Results 171 to 180 of about 7,899 (310)

Targeted Anti‐IL‐1 Immunomodulatory Therapy in Pediatric Onset PPP1R13L‐Related Arrhythmogenic Cardiomyopathy

American Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Autosomal recessive loss‐of‐function variants in PPP1R13L cause an ultra‐rare cardiocutaneous syndrome characterized by rapidly progressive arrhythmogenic cardiomyopathy (ACM). PPP1R13L encodes iASPP, which has two potentially overlapping mechanisms driving ACM as both a regulator of NFκB‐mediated inflammation and a binding partner within the ...
Aaron Renberg, Savannah Coppersmith, Owen Merritt, Amer Heider, Adam Helms, Thomas Michniacki, Jack Luxford, Sarah Josephi‐Taylor, Philip Roberts, Joshua Meisner   +9 more
wiley   +1 more source

Continuous tuning of ejector parameters via zeotropic component migration for optimising high-temperature heat pump. [PDF]

Commun Eng
Li Z, Liang Y, Zhu Y, Yao S, Yu Z.
europepmc   +1 more source

Response of an Infant With Presumed Multiple Acyl‐CoA Dehydrogenase Deficiency (MADD) to Ketone Supplementation

American Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Multiple Acyl‐CoA Dehydrogenase Deficiency (MADD) is an autosomal recessive inborn error of metabolism caused by biallelic pathogenic variants in one of three known genes: ETFA, ETFB, and ETFDH. It can cause multisystem dysfunction, including cardiomyopathy in severe cases.
Yutaka Furuta, Kaitlyn N. Bloom, Jerry Vockley, Angela R. Grochowsky, Neena S. Agrawal, Ellen W. Strickler, Natalie N. Owen, Erica T. Gray, B. Lakshitha A. Perera, Eric R. Gamazon, Lynette C. Rives, Hua‐Chang Chen, Qi Liu, Rizwan Hamid, Joy D. Cogan, John A. Phillips III, Thomas A. Cassini, Bryce A. Schuler   +17 more
wiley   +1 more source

A Uniformity Coefficient-Based Method for Improving the Wear Resistance of Mold Ejector Pin Guide Holes via Oblique Laser Shock Peening. [PDF]

Materials (Basel)
Liu E, Ye Y, Zhang Y, Mu S, Xu Z, Jiang W, Li Y.   +6 more
europepmc   +1 more source

Chrysin alleviates pressure overload–induced myocardial remodeling through regulating the PI3K/AKT/NRF2 pathway–mediated oxidative stress response

Animal Models and Experimental Medicine, EarlyView.
In this study, we primarily simulated pathological myocardial remodeling induced by transverse aortic constriction surgery and found significant cardiac hypertrophy and fibrosis, characterized by deteriorated cardiac function. Oxidative stress response is considered as a pivotal pathological process, which contributes to inflammation and apoptosis of ...
Yijia Wang, Xing Feng, Shuhui Zhao, Yuchong Fu, Ao Zhang, Xiaofeng Shen, Bowen Yu, Yihao Wang, Jiahui Lin, Bing Zhang, Weiping Ji, Lianpin Wu, Xiaoling Guo   +12 more
wiley   +1 more source

Impact of Various Moisture Control Methods on Intraoral Humidity. [PDF]

J Adhes Dent
Washino T, Ikeda M, Burrow MF, Nikaido T.   +3 more
europepmc   +1 more source

Mathematical modelling of an ejector refrigeration system

, 2012
The purpose of this project is to examine the working principals of an ejector refrigeration cycle and develop a mathematical model of the ejector refrigeration system.
N Satheesh Kumar
core  

Enhancement in production efficiency using DMAIC methodology of six sigma. [PDF]

Sci Rep
Deepak D, Farwaha HS, Alqahtani FM, Dwivedi S, Singh RP, Singh P, Ranjan N, Kumar A.   +7 more
europepmc   +1 more source

Thermoeconomic optimization of a hybrid power and cooling facility using waste heat recovery from a marine diesel engine. [PDF]

Sci Rep
Ben Hamida MB, Al-Mussawi W, Shaban M, Marefati M.   +3 more
europepmc   +1 more source

The Research and Application of Ejectors in Managing Low Oxygen Levels in Workface Corners. [PDF]

ACS Omega
Jin Y, Li J, Yan L, Guo J, Lei Z.
europepmc   +1 more source