Results 61 to 70 of about 4,207,342 (185)

Expert Consensus on the Diagnosis and Monitoring of Paroxysmal Nocturnal Hemoglobinuria (PNH): An Algorithmic Approach in an Era of New Treatments

European Journal of Haematology, EarlyView.
ABSTRACT Paroxysmal nocturnal hemoglobinuria (PNH) is a rare hematologic disorder caused by a defect of glycosylphosphatidyl‐anchored proteins, leading to an uncontrolled complement‐mediated hemolysis. The advent of complement inhibitors in clinical practice radically changed patients' outcomes and survival.
Bruno Fattizzo, Monia Marchetti, Elisa Cannizzo, Arianna Gatti, Massimo Geuna, Anna Paola Iori, Maddalena Raia, Simona Sica, Francesco Buccisano   +8 more
wiley   +1 more source

Safety and efficacy of endovascular patent foramen ovale closure: the first results of a Russian multicenter study

Неврология, нейропсихиатрия, психосоматика, 2020
Patent foramen ovale (PFO) is detectable in more than 25% of the adult population and is generally clinically insignificant. However, it can be a cause of paradoxical embolism in some cases.
D. V. Ognerubov, A. S. Tereshchenko, A. N. Samko, G. К. Arutyunyan, O. A. Sivakova, D. V. Pevzner, M. I. Makeev, T. V. Balakhonova, A. V. Belopasova, M. Yu. Maksimova, S. E. Chuprina, E. P. Khodyakova, A. A. Kulesh, S. A. Mekhryakov, D. Yu. Shchekochikhin, A. A. Bogdanova, E. V. Merkulov   +16 more
doaj   +1 more source

Cisterna Chyli Dilation Is a Risk Factor for Liver Nodules and Hepatocellular Carcinoma in Fontan‐Associated Liver Disease: Pathophysiological Role of Lymphatic Dysfunction

Hepatology Research, EarlyView.
ABSTRACT Aim In Fontan‐associated liver disease (FALD), chronic congestion often confounds conventional fibrosis markers, complicating surveillance for hepatocellular carcinoma (HCC). Although lymphatic dysfunction is fundamental to Fontan physiology, its contribution to hepatocarcinogenesis remains unclear.
Koji Imoto, Masatake Tanaka, Takeshi Goya, Yuuki Azuma, Tomonobu Hioki, Yusuke Morita, Keisuke Sakaguchi, Nobuhiro Fujita, Takamori Kakino, Ayako Ishikita, Kenichiro Yamamura, Ichiro Sakamoto, Kousei Ishigami, Kohtaro Abe, Yoshihiro Ogawa   +14 more
wiley   +1 more source

Transcribing speech: errors in corpora and experimental setting

, 2007
Transcription of speech is often driven by different transc ribers’ understanding strategies, leading to specif ic error typologies (Chiari, 2006a; Chiari, 2006b; Lindsay and O’Connell, 1995; Pallaud, 2002; Pa llaud, 2003).
CHIARI, ISABELLA
core  

Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case report

International Medical Case Reports Journal, 2011
Minji Jennifer Kim1, Yong Suk Jo2, Jee Hyun Kim2, Yong-Jin Kim3, Kyung Hwan Kim4, Eun Bong Lee2, Yeong Wook Song2, Eun Young Lee21School of Medicine, University of Manchester, Manchester, UK; 2Division of Rheumatology, 3Division of Cardiology, Department
Kim MJ, Jo YS, Kim JH, Kim YJ, Kim KH, Lee EB, Song YW, Lee EY   +7 more
doaj  

De novo syrinx formation in a patient with Type I Chiari malformation: Case report and review of the literature

Journal of Craniovertebral Junction and Spine, 2018
This report highlights the case of a 56-year-old woman with an incidental type I Chiari malformation who on initial presentation had no associated cervical syrinx on magnetic resonance imaging (MRI), but who on subsequent MRI 8 years later was found to ...
David Stewart-Watson, Prynk Sinha, Thomas A Carroll   +2 more
doaj   +1 more source

Taxonomic and methodological biases in saproxylic beetles: Body size, trophic group and detection probability

Insect Conservation and Diversity, EarlyView.
Smaller saproxylic beetle species are described later and appear later in georeferenced databases, demonstrating a persistent body‐size bias that contributes to Linnean and Wallacean shortfalls. Trophic group, not body size, is the primary driver of detection probability in standardised flight‐trap surveys, with sapro‐xylophagous species detected most ...
Markus Franzén, Nicklas Jansson, Mustafa Avci, Antoine Brin, Hervé Brustel, Jan Budka, Jörn Buse, Giuseppe Carpaneto, Stefano Chiari, Lukáš Čížek, Mustafa Coskun, Jeremy Dagley, Peter M. Hammond, Estefanía Micó, Tuğba Öncül Abacıgil, Tomáš Pavlíček, Jiří Schlaghamerský, Pavel Šebek, Anne Sverdrup‐Thygeson, Sakin Vural Varli, Lars Westerberg, Inge Wilde, Agnese Zauli, Per Milberg   +23 more
wiley   +1 more source

Malformación de Arnold Chiari tipo I. Presentación de un caso Arnold-Chiari malformation Type I. Presentation of a case

Revista Médica Electrónica, 2010
La malformación de Arnold Chiari es una rara enfermedad incapacitante que afecta al 0,5 % de la población, siendo el 80 % mujeres. La hidrocefalia resultante es causada por el exceso de líquido cefalo raquídeo en el sistema ventricular, o por una falta ...
Ihosvany Ruiz Hernández, Antonis Cano Soler   +1 more
doaj  

When Virchow's law fails: Crouzon syndrome as a test case for quantitative suture closure–endocranial shape relationships

Journal of Anatomy, EarlyView.
Crouzon syndrome shows preserved intracranial volume but profoundly altered endocranial shape, with disrupted allometric coupling relative to controls. Treating calvarial suture patency as a continuous, age‐adjusted variable reveals strong system‐level covariation with endocranial morphology, effects invisible to conventional categorical suture scoring.
F. W. R. Steup, E. V. Groenenboom, O. Delassus, A. Balzeau, A. Profico, G. Paternoster, M. Moazen, R. H. Khonsari, L. S. Van De Lande, M. Taverne   +9 more
wiley   +1 more source

A frontal lobe mass in a 6‐year‐old girl

Brain Pathology, EarlyView.
Francesca S. Vacca, Aaron Mochizuki, Smruti K. Patel, Blaise Jones, Somak Roy, Kirti Gupta   +5 more
wiley   +1 more source