Results 1 to 10 of about 2,738 (133)

Clinicopathological Features, Treatment Response, and Outcome of Rosai‐Dorfman Disease in Two Children [PDF]

Clinical Case Reports
Rosai‐Dorfman disease is a rare non‐Langerhans cell histiocytic disorder. It is common in male children and young adults of African descent. It is classified into sporadic and familial types.
George Evele, Kouya Francine, Richard Bardin   +2 more
doaj   +3 more sources

Primary Tracheal Rosai-Dorfman Disease Coexisting With Active Pulmonary Tuberculosis. [PDF]

Respirol Case Rep
We report a rare case of primary tracheal Rosai‐Dorfman disease (RDD) with active pulmonary tuberculosis. Bronchoscopic resection immediately relieved > 90% airway obstruction, and anti‐tuberculosis therapy was given, resulting in no recurrence at one‐year follow‐up. ABSTRACT Rosai‐Dorfman disease (RDD) rarely involves the trachea, and active pulmonary
Yang S, Li S, Sun W, Gu Y, Yang L.
europepmc   +2 more sources

Multifocal Rosai Dorfman disease and simultaneous endometrioid ovarian cancer: a case report [PDF]

Journal of Medical Case Reports
Background Rosai Dorfman disease is a rare histiocytosis, which is characterized by accumulation of histiocytes in lymph nodes, but also in extranodal locations. Histologically, one of the key features of Rosai Dorfman disease is emperipolesis. Treatment
Nele Graf, Teresa Halbsguth, Sven Becker, Morva Tahmasbi Rad   +3 more
doaj   +2 more sources

Rosai‐Dorfman disease in 6‐year‐old child: Presentation, diagnosis, and treatment

Clinical Case Reports, 2021
Rosai‐Dorfman disease is referred to as sinus histiocytosis massive lymphadenopathy. We are reporting a rare case of Rosai‐Dorfman disease, a case of 6‐year‐old boy with a history of multiple painless submandibular and cervical lymphadenopathy.
Kalpana Giri, Ashok Baral, Niva Tiwari, Krishna Sagar Sharma   +3 more
doaj   +2 more sources

H Syndrome Associated With Pure Red Cell Aplasia, Rosai-Dorfman Disease, and Sensorineural Hearing Loss: Phenotypic Variability in Three Children With the Same SLC29A3 Mutation. [PDF]

Clin Case Rep
ABSTRACT H syndrome is a rare autosomal recessive disorder caused by mutations in the SLC29A3 gene. We report three pediatric patients with a homozygous c.1309G>A (p.Gly437Arg) mutation presenting with distinct phenotypic variations. These cases expand the clinical spectrum and emphasize the importance of early genetic diagnosis and family counseling.
Najajrah M, Bouzia HI, Darawi NK, Hajjaj FS, Moosa NH, Awad NM.   +5 more
europepmc   +2 more sources

Rosai-Dorfman disease mimicking gastrointestinal tuberculosis and fungal sinusitis: A case report

Radiology Case Reports, 2022
Every organ can be affected by Rosai-Dorfman disease, the most common being skin and soft tissue, bone and upper respiratory tract. Here we present a Rosai-Dorfman disease patient who manifested with multiple organ involvement.
Seid Getahun Abdela, MD, Chalew Abebe Mengesha, MD   +1 more
doaj   +1 more source

Temporal bone manifestation of primary extranodal Rosai–Dorfman disease: a case report

Journal of Medical Case Reports, 2023
Background Rosai–Dorfman disease is a rare benign histiocytic disorder characterized in most cases by painless cervical adenopathy. Less than 10% of extranodal cases involve bony lesions. Primary bone Rosai–Dorfman disease in the absence of nodal disease
E. Koonar, F. Ramazani, M. Hyrcza, J. Chau   +3 more
doaj   +1 more source

Emergence of cutaneous Rosai–Dorfman disease during immunosuppressive treatment of follicular B-cell lymphoma: A case report

SAGE Open Medical Case Reports, 2021
Background: Sinus histiocytosis with massive lymphadenopathy, also known as Rosai–Dorfman disease, is a rare proliferation of non-Langerhans histiocytes.
Sharon L Kipfer, Michael Samycia, Carolyn J Shiau   +2 more
doaj   +1 more source

Histological variability and the importance of clinicopathological correlation in cutaneous Rosai-Dorfman disease [PDF]

Anais Brasileiros de Dermatologia, 2016
: Rosai-Dorfman disease is a benign histiocytic proliferative disorder of unknown etiology. The disease mainly affects lymph node tissue, although it is rarely confined to the skin.
Ana Gameiro, Miguel Gouveia, José Carlos Cardoso, Oscar Tellechea   +3 more
doaj   +1 more source

Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement

South African Journal of Radiology, 2023
Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented.
Smily Sharma, Poonam Sherwani, Venkata S. Arunachalam, Rahul Dev   +3 more
doaj   +1 more source