Predicting Loss of Ambulation in Limb Girdle Muscular Dystrophy R9
ABSTRACT Background Limb girdle muscular dystrophy type R9 (LGMDR9) results from biallelic variants in FKRP. There is limited data to predict loss of ambulation (LOA) among those with LGMDR9. Methods Participants in an ongoing dystroglycanopathy natural history study (NCT00313677) with FKRP variants who had achieved ambulation and were more than 3 ...
Chandra L. Miller +6 more
wiley +1 more source
Lower limb exoskeleton robot and its cooperative control: A review, trends, and challenges for future research. [PDF]
Masengo G +5 more
europepmc +1 more source
ABSTRACT Objective To delineate specific in vivo white matter pathology in neuronal intranuclear inclusion disease (NIID) using diffusion spectrum imaging (DSI) and define its clinical relevance. Methods DSI was performed on 42 NIID patients and 38 matched controls.
Kaiyan Jiang +10 more
wiley +1 more source
Effects of Conductive Materials on Anaerobic Digestion of Polysaccharides and Proteins
Anaerobic digestion is a promising technology for the resource recovery from sewage and organic solid waste. Recent studies have shown that conductive materials can enhance anaerobic digestion, but their specific effects on different types of substrates ...
Muxiang LIANG +7 more
doaj +1 more source
Simultaneous Recognition and Separation of Organic Isomers Via Cooperative Control of Pore-Inside and Pore-Outside Interactions. [PDF]
Xue S +6 more
europepmc +1 more source
The international stock pollutant control: a stochastic formulation [PDF]
In this paper we provide a stochastic dynamic game formulation of the economics of international environmental agreements on the transnational pollution control when the environmental damage arises from stock pollutant that accumulates, for accumulating ...
Omar J. Casas, Rosario Romera
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Value of MRI Outcomes for Preventive and Early‐Stage Trials in Spinocerebellar Ataxias 1 and 3
ABSTRACT Objective To examine the value of MRI outcomes as endpoints for preventive and early‐stage trials of two polyglutamine spinocerebellar ataxias (SCAs). Methods A cohort of 100 participants (23 SCA1, 63 SCA3, median Scale for the Assessment and Rating of Ataxia (SARA) score = 5, 42% preataxic, and 14 gene‐negative controls) was scanned at 3T up ...
Thiago J. R. Rezende +26 more
wiley +1 more source
In this work, a CdTe@TiO2 single atoms (SAs) catalysts is successfully synthesized, realizing unique portion of nonbonding oxygen‐coordinated configuration of Cd─O─Te dimers coupling.
Yihang Zhang +5 more
doaj +1 more source
Event-Triggered Finite-Time Attitude Cooperative Control for Multiple Unmanned Aerial Vehicles. [PDF]
Han Q, Zhou Y, Liu X, Tuo X.
europepmc +1 more source
Evidence of Iron Accumulation in Cerebral Adrenoleukodystrophy: A Potential Novel Disease Mechanism
ABSTRACT In this first application of Quantitative Susceptibility Mapping Source Separation to cerebral adrenoleukodystrophy, we uncovered alterations in iron and myelin within lesions and normal appearing white matter. As validation, we demonstrate abnormal iron accumulation in those same compartments within primary brain tissue.
Christina L. Nemeth +8 more
wiley +1 more source

