Results 141 to 150 of about 30,233 (313)
Impact of the vaneless diffuser geometry on stall mechanism development
openThe stall mechanism in vaneless diffuser has been matter of research since the 1950. The work presented has the aim to analyze the behavior of diffusers in critical conditions.
LA GAMBA, JACOPO
core
Developmental and Epileptic Encephalopathy due to Biallelic Pathogenic Variants in PIGM
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective PIGM encodes a critical enzyme in the glycosylphosphatidylinositol (GPI)‐anchor biosynthesis pathway. While promoter‐region mutations in PIGM have been associated with a relatively mild phenotype characterized by portal vein thrombosis and absence seizures, recent evidence suggests that coding‐region mutations result in a more severe
Júlia Sala‐Coromina +11 more
wiley +1 more source
Epilepsy‐Associated Variants of a Single SCN1A Codon Exhibit Divergent Functional Properties
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective Pathogenic variants in SCN1A, which encodes the voltage‐gated sodium channel NaV1.1, are associated with multiple epilepsy syndromes exhibiting a range of clinical severity. SCN1A variants are reported in different syndromes, including Dravet syndrome, which is associated with loss‐of‐function, whereas neonatal/infantile‐onset ...
Lanie N. Liebovitz +3 more
wiley +1 more source
Investigation of a High Pressure Ratio Centrifugal Compressor with Wedge Diffuser and Pipe Diffuser
, 2017 This present work is aimed at providing detailed understanding of the flow mechanisms in a highly loaded centrifugal compressor with different diffusers. Performance comparison between compressor stages with pipe diffuser and wedge diffuser was conducted
Chengwu Yang +4 more
core +1 more source
Multidimensional Profiling of MRI‐Negative Temporal Lobe Epilepsy Uncovers Distinct Phenotypes
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective Although hippocampal sclerosis (TLE‐HS) represents the most frequent cause of temporal lobe epilepsy (TLE), up to 30% of patients show no lesion on visual MRI inspection (TLE‐MRIneg). These cases pose diagnostic and therapeutic challenges and are underrepresented in surgical series.
Alice Ballerini +28 more
wiley +1 more source
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objectives Retrograde trans‐synaptic degeneration (rTSD) from posterior visual pathway lesions in multiple sclerosis (MS) is characterized by hemi‐macular ganglion cell‐inner plexiform layer (GCIPL) thinning and contralateral visual field loss.
Abdul Jaber Tayem +17 more
wiley +1 more source
Effects of Pre-Diffuser on Performance of Dump Diffuser [PDF]
, 2015 研究了突扩扩压器中前置扩压器各参数与总压损失和静压恢复间的关系。采用实验与fluEnT计算结合的方法,通过水槽PIV实验得出扩压器内的流场信息,对照不同的湍流模型,得出最佳的计算方案。根据此计算方案计算不同的扩张角下前置扩压器性能的变化,得出各参数之间的规律。结果表明雷诺应力模型能够较好地预测扩压器内部流场;前置扩压器扩张角存在一个最佳值,大于最佳值前置扩压器会出现流动分离;结合理论分析和计算数据总结出计算前置扩压器总压损失系数和静压恢复系数的公式,利用此公式还可求出最佳的前置扩张角和前置扩压器长度 ...
邢菲 +4 more
core
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective To explore how cerebral hypoxia and Normal‐Appearing White Matter (NAWM) integrity affect MS lesion burden and clinical course. Methods Seventy‐nine MS patients, including 13 clinically isolated syndrome (CIS) patients and 66 relapsing–remitting multiple sclerosis (RRMS) patients, and 44 healthy controls (HCs) were recruited from ...
Xinli Wang +8 more
wiley +1 more source
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective This analysis evaluates the effect of successful reperfusion on functional outcomes after MT, stratified by admission National Institutes of Health Stroke Scale (NIHSS) and Alberta Stroke Program Early CT Score (ASPECTS) as surrogates for clinical‐core mismatch, using multicenter registry data.
Felix Schlicht +53 more
wiley +1 more source
CoRRUniform-state discrete diffusion models hold the promise of fast text generation due to their inherent ability to self-correct. However, they are typically outperformed by autoregressive models and masked diffusion models. In this work, we narrow this performance gap by leveraging a key insight: Uniform-state diffusion processes naturally emerge from ...
Subham Sekhar Sahoo +5 more
openaire +4 more sources