Results 71 to 80 of about 1,484 (136)

Comparison Between Dichloroacetate and Phenylbutyrate Treatment for Pyruvate Dehydrogenase Deficiency. [PDF]

open access: yesBr J Biomed Sci, 2022
Karissa P   +8 more
europepmc   +1 more source

Escherichia coli 2-oxoglutarate dehydrogenase multienzyme complex: e1 and e2 substrate specificty, e1 carboligase activity, and e2 interchain succinyl transfer [PDF]

open access: yes, 2013
Escherichia coli (E. coli) 2-oxoglutarate dehydrogenase multienzyme complex (OGDHc) contains three components: a thiamin di phosphate (ThD P) dependent 2-oxogl utarate dehydrogenase (E1 o), a di hydrol i poylsucci nyl transferase (E2o), and a di hydrol i
Shim, Da Jeong
core   +1 more source

Pyruvate dehydrogenase complex from Azotobacter vinelandii [PDF]

open access: yes
The isolation and some alternatives for purification of PDC from Azotobacter vinelandii are described (CHAPTER 3). Ultimate extent and recovery seem to be limited by the lability of the enzyme: sensitivity to shearing forces.
Bresters, T.W.
core   +1 more source

Lipoamide dehydrogenase deficiency: A new cause for recurrent myoglobinuria [PDF]

open access: yes, 2004
A. Shaag   +6 more
core   +1 more source

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