Rosai-Dorfman Disease: A Clinico-pathological Presentation of Three Cases and Review of Literature [PDF]
Rosai-Dorfman Disease (RDD) or Sinus Histiocytosis with Massive Lymphadenopathy (SHML) is a rare histiocytic disorder of unknown aetiology which presents as a benign, self-limiting disease of phagocytic histiocytes occurring mainly in the first and ...
Francis Ikechukwu Ukekwe +4 more
doaj +1 more source
Diagnostics of Autoimmune Hepatitis Enabled by Non‐Invasive Clinical Proteomics
Mass‐spectrometry‐based proteomic analyses of paired liver‐plasma samples from patients with AIH enabled discovery of numerous proteins showing high diagnostic accuracy. Proteomics may constitute a novel non‐invasive diagnostic tool for AIH if validated in larger, age‐ and sex‐matched cohorts.
Anne‐Sofie Houlberg Jensen +20 more
wiley +1 more source
Natural history and outcomes in drug induced autoimmune hepatitis [PDF]
Aim: Drug-induced autoimmune hepatitis (DIAIH) remains poorly characterized. Our aim was to assess natural history and outcomes in DIAIH. Methods: This was a retrospective cohort study.
Alla +33 more
core +1 more source
Intrathoracic Rosai–Dorfman Disease in Elderly Patients: A Case Report
ABSTRACT Rosai–Dorfman disease (RDD), a rare form of histiocytosis, predominantly affects young individuals. Clinically categorized into nodal and extranodal subtypes, the disease primarily involves systemic lymph nodes with possible involvement of other organs.
JianFeng Xiao, Li Ma, Wei Cao
wiley +1 more source
Purely cutaneous rosai-dorfman disease with immunohistochemistry
Background: The cutaneous form of Rosai-Dorfman disease (RDD) is a rare entity that manifests solely with skin papules or nodules and does not present with the usual myriad of symptoms of classical RDD.
Uzma Farooq +3 more
doaj +1 more source
Recommendations for the standardization of bone marrow disease assessment and reporting in children with neuroblastoma; on behalf of the International Neuroblastoma Response Criteria Bone Marrow Working Group [PDF]
BACKGROUND: The current study was conducted to expedite international standardized reporting of bone marrow disease in children with neuroblastoma and to improve equivalence of care.
Aronica +39 more
core +1 more source
Autoimmune gastrointestinal complications in patients with Systemic Lupus Erythematosus: case series and literature review [PDF]
The association of systemic lupus erythematosus (SLE) with gastrointestinal autoimmune diseases is rare, but has been described in the literature, mostly as case reports.
Agmon-Levin N +101 more
core +1 more source
Abstract IgG4‐related chronic rhinosinusitis (IgG4‐related CRS) is gaining recognition among various specialized physicians. As a systemic disease involving multiple organs, IgG4‐related CRS is still not widely recognized as an independent clinical entity. Given the complexity of diagnosing autoimmune‐related multisystem diseases, early recognition and
Lianqi Wan +3 more
wiley +1 more source
ABSTRACT Background and Aims SARS‐CoV‐2 vaccine‐associated liver injury (SVALI) is a rare event and its pathophysiology remains unclear. Previous studies have found an oligoclonal CD8+ T cell infiltrate and SARS‐CoV‐2 spike antigen‐specific T cells in the liver of patients with SVALI. Therefore, we aimed to characterise the immune infiltrate in a liver
Sarp Uzun +11 more
wiley +1 more source
Clinical and Molecular Characteristics of Megakaryocytes in Myelodysplastic Syndrome
Objective Myelodysplastic syndrome (MDS) is a malignant clonal disorder of hematopoietic stem cells which is characterized by morphologic dysplasia.
Fangxiu Luo +6 more
doaj +1 more source

