Results 41 to 50 of about 5,947 (182)

A Case of Primary Intramedullary Infantile Fibrosarcoma With an RBPMS::NTRK3 Fusion and Response to Larotrectinib

Neuropathology and Applied Neurobiology, Volume 52, Issue 5, October 2026.
We report a case of primary intramedullary infantile fibrosarcoma (IFS) in a 4‐week‐old infant with rapidly progressive cervical myelopathy. Histology showed a spindle cell tumour with diffuse S100 and pan‐TRK expression. RNA sequencing identified an RBPMS::NTRK3 fusion.
Mégane Le Quang, Julie Tandonnet, Nathalène Truffaux, Lucile Vanhersecke, Jean Delmas, Arthur Durouchoux, Dorian Bochaton, Arnault Tauziède‐Espariat, Guillaume Chotard   +8 more
wiley   +1 more source

How to differentiate abdominal wall leiomyomas from desmoid tumors?

Formosan Journal of Surgery, 2019
Background: Desmoid tumor and leiomyoma are abdominal wall tumors with similar clinical, radiographic, and histological features. However, differentiation between these two diseases is important because each may be linked to different systemic diseases ...
Tommy Nai-Jen Chang, Ming-Mo Hou, Mohamed AbdelRahman, Chih-Wei Wang, Li-Jen Wang, Dennis S Kao, Shao-Chih Hsu, Soo-Ha Kwon, Shih-Yin Huang, John Wen-Cheng Chang, Chih-Hung Lin   +10 more
doaj   +1 more source

Long-term follow up of a patient with a recurrent desmoid tumor that was successfully treated with proton beam therapy: A case report and literature review

Clinical and Translational Radiation Oncology, 2021
Desmoid tumors are benign, but may have a locally invasive tendency that commonly results in local recurrence. Most occur on the body trunk or extremities, whereas a head and neck desmoid tumor is relatively rare.
Takuya Sawada, Masashi Mizumoto, Yoshiko Oshiro, Haruko Numajiri, Shosei Shimizu, Yuichi Hiroshima, Masatoshi Nakamura, Takashi Iizumi, Toshiyuki Okumura, Hideyuki Sakurai   +9 more
doaj   +1 more source

Update on desmoid tumors

Annals of Oncology, 2012
Desmoid tumors (DTs) are histologically benign proliferations of stromal cells but may grow locally aggressive. Overall, DTs are rare (0.03% of all neoplasms). A minority of DTs is associated with Gardner syndrome and mutations of the familial adenomatous polyposis (FAP) gene. Most spontaneous DTs are associated with mutations of the beta-catenin gene.
C, Escobar, R, Munker, J O, Thomas, B D, Li, G V, Burton   +4 more
openaire   +2 more sources

Breast Fibromatosis: Clinical and Pathological Insights From Two Case Reports

Clinical Case Reports, Volume 14, Issue 9, September 2026.
ABSTRACT Breast fibromatosis is a benign, locally aggressive spindle‐cell tumor mimicking carcinoma. We report two cases in patients aged 15 and 61 years, highlighting its wide age range. Accurate histopathology prevents overtreatment. Modern management emphasizes individualized care, including active surveillance, complete surgical excision when ...
Vahid Soleimani, Behnaz Jahanbin, Aysan Nozheh   +2 more
wiley   +1 more source

Recurrent desmoid tumor of the abdominal wall

The Pan African Medical Journal, 2012
Desmoid tumors most often occur in abdominal wall. Their tendency to recur lead to repeated operations which can make the abdominal wall reconstruction difficult. We report a 28-year-old female history.
Imane Toughrai, Aya Oufkir, Said Ait Laalim, Karim Ibn Majdoub, Khalid Mazaz   +4 more
doaj   +1 more source

Surgical management of recurrent desmoid tumor in a young male

Journal of Pediatric Surgery Case Reports, 2022
Desmoid tumors are rare, aggressive fibroblastic soft tissue tumors. We report a case of a 20-year-old male with recurrence of desmoid tumor of the left shoulder after initial complete resection 3 years prior. Pathology revealed fibromatosis desmoid type.
Omar A. Santiago Báez, Atenas A. Martínez Bernal, Pedro E. Ruiz Medina, Jaime A. Aponte Ortiz, Victor N. Ortiz Justiniano   +4 more
doaj   +1 more source

Perineurioma‐like EMA‐positive calvarial neoplasms: clinicopathological study of eight cases

Histopathology, Volume 89, Issue 3, Page 544-553, September 2026.
Perineurioma‐like, EMA‐positive calvarial neoplasms (PLECN) are a rare group of intraosseous spindle cell tumours that demonstrate overlapping morphologic features of perineurioma and fibroblastic meningioma. These lesions tend to behave indolently but show a propensity for progressive growth.
Raheel Rizwan, Yingting Mok, Josephine K Dermawan, Alexandra Isaacson, Veronica Ulici, Scott E Kilpatrick, John D Reith, Gabrielle Yeaney, Hakan Ilaslan, Karen J Fritchie   +9 more
wiley   +1 more source

Increased Risk of Sarcomas in Children With Congenital Anomalies: Findings From the Genetic Overlap Between Anomalies and Cancer in Kids (GOBACK) Registry Linkage Study

Pediatric Blood &Cancer, Volume 73, Issue 8, August 2026.
ABSTRACT Background Pediatric sarcomas are a heterogeneous group of tumors that contribute disproportionately to cancer mortality in children. Although congenital anomalies are among the strongest known risk factors for childhood cancer, the risk of specific sarcoma subtypes among affected individuals has not yet been thoroughly evaluated. Procedure We
Russ Wolters, Ji Yun Tark, Tiffany M. Chambers, Tania A. Desrosiers, Michael E. Scheurer, Charles Shumate, Wendy N. Nembhard, Mahsa M. Yazdy, Eirini Nestoridi, Amanda E. Janitz, Jean Paul Tanner, Russell S. Kirby, Jason L. Salemi, Yao Yu, Chad D. Huff, Sharon E. Plon, Philip J. Lupo, Jeremy M. Schraw   +17 more
wiley   +1 more source

Giant Desmoid Tumor of the Anterior Abdominal Wall in a Young Female: A Case Report

Case Reports in Surgery, 2013
Desmoid tumors (also called desmoids fibromatosis) are rare slow growing benign and musculoaponeurotic tumors. Although these tumors have a propensity to invade surrounding tissues, they are not malignant.
Mahim Koshariya, Samir Shukla, Zuber Khan, Vaibhav Vikas, Avinash Pratap Singh, Puspendra Baghel, Varun Pendro, Vishal Kirti Jain, Shrikant Jagdish Jai, Sanjeev Kumar, M. C. Songra   +10 more
doaj   +1 more source