine.
Jinkyung Park +6 more
doaj +2 more sources
Caroli disease: an update on pathogenesis [PDF]
Wen Shi, Ai-Ming Yang, Yuanyuan Ji
doaj +2 more sources
Compound heterozygous WDR19 variants associated with nephronophthisis, Caroli disease, refractory epilepsy and congenital bilateral central blindness: Case report [PDF]
The WDR19 gene has been reported to be involved in nephronophthisis-related ciliopathies such as isolated nephronophthisis 13 (NPHP13), Sensenbrenner syndrome, Jeune syndrome, Senior-Loken syndrome, Caroli disease, retinitis pigmentosa and ...
Xianglian Tang +7 more
doaj +2 more sources
Liver Transplantation for Caroli Disease [PDF]
Caroli disease is a rare congenital disorder characterized by multifocal, segmental dilatation of intrahepatic bile ducts. Patients with Caroli disease who have recurrent bouts of biliary infection, particularly those who also have complications related ...
M Zahmatkeshan +4 more
doaj +1 more source

