Results 11 to 20 of about 258 (146)

Focal Segmental Glomerulosclerosis and Scheduled Pretransplant Plasmapheresis: A Timely Diagnosis of Nail-Patella Syndrome Avoided More Futile Immunosuppression. [PDF]

Case Rep Nephrol, 2020
Focal and segmental glomerulosclerosis (FSGS) is a histopathological pattern of injury. As such, it encompasses a wide variety of dissimilar entities with different pathophysiologic mechanisms. Although ultrastructural morphological characteristics can specifically diagnose certain diseases and genetic mutations can also be unravelled, this ideal ...
Trimarchi H.
europepmc   +2 more sources

Intravascular hemolysis and multitreatment predict thrombosis in patients with autoimmune hemolytic anemia

Journal of Thrombosis and Haemostasis, Volume 20, Issue 8, Page 1852-1858, August 2022., 2022
Abstract Background Thrombosis may complicate autoimmune hemolytic anemia (AIHA), but its predictors are still lacking, and no clear‐cut indications for anticoagulant prophylaxis are available. Objectives To characterize frequency and severity of thromboses in AIHA patients and identify risk factors for thrombosis that may advise primary anticoagulant ...
Bruno Fattizzo, Marta Bortolotti, Juri Alessandro Giannotta, Anna Zaninoni, Dario Consonni, Wilma Barcellini   +5 more
wiley   +1 more source

Ethnopharmacological Study of the Medicinal Plants Used in the Treatment of Sickle Cell Anemia in the West Region of Cameroon

Evidence-Based Complementary and Alternative Medicine, Volume 2022, Issue 1, 2022., 2022
Background. Sickle cell anemia (SCA) or sickle cell disease (SCD) is a genetic disease associated with increased morbidity and mortality in Africa and other developing nations. Therefore, modern and traditional remedies are being introduced for use in the treatment and management of this disease.
Natacha Lena Yembeau, Prosper Cabral Biapa Nya, Constant Anatole Pieme, Kevin Dedjam Tchouane, Christian Bernard Kengne Fotsing, Prudence Josela Nya Nkwikeu, Alfloditte Flore Feudjio, Phelix Bruno Telefo, Francesco Cardini   +8 more
wiley   +1 more source

Pathological basis of symptoms and crises in sickle cell disorder: implications for counseling and psychotherapy

Hematology Reports, 2010
Sickle Cell Disorder (SCD) is a congenital hemoglobinopathy. There is little in literature regarding the psychological variables affecting individuals living with SCD and all of the significant people around them.
Oluwatoyin Olatundun Ilesanmi
doaj   +1 more source

ROLE OF STEM CELL FACTOR IN THE REACTIVATION OF HUMAN FETAL HEMOGLOBIN

Mediterranean Journal of Hematology and Infectious Diseases, 2009
In humans the switch from fetal to adult  hemoglobin (HbF→ HbA) takes place in the perinatal and postnatal period, determining the progressive replacement of HbF with HbA synthesis ( i.e., the relative HbF content in red blood cells decreases from 80-90%
Marco Gabbianelli, Ugo Testa
doaj   +3 more sources

Renal Thrombotique microangiopathy: An unusual renal involvement in Niemann‐Pick disease type B

Clinical Case Reports, Volume 8, Issue 12, Page 3315-3320, December 2020., 2020
Renal involvement in Niemann‐Pick disease type B is very rare. Kidney check‐up and renal biopsy should be performed in any patient presented with hypertension and kidney disease. Histology identifies the lesion, the prognosis, and guide treatment. Abstract Renal involvement in Niemann‐Pick disease type B is very rare.
Mouna Jerbi, Mariem Sayhi, Hanene Gaied, Hafedh Hedri, Raja Aoudia, Rim Goucha, Taieb Ben Abdallah   +6 more
wiley   +1 more source

Gender-Related Differences in Sickle Cell Disease in a Pediatric Cohort: A Single-Center Retrospective Study

Frontiers in Molecular Biosciences, 2019
Sickle cell disease (SCD) is one of the most common monogenic disease worldwide. The incidence of SCD is not strictly gender-related as it is transmitted as an autosomal recessive disorder.
Giulia Ceglie, Giulia Ceglie, Margherita Di Mauro, Margherita Di Mauro, Isabella Tarissi De Jacobis, Francesca de Gennaro, Martina Quaranta, Martina Quaranta, Carlo Baronci, Alberto Villani, Giuseppe Palumbo   +10 more
doaj   +1 more source

The 4th Global Congress on Sickle Cell Disease Abstract Book 2022

, 2022
HemaSphere, Volume 6, Issue S4, Page 1-64, August 2022.
wiley   +1 more source

Retrospective Analysis of Endocrine Dysfunctions in a Population of Adult Polytransfused Patients: Correlation of GH‐IGF1 Axis Alteration with Cardiac Performance

BioMed Research International, Volume 2018, Issue 1, 2018., 2018
Endocrine complications of haemochromatosis and heart failure mostly affect morbidity and mortality in polytransfused patients. This study analyzes endocrine dysfunctions and the impact of GH‐IGF‐1 axis alteration on cardiac performance in a population of 31 patients.
Michela Rosaria Campo, Anna Farese, Michele Correale, Giuseppe Berti, Michela Massa, Maria Rosaria Sorrentino, Grazia Roberti, Filomena Sportelli, Mauro Cignarelli, Olga Lamacchia, Sheba Mohankumar   +10 more
wiley   +1 more source

Visualization of poikilocytosis as an emerging erythrocytic biomarker for fish health assessment

Animal Research and One Health, Volume 2, Issue 2, Page 136-157, May 2024.
Poikilocytosis in fish encompasses various morphological changes in erythrocytes, including acanthocytes, echinocytes, spherocytes, dacrocytes, degmacytes, and more. This phenomenon results from both living and nonliving factors, such as pathological influences, environmental stress, anthropogenic impacts, and hereditary factors.
Avishek Bardhan, Thangapalam Jawahar Abraham, Ratnapriya Das, Prasanna Kumar Patil   +3 more
wiley   +1 more source