Results 1 to 10 of about 1,674 (114)

Best management in isolated right ventricular hypoplasia with septal defects in adults [PDF]

Journal of Cardiovascular and Thoracic Research, 2020
Hypoplastic right ventricle is a rare congenital disease usually associated with pulmonary atresia or tricuspid atresia. Isolated right ventricular hypoplasia is a rare anomaly without important valvular abnormalities.
Zahra Khajali, Maedeh Arabian, Maryam Aliramezany   +2 more
doaj   +1 more source

Autoimmune Hemolytic Anemia: A Late Presentation of Post-COVID-19 Syndrome

Oman Medical Journal, 2023
COVID-19 is a severe respiratory disease with a spectrum of clinical presentations and complications. Warm autoimmune hemolytic anemia (WAIHA) is increasingly recognized in patients with COVID-19 either while infected or shortly after infection.
Emad Al Khoufi, Bader Al-Muhainy, Kefah Algadeeb, Mortadah Alsalman   +3 more
doaj   +1 more source

Neurological and Neuroimaging Features of CYB5R3-Related Recessive Hereditary Methemoglobinemia Type II

Brain Sciences, 2022
Recessive hereditary methemoglobinemia (RHM) due to NADH-cytochrome b5 reductase deficiency is a rare disease caused by pathogenic variants in CYB5R3. Unlike type I, in RHM type II (RHM2), the enzymatic defect affects erythrocytes and all body tissues ...
Francesco Nicita, Letizia Sabatini, Viola Alesi, Giulia Lucignani, Ester Sallicandro, Antonella Sferra, Enrico Bertini, Ginevra Zanni, Giuseppe Palumbo   +8 more
doaj   +1 more source

English Case report: Succesfully Management of Critical Pulmonary Stenosis in a 12-Month-Old Boy By percutaneous transluminal balloon valvuloplasty

WMJ (Warmadewa Medical Journal), 2021
Critical pulmonary stenosis (PS) is used in infants born with very severe narrowing valves and requires treatment soon after birth. At four months old, an A-12-month-old boy was diagnosed with critical pulmonary stenosis but still successfully managed by
Dyahris Koentartiwi
doaj   +1 more source

Preoperative Hemoglobin Level, Oxygen Saturation and Postoperative Outcomes in Children With Cyanotic Congenital Heart Disease: A Propensity-Score Matching Analysis

Frontiers in Pediatrics, 2022
BackgroundThe optimal preoperative hemoglobin (Hb) level is difficult to define in children with cyanotic congenital heart disease (CHD) due to hypoxemia-induced secondary erythrocytosis.
Dan Zhou, Dan Zhou, Li-Jing Deng, Yun-Fei Ling, Meng-Lin Tang, Meng-Lin Tang   +5 more
doaj   +1 more source

Management of failing bidirectional cavopulmonary shunt: Influence of additional systemic-to-pulmonary-artery shunt with classic Glenn physiologyCentral MessagePerspective

JTCVS Open, 2022
Objectives: Severe hypoxemia in the early postoperative period after bidirectional cavopulmonary shunt (BCPS) is a critical complication. We aimed to evaluate patients who underwent additional systemic to pulmonary shunt and septation of central ...
Caecilia Euringer, MS, Takashi Kido, MD, PhD, Bettina Ruf, MD, Melchior Burri, MD, PhD, Paul Philipp Heinisch, MD, PhD, Janez Vodiskar, MD, Martina Strbad, MSc, Julie Cleuziou, MD, PhD, Daniel Dilber, MD, PhD, Alfred Hager, MD, PhD, Peter Ewert, MD, PhD, Jürgen Hörer, MD, PhD, Masamichi Ono, MD, PhD   +12 more
doaj   +1 more source

Brain Abscess and the Nonfenestrated Fontan Circulation

JACC: Case Reports, 2020
Brain abscess is a rare but life-threatening condition. Intracardiac or extracardiac right-to-left shunting in patients with unrepaired cyanotic congenital heart disease, pulmonary arteriovenous malformations, or venovenous collaterals allows microbes ...
Bethany G. Runkel, MD, William B. Drake, MD, MS, Geetha Raghuveer, MD, MPH   +2 more
doaj   +1 more source

A Case of Dextrotransposition of the Great Arteries Type I with Reversed Differential Cyanosis

American Journal of Perinatology Reports, 2019
Transposition of the great arteries type I is a severe congenital heart disease that induces serious cyanosis immediately after birth and death within 24 hours, unless proper treatment is administered.
Yuichi Morimoto, Noboru Inamura, Tukasa Takemura   +2 more
doaj   +1 more source

Surgical repair of large pulmonary artery to left atrium fistula

Clinical Case Reports, 2021
We report a successful surgical closure of a rught pulmonary artery to left atrium fistula (RPALAF) with secondary atrial septal defect (ASD) in a 3.5 years old girl.
Alaa Hussain, Muhamed Younis, Samir Srour, Mohamed Saleh, Mohammed Ismael   +4 more
doaj   +1 more source

Cyanosis in a patient with atrial septal defect

Journal of the Practice of Cardiovascular Sciences, 2015
Cyanosis in ASD has multiple causes requiring etiology directed management. Cyanosis can present in the setting of elevated pulmonary artery pressure, as in Eisenmenger syndromes having a poor prognosis.
Vikas Thakran, Anunay Gupta
doaj   +1 more source