Congenital Long QT Syndrome: a Systematic Review [PDF]
Congenital long QT syndrome (LQTS) is a disorder of myocardial repolarization defined by a prolonged QT interval on electrocardiogram (ECG) that can cause ventricular arrhythmias and lead to sudden cardiac death.
Edvard Galić +7 more
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Management of Congenital Long-QT Syndrome: Commentary From the Experts. [PDF]
Supplemental Digital Content is available in the text. While published guidelines are useful in the care of patients with long-QT syndrome, it can be difficult to decide how to apply the guidelines to individual patients, particularly those with ...
Kaufman ES +23 more
europepmc +4 more sources
Diagnostic Accuracy of the Standing Test in Adults Suspected for Congenital Long-QT Syndrome. [PDF]
Background An elegant bedside provocation test has been shown to aid the diagnosis of long‐QT syndrome (LQTS) in a retrospective cohort by evaluation of QT intervals and T‐wave morphology changes resulting from the brief tachycardia provoked by standing.
Vink AS +10 more
europepmc +2 more sources
QT Adaptation and Intrinsic QT Variability in Congenital Long QT Syndrome [PDF]
Background Increased variability of QT interval (QTV) has been linked to arrhythmias in animal experiments and multiple clinical situations. Congenital long QT syndrome (LQTS), a pure repolarization disease, may provide important information on the ...
Srikanth Seethala +5 more
doaj +2 more sources
Congenital Long QT Syndrome, Coinciding With Cavitary Mycobacterium avium Lung Infection, Led to Cardiac Arrest [PDF]
Congenital long QT syndrome is a cardiac disorder leading to arrhythmias and sudden cardiac death. We present a case of a 55-year-old woman with altered mental status experiencing cardiac arrest caused by congenital long QT syndrome, coincidentally found
Muhammad Ghallab, MD +5 more
doaj +2 more sources
Congenital long QT syndrome [PDF]
Congenital long QT syndrome (LQTS) is a hereditary cardiac disease characterized by a prolongation of the QT interval at basal ECG and by a high risk of life-threatening arrhythmias. Disease prevalence is estimated at close to 1 in 2,500 live births. The
Celano Giuseppe +3 more
doaj +2 more sources
Clinical Advances in Congenital Long QT Syndrome
. Long QT syndrome is an inherited arrhythmia characterized by a prolonged QT interval and increased risk of life-threatening cardiac events, including arrhythmogenic syncope, seizures, and sudden cardiac death with a structurally normal heart. Since its
Kun Li +3 more
doaj +2 more sources
Diagnosis, management and therapeutic strategies for congenital long QT syndrome. [PDF]
Congenital long QT syndrome (LQTS) is characterised by heart rate corrected QT interval prolongation and life-threatening arrhythmias, leading to syncope and sudden death.
Wilde AAM, Amin AS, Postema PG.
europepmc +2 more sources
Congenital Long QT Syndrome in Children and Adolescents: A General Overview. [PDF]
Congenital long QT syndrome (LQTS) represents a disorder of myocardial repolarization characterized by a prolongation of QTc interval on ECG, which can degenerate into fast polymorphic ventricular arrhythmias. The typical symptoms of LQTS are syncope and
Balestra E +6 more
europepmc +2 more sources
A deep learning approach identifies new ECG features in congenital long QT syndrome. [PDF]
Congenital long QT syndrome (LQTS) is a rare heart disease caused by various underlying mutations. Most general cardiologists do not routinely see patients with congenital LQTS and may not always recognize the accompanying ECG features.
Aufiero S +8 more
europepmc +2 more sources

