Results 301 to 310 of about 1,061,223 (312)

Clinical Mechanism of the Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor in G551D-mediated Cystic Fibrosis

American Journal of Respiratory and Critical Care Medicine, 2014
Steven M Rowe, Sonya L Heltshe, Scott H Donaldson   +2 more
exaly  

Antimicrobial resistance, respiratory tract infections and role of biofilms in lung infections in cystic fibrosis patients

Advanced Drug Delivery Reviews, 2015
Oana Ciofu, Tim Tolker-Nielsen, Peter Østrup Jensen   +2 more
exaly  

Correlating Cystic Fibrosis Transmembrane Conductance Regulator Function with Clinical Features to Inform Precision Treatment of Cystic Fibrosis

American Journal of Respiratory and Critical Care Medicine, 2019
Karen S Raraigh, Matthew J Pellicore, Emily F Davis-Marcisak   +2 more
exaly  

Abnormal localization of cystic fibrosis transmembrane conductance regulator in primary cultures of cystic fibrosis airway epithelia.

Journal of Cell Biology, 1992
Gerene M Denning, Lynda S Ostedgaard, Michael J Welsh   +2 more
exaly  

A functional CFTR assay using primary cystic fibrosis intestinal organoids

Nature Medicine, 2013
J. Dekkers, C. L. Wiegerinck, H. Jonge, I. Bronsveld, H. Janssens, K. W. Groot, A. Brandsma, N. Jong, M. Bijvelds, B. Scholte, E. Nieuwenhuis, S. Brink, H. Clevers, C. Ent, S. Middendorp, J. Beekman   +15 more
semanticscholar   +1 more source

A molecular mechanism for aberrantCFTR-dependent HCO3- transport in cystic fibrosis

EMBO Journal, 2002
Shigeru B H Ko, Nikolay Shcheynikov, Joo Young Choi   +2 more
exaly  

Effects of Lumacaftor–Ivacaftor Therapy on Cystic Fibrosis Transmembrane Conductance Regulator Function in Phe508del Homozygous Patients with Cystic Fibrosis

American Journal of Respiratory and Critical Care Medicine, 2018
Simon Y Graeber, Lutz Naehrlich, Stephanie Hirtz   +2 more
exaly  

Cystic Fibrosis Transmembrane Conductance Regulator Channel Dysfunction in Non–Cystic Fibrosis Bronchiectasis

American Journal of Respiratory and Critical Care Medicine, 2010
Thierry Bienvenu, Isabelle Sermet-Gaudelus, Pierre-Regis Burgel   +2 more
exaly  

Cystic fibrosis

Nature Reviews Disease Primers
Marcus A Mall, Pierre-Regis Burgel, Carlo Castellani   +2 more
exaly  

Ataluren (PTC124) Induces Cystic Fibrosis Transmembrane Conductance Regulator Protein Expression and Activity in Children with Nonsense Mutation Cystic Fibrosis

American Journal of Respiratory and Critical Care Medicine, 2010
François Vermeulen, Teresinha Leal, Janine Fritsch   +2 more
exaly