Results 291 to 300 of about 1,061,223 (312)

Characterizing responses to CFTR-modulating drugs using rectal organoids derived from subjects with cystic fibrosis

Science Translational Medicine, 2016
J. Dekkers, G. Berkers, E. Kruisselbrink, A. Vonk, H. D. de Jonge, H. Janssens, I. Bronsveld, E. A. van de Graaf, E. Nieuwenhuis, R. Houwen, F. Vleggaar, J. Escher, Y. D. de Rijke, C. Majoor, H. Heijerman, K. M. de Winter-de Groot, H. Clevers, C. K. van der Ent, J. Beekman   +18 more
semanticscholar   +1 more source

Cystic fibrosis from the gastroenterologist's perspective

Nature Reviews Gastroenterology and Hepatology, 2016
Chee Y Ooi, Peter R Durie, Ooi Chee Y
exaly  

Cystic fibrosis carriers are at increased risk for a wide range of cystic fibrosis-related conditions

Proceedings of the National Academy of Sciences of the United States of America, 2020
Aaron C Miller, Alejandro P Comellas, Douglas B Hornick   +2 more
exaly  

Quorum-sensing signals indicate that cystic fibrosis lungs are infected with bacterial biofilms

Nature, 2000
John I. Glass, Elliot J. Lefkowitz, Jennifer S. Glass, Cheryl R. Heiner, Ellson Y. Chen, G. Cassell   +5 more
semanticscholar   +1 more source

Medullary Cystic Disease and Familial Juvenile Nephronophthisis

New England Journal of Medicine, 1967
Sheldon C Sommers, Sheldon C Sommers, Strauss Maurice B   +2 more
exaly  

Real-Life Safety and Effectiveness of Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis

American Journal of Respiratory and Critical Care Medicine, 2020
Marlene Murris-Espin, Lydie Lemonnier, Clemence Dehillotte   +2 more
exaly  

Progress in therapies for cystic fibrosis.

The Lancet Respiratory Medicine, 2016
K. De Boeck, M. Amaral
semanticscholar   +1 more source

Efficacy and Safety of Ivacaftor in Patients Aged 6 to 11 Years with Cystic Fibrosis with a G551D Mutation

American Journal of Respiratory and Critical Care Medicine, 2013
Jane C Davies, Claire E Wainwright, Mark A Chilvers   +2 more
exaly  

Restoring Cystic Fibrosis Transmembrane Conductance Regulator Function Reduces Airway Bacteria and Inflammation in People with Cystic Fibrosis and Chronic Lung Infections

American Journal of Respiratory and Critical Care Medicine, 2017
Katherine B Hisert, Sonya L Heltshe, Peter Jorth   +2 more
exaly  

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis.

Cell, 1990
Seng H. Cheng, R. Gregory, J. Marshall, S. Paul, D. Souza, Gary A. White, C. O’Riordan, Alan E. Smith   +7 more
semanticscholar   +1 more source