Results 1 to 10 of about 421,652 (362)

Left Ventricular Physiology and Ventricular‐Vascular Interactions in Young Patients After Heart Transplantation

Journal of the American Heart Association: Cardiovascular and Cerebrovascular Disease, 2023
Background In patients after heart transplantation, systemic arterial hypertension and enhanced central aortic stiffness contribute to increased ventricular afterload, which might lead to graft dysfunction.
Heiner Latus, Ramona Raap, Karin Klingel, Christoph Happel, Axel Moysich, Markus Khalil, Gunter Kerst, Jakob Milla, Susanne Skrzypek, Josef Thul, Christian Jux, Dietmar Schranz, Christian Apitz   +12 more
doaj   +1 more source

Pulmonary hypertension— a novel phenotypic hypothesis of Kabuki syndrome: a case report and literature review

BMC Pediatrics, 2023
Background Pediatric pulmonary hypertension (PH) is a serious and rare disease that is often derived from genetic mutations. Kabuki syndrome (KS) is a chromosomal abnormality disease that has its origin in the mutation of lysine methyltransferase 2D ...
Xiao-xian Deng, Bo-wen Jin, Shan-shan Li, Hong-mei Zhou, Qun-shan Shen, Yun-yan Li   +5 more
doaj   +1 more source

Wearable cardioverter-defibrillator (life-vest): A feasible bridging treatment in adult congenital heart disease

Indian Pacing and Electrophysiology Journal, 2022
Background: Wearable cardioverter-defibrillators (WCDs) are currently used in patients at temporarily heightened risk for sudden cardiac death (SCD) who are temporarily unable to receive an implantable cardioverter-defibrillator (ICD).
Berardo Sarubbi, Michela Palma, Assunta Merola, Flavia Fusco, Anna Correra, Diego Colonna, Emanuele Romeo, Nicola Grimaldi, Giovanni Domenico Ciriello, Giancarlo Scognamiglio, Maria Giovanna Russo   +10 more
doaj   +1 more source

Subcutaneous implantable cardioverter defibrillator in complex adult congenital heart disease. Results from the S-ICD “Monaldi Care” registry

International Journal of Cardiology Congenital Heart Disease, 2021
Background: Implantable cardioverter defibrillators (ICD) are widely accepted therapy in congenital heart disease (CHD) patients at risk of life-threatening ventricular arrhythmias or sudden cardiac death (SCD).
Berardo Sarubbi, Anna Correra, Diego Colonna, Emanuele Romeo, Michela Palma, Assunta Merola, Michele D'Alto, Giancarlo Scognamiglio, Flavia Fusco, Rosaria Barracano, Nunzia Borrelli, Nicola Grimaldi, Antonio D'Onofrio, Maria Giovanna Russo   +13 more
doaj   +1 more source

Where the congenital heart disease meets the pulmonary arterial hypertension, FLNA matters: a case report and literature review

BMC Pediatrics, 2020
Background Pediatric patients with genetic disorders have a higher incidence of pulmonary arterial hypertension (PAH) regardless of their heart defects. Filamin A (FLNA) mutation is recently recognized to be associated with pediatric pulmonary disorders,
Xiaoxian Deng, Shanshan Li, Qiu Qiu, Bowen Jin, Menghuan Yan, Yuanpin Hu, Yang Wu, Hongmei Zhou, Gangcheng Zhang, Xuan Zheng   +9 more
doaj   +1 more source

Overview of Long-Term Outcome in Adults with Systemic Right Ventricle and Transposition of the Great Arteries: A Review

Diagnostics, 2023
The population of patients with a systemic right ventricle (sRV) in biventricular circulation includes those who have undergone an atrial switch operation for destro-transposition of the great arteries (d-TGA) and those with congenitally corrected ...
Francesca Bevilacqua, Giulia Pasqualin, Paolo Ferrero, Angelo Micheletti, Diana Gabriela Negura, Angelo Fabio D’Aiello, Alessandro Giamberti, Massimo Chessa   +7 more
doaj   +1 more source

Bile acid predicts congenital portosystemic venous shunt in patients with pulmonary arterial hypertension

European Journal of Medical Research, 2023
The etiology of pulmonary arterial hypertension (PAH) is complex, especially the investigation of rare pathogeny is difficult. Congenital portosystemic venous shunt (CPSS) is a rare congenital anomaly in which the portal blood completely or partially ...
Yunyan Li, Xiaoxian Deng, Hongmei Zhou, Xuan Zheng, Gangcheng Zhang, Qingfeng Xiong   +5 more
doaj   +1 more source

Coarctation of the Aorta: Diagnosis and Management

Diagnostics, 2023
Coarctation of the aorta (CoA) accounts for approximately 5–8% of all congenital heart defects. Depending on the severity of the CoA and the presence of associated cardiac lesions, the clinical presentation and age vary.
Sadaf Raza, Suneil Aggarwal, Petra Jenkins, Ahmed Kharabish, Shehab Anwer, Damien Cullington, Julia Jones, Jaspal Dua, Vasileios Papaioannou, Reza Ashrafi, Sarah Moharem-Elgamal   +10 more
doaj   +1 more source

Protein-losing enteropathy in Fontan circulation: Pathophysiology, outcome and treatment options of a complex condition

International Journal of Cardiology Congenital Heart Disease, 2022
Protein-losing enteropathy (PLE) represents a rare but severe and potentially life-threatening complication following Fontan operation in patients with a functional single ventricle.
Rosaria Barracano, Assunta Merola, Flavia Fusco, Giancarlo Scognamiglio, Berardo Sarubbi   +4 more
doaj   +1 more source

Imaging of ventricular septal defect: Native and post-repair

International Journal of Cardiology Congenital Heart Disease, 2022
Cardiac imaging using a combination of multiple modalities has become an essential tool in the management of adults with congenital heart disease with the potential to improve the outcome.
Flavia Fusco, Nunzia Borrelli, Michela Palma, Berardo Sarubbi, Giancarlo Scognamiglio   +4 more
doaj   +1 more source