Improving the prognosis of nephropathic cystinosis
Martine TP Besouw,1,2 Elena N Levtchenko1,21Department of Pediatric Nephrology, University Hospitals Leuven, Belgium; 2Laboratory of Pediatrics, Catholic University Leuven, Leuven, BelgiumAbstract: Cystinosis is an autosomal recessive inherited lysosomal
Besouw MTP, Levtchenko EN
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Synthesis of 1,2,5,7-dithiadiazonan-6-ylidenecyanamide. A New Potential Cysteamine Derivate Radioprotector Compound [PDF]
Enrique Ángeles +8 more
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Therapeutic strategies in cystinosis: A focus on cysteamine and beyond
Cystinosis is a autosomal recessive lysosomal storage disorder caused by mutations in the CTNS gene, which encodes cystinosin, a cystine transporter.
Angelo Santoro +2 more
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Mitigative role of cysteamine against unilateral renal reperfusion injury in Wistar rats
BackgroundIschemia-reperfusion injury (IRI) is unavoidable during kidney transplant and it is responsible for delayed or non-function after kidney transplantation. Cysteamine is the standard drug in the management of nephropathic cystinosis and its extra-
Babatunde Adebola Alabi +7 more
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Real-time monitoring of cellular dynamics using a microfluidic cell culture system with integrated electrode array and potentiostat [PDF]
A versatile microfluidic, multichamber cell culture and analysis system with an integrated electrode array and potentiostat suitable for electrochemical detection and microscopic imaging is presented in this paper.
Adamovski, M. +23 more
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Long-term follow-up of cystinosis patients treated with 0.55% cysteamine hydrochloride [PDF]
Hong Liang +4 more
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Gold or silver nanoparticles decorating superparamagnetic calcium ferrite nanoparticles for application in SERS [PDF]
In this work, we report the synthesis of Ag and Au nanoparticles capped with either cysteamine or cysteine. Purification of these NPs turned out to originate irreversible aggregation, so that the coupling of NH2 groups from Au (or Ag) nanoparticles to OH
Coutinho, Paulo J. G., Gomes, M. Lúcia
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Pre-clinical evaluation of cysteamine bitartrate as a therapeutic agent for mitochondrial respiratory chain disease [PDF]
Sujay Guha +14 more
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Factors Influencing the Surface Functionalization of Citrate Stabilized Gold Nanoparticles with Cysteamine, 3-Mercaptopropionic Acid or l-Selenocystine for Sensor Applications [PDF]
Georgia I. Sakellari +2 more
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Conformational Equilibrium of Cysteamine on Silver Metal Surface Studied by Surface‐Enhanced Raman Scattering [PDF]
Sungjun Kwak +3 more
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