Clinicopathological Features, Treatment Response, and Outcome of Rosai-Dorfman Disease in Two Children. [PDF]
Clin Case RepRosai‐Dorfman disease is a rare non‐Langerhans cell histiocytic disorder. It is common in male children and young adults of African descent. It is classified into sporadic and familial types.
Evele G, Francine K, Bardin R.
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Primary Tracheal Rosai-Dorfman Disease Coexisting With Active Pulmonary Tuberculosis. [PDF]
Respirol Case RepWe report a rare case of primary tracheal Rosai‐Dorfman disease (RDD) with active pulmonary tuberculosis. Bronchoscopic resection immediately relieved > 90% airway obstruction, and anti‐tuberculosis therapy was given, resulting in no recurrence at one‐year follow‐up. ABSTRACT Rosai‐Dorfman disease (RDD) rarely involves the trachea, and active pulmonary
Yang S, Li S, Sun W, Gu Y, Yang L.
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Multifocal Rosai Dorfman disease and simultaneous endometrioid ovarian cancer: a case report. [PDF]
J Med Case RepBackground Rosai Dorfman disease is a rare histiocytosis, which is characterized by accumulation of histiocytes in lymph nodes, but also in extranodal locations. Histologically, one of the key features of Rosai Dorfman disease is emperipolesis. Treatment
Graf N +3 more
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H Syndrome Associated With Pure Red Cell Aplasia, Rosai-Dorfman Disease, and Sensorineural Hearing Loss: Phenotypic Variability in Three Children With the Same SLC29A3 Mutation. [PDF]
Clin Case RepABSTRACT H syndrome is a rare autosomal recessive disorder caused by mutations in the SLC29A3 gene. We report three pediatric patients with a homozygous c.1309G>A (p.Gly437Arg) mutation presenting with distinct phenotypic variations. These cases expand the clinical spectrum and emphasize the importance of early genetic diagnosis and family counseling.
Najajrah M +5 more
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Rosai-Dorfman disease mimicking gastrointestinal tuberculosis and fungal sinusitis: A case report
Radiology Case Reports, 2022 Every organ can be affected by Rosai-Dorfman disease, the most common being skin and soft tissue, bone and upper respiratory tract. Here we present a Rosai-Dorfman disease patient who manifested with multiple organ involvement.
Seid Getahun Abdela, MD +1 more
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Temporal bone manifestation of primary extranodal Rosai–Dorfman disease: a case report
Journal of Medical Case Reports, 2023 Background Rosai–Dorfman disease is a rare benign histiocytic disorder characterized in most cases by painless cervical adenopathy. Less than 10% of extranodal cases involve bony lesions. Primary bone Rosai–Dorfman disease in the absence of nodal disease
E. Koonar +3 more
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SAGE Open Medical Case Reports, 2021 Background: Sinus histiocytosis with massive lymphadenopathy, also known as Rosai–Dorfman disease, is a rare proliferation of non-Langerhans histiocytes.
Sharon L Kipfer +2 more
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Histological variability and the importance of clinicopathological correlation in cutaneous Rosai-Dorfman disease [PDF]
Anais Brasileiros de Dermatologia, 2016 : Rosai-Dorfman disease is a benign histiocytic proliferative disorder of unknown etiology. The disease mainly affects lymph node tissue, although it is rarely confined to the skin.
Ana Gameiro +3 more
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Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement
South African Journal of Radiology, 2023 Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented.
Smily Sharma +3 more
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International Journal of Hematology-Oncology and Stem Cell Research, 2021 Rosai Dorfman disease is a rare histiocytic disorder of over-production of non-Langerhans histiocytes, which typically manifests with massive lymphadenopathy and sinonasal involvement.
Yi Li +5 more
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