Results 141 to 150 of about 2,418 (178)
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Annual Review of Physiology, 2000
▪ Abstract In contrast to the airways, the defects in colonic function in cystic fibrosis (CF) patients are closely related to the defect in CFTR. The gastrointestinal phenotype of CF transgenic mice closely resembles the phenotype in CF patients, which clearly indicates the crucial role of CFTR in colonic Cl− secretion and the absence of an ...
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▪ Abstract In contrast to the airways, the defects in colonic function in cystic fibrosis (CF) patients are closely related to the defect in CFTR. The gastrointestinal phenotype of CF transgenic mice closely resembles the phenotype in CF patients, which clearly indicates the crucial role of CFTR in colonic Cl− secretion and the absence of an ...
openaire +3 more sources
Expanding CFTR Modulator Testing to Carriers of CFTR Variants
Annals of the American Thoracic Society, 2021Preston E, Bratcher, Pamela L, Zeitlin
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Mechanism of CFTR correction by type I folding correctors
Cell, 2022Karol Fiedorczuk, Jue Chen
exaly
Evaluation of Fused Pyrrolothiazole Systems as Correctors of Mutant CFTR Protein
Molecules, 2021Alessandra Montalbano +2 more
exaly
ECFS standards of care on CFTR-related disorders: Updated diagnostic criteria
Journal of Cystic Fibrosis, 2022Kevin Southern +2 more
exaly
Modulators of CFTR. Updates on clinical development and future directions
European Journal of Medicinal Chemistry, 2021Anita Golec +2 more
exaly
The Impact of Highly Effective CFTR Modulators on Growth and Nutrition Status
Nutrients, 2021Rosara Bass, Jefferson N Brownell
exaly
Phenotyping of Rare CFTR Mutations Reveals Distinct Trafficking and Functional Defects
Cells, 2020Ricard Farré +2 more
exaly