Results 171 to 180 of about 25,211 (207)
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Hand Surgery for Dystrophic Epidermolysis Bullosa
Journal of Pediatric Orthopaedics, 2014Epidermolysis bullosa (EB) is a group of inherited, mechanobullous disorders caused by mutations in various structural proteins in the skin. The manifestation of these disorders in the hand is of digital contractures and pseudosyndactyly or "cocoon hands," causing significant functional impairment.Our preferred surgical treatment of these patients ...
Shai, Luria +3 more
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THE HAND IN RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA
Hand Clinics, 2000Recessive dystrophic epidermolysis bullosa is still a difficult challenge for surgeons and doctors. Hand retractions are different from burns. The medical team must have a good knowledge of the disease. Surgery must be performed with the collaboration of every member of the team, as well as the family.
J, Glicenstein, D, Mariani, R, Haddad
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Gastrostomy and growth in dystrophic epidermolysis bullosa
British Journal of Dermatology, 1996Chronic malnutrition and growth failure are features of severe dystrophic epidermolysis bullosa (DEB). Conventional dietetic intervention is of limited benefit. Oesophageal dilatation or reconstruction to alleviate stricture is associated with substantial risks.
Haynes, L. +4 more
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British Journal of Dermatology, 1994
We report a study of eight unrelated adult patients with a highly distinctive phenotype of dystrophic epidermolysis bullosa. It is characterized clinically by pruritus, lichenified or nodular prurigo-like lesions, violaceous linear scarring, occasional trauma-induced blistering, excoriations, milia, nail dystrophy and, in some cases, albopapuloid ...
J A, McGrath, O M, Schofield, R A, Eady
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We report a study of eight unrelated adult patients with a highly distinctive phenotype of dystrophic epidermolysis bullosa. It is characterized clinically by pruritus, lichenified or nodular prurigo-like lesions, violaceous linear scarring, occasional trauma-induced blistering, excoriations, milia, nail dystrophy and, in some cases, albopapuloid ...
J A, McGrath, O M, Schofield, R A, Eady
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Epidermolysis Bullosa Nevus in a Patient With Recessive Dystrophic Epidermolysis Bullosa
The American Journal of Dermatopathology, 2014We present a case of a 6-year-old girl with recessive dystrophic epidermolysis bullosa (EB) who presented with a large pigmented lesion clinically concerning for melanoma. After histological examination and fluorescent in situ hybridization analysis, diagnosis of EB nevus was performed.
Katherine, Fening +5 more
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CYCLOSPORIN FOR DYSTROPHIC EPIDERMOLYSIS BULLOSA
The Lancet, 1989A 65-year-old woman with epidermolysis bullosa since childhood was first admitted to our clinic in September, 1987. At first we treated the patient with high doses of vitamin E, phenytoin, prednisolone, and erythromycin but without sucess. When we read a report of the use of cyclosporin in a patient with epidermolysis bullosa acquisita, we began ...
Sándor Husz +5 more
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Care of a patient with dystrophic epidermolysis bullosa
Journal of Wound Care, 1995A report of an improved dressing regime for a young patient with a chronic skin condition
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TETRACYCLINES FOR DYSTROPHIC EPIDERMOLYSIS BULLOSA
The Lancet, 1989P, Humbert +3 more
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The management of dystrophic epidermolysis bullosa
Clinical and Experimental Dermatology, 1995M G, Dunnill, R A, Eady
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