Results 21 to 30 of about 4,879,457 (188)
Hepatobiliary langerhans cell histiocytosis mimicking Caroli syndrome and recurring in a liver allograft [PDF]
Frontiers in MedicineLangerhans cell histiocytosis (LCH) involving the hepatobiliary system can progress to sclerosing cholangitis and cirrhosis and may require liver transplantation (LT).
Tingting Hu +3 more
doaj +2 more sources
Diagnosis of Caroli Disease with Gadoxetic Acid-Enhanced Magnetic Resonance Imaging
Current Research in MRICaroli disease (CD) is a condition in which there are multiple cystic dilations of the bile ducts within the liver that are present from birth. In this case report, we present the imaging findings of a 33-year-old woman who was diagnosed noninvasively ...
Ramazan Orkun Önder +2 more
doaj +2 more sources
Clinical outcomes of liver transplantation in Caroli syndrome: a retrospective analysis [PDF]
Orphanet Journal of Rare DiseasesObjective To evaluate the clinical outcomes of liver transplantation (LT) in patients with Caroli syndrome. Methods We retrospectively analyzed clinical data from 20 patients diagnosed with Caroli syndrome who underwent LT at Beijing Friendship Hospital,
Fei Hou +11 more
doaj +2 more sources
Indian Journal of Gastroenterology, 2013 Caroli’s disease, also known as congenital communicating cavernous ectasia of the biliary tree, is a rare autosomal recessive developmental abnormality characterized by saccular dilatation of the intrahepatic bile ducts. The magnetic resonance (MR) images shown here are from a 21-year-old man who presented with jaundice, abdominal pain, and fever for 5
Pratibha, Issar, Sanjeev Kumar, Issar
openaire +3 more sources
CAROLI DISEASE AND CAROLI SYNDROME [PDF]
Medical Journal Armed Forces India, 1999 Caroli syndrome consists of Caroli disease and congenital hepatic fibrosis [1]. It is an uncommon congenital disorder of the intrahepatic bile ducts. The disease is presumably of autosomal recessive hereditary character [2]. A classical case history of the Caroli syndrome is presented. Non surgical management with endoprosthesis is discussed.
Man Mohan, Harjai +5 more
openaire +2 more sources
Medical Journal Armed Forces India, 2007 Caroli's disease is a rare congenital disorder of the liver characterized by saccular or fusiform dilatation of the intrahepatic biliary ducts. In majority the transmission is autosomal recessive [1] but autosomal dominant inheritance has also been reported [2].
N K, Biswas, U, Raju, K, Sodhi
openaire +2 more sources
Monolobar Caroli's disease [PDF]
HPB, 2009 Caroli's disease (CD) is defined as the segmental dilatation of the intrahepatic bile ducts, which is generally diffuse throughout the liver, but may occasionally involve a single lobe, most commonly the left.1 We report the case of a 78-year-old male with recurrent cholangitis due to left monolobar CD.
Jarry, Julien, Saric, Jean
openaire +2 more sources
Caroli syndrome associated with atrial septal defect and polydactyly: a case report
Journal of Medical Case Reports, 2023 Introduction Caroli disease is multifocal segmental dilatation of the large intrahepatic bile ducts that connect to the main duct. It is considered a rare disease with an incidence rate of 1 in 1,000,000 births.
Ali Ghassa, Lina Khouri
doaj +1 more source
The Indian Journal of Pediatrics, 2006 Caroli's disease is a rare congenital disorder and occasional cases have been reported from Japan and other parts of Asia. It comprises of congenital dilation of the lower (segmental) intrahepatic bile duct. Cholangitis liver, cirrhosis and cholangiocarcinoma are its potential complication.
Ashish K, Gupta +3 more
+7 more sources
Laparoscopic Hepp Couinaud for the treatment of Caroli's disease: A case report
Ciencia y Salud, 2023 Caroli disease is a rare congenital disorder characterized by dilatation of intrahepatic bile ducts. The treatment could correspond to hepatic resection for localized disease.
Mohamad Hamaoui +5 more
doaj +1 more source