Results 41 to 50 of about 4,871,906 (165)
Giant intracranial Rosai-Dorfman disease
, 2004 Rosai-Dorfman disease is a rare, non-neoplastic disease characterized by an unusual proliferation of histiocytic cells. It rarely manifests intracranially, and only 50 cases of intracranial lesions have been reported.
BOZKURT, SÜHEYLA
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eJHaem, Volume 7, Issue 5, October 2026.ABSTRACT Introduction Primary cutaneous peripheral T‐cell lymphoma, not otherwise specified (pcPTCL‐NOS), is exceptionally rare in children, and evidence guiding diagnosis and treatment is limited. Case Presentation A 10‐year‐old boy with pcPTCL‐NOS refractory to chemotherapy received mogamulizumab prior to allogeneic haematopoietic stem cell ...
Maria Ebbesen Sørum +9 more
wiley +1 more source
Targeted proteomics reveal histiocytosis‐associated neurodegeneration signatures
HemaSphere, Volume 10, Issue 9, September 2026.Abstract Neurodegeneration (ND) is a severe complication of Langerhans cell histiocytosis (LCH), yet its underlying biology and reliable biomarkers remain poorly defined. The aim of this study was to (1) gain insight into neuroimmunological mechanisms governing ND and (2) assess the clinical value of established and novel biomarkers for ND‐LCH.
Egle Kvedaraite +29 more
wiley +1 more source
Rosai-Dorfman disease with diffuse gastrointestinal involvement
, 2013 Rosai-Dorfman disease, formerly known as sinus histiocytosis with massive lymphadenopathy', is a rare self-limiting histiocytic proliferative disorder typically presenting early in life with cervical lymphadenopathy and nonspecific systemic symptoms ...
Nalcaci, Meliha +8 more
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Rosai-dorfman disease: A rare entity in eastern India
, 2022 Rosai-dorfman disease is a very rare disease. It is first time reported in Odisha, in IMS and SUM Hospital, Bhubaneswar. After all necessary investigations, Clinicians came to conclude that it's Rosai-dorfman disease also known as sinus histiocytosis ...
Dr. Sandeep Kumar Ratha, Sumita Sharma
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BMC Ophthalmology, 2019 Background Rosai-Dorfman disease is a rare non–Langerhans cell histiocytosis. Ocular involvement is even rarer, mostly involving the orbit and eyelids, although marginal corneal ulcers, uveitis, and epibulbar masses have also been reported, and is ...
Yu-Kuei Lee +3 more
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Histiocytosis development and clinical variation through the lens of genomics
The Journal of Pathology, Volume 270, Issue 1, Page 23-39, September 2026.Abstract Histiocytic neoplasms are rare haematologic diseases characterised by clonal expansions of cells with a monocyte, macrophage or dendritic cell phenotype. Their clinical manifestations are diverse, ranging from indolent lesions to aggressive systemic disease.
Paul G Kemps +3 more
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Rosai-Dorfman disease of the lung.
, 2009 Rosai-Dorfman disease is a rare disorder which seems to involve not only the lymph nodes but most other organs of the body. The case history is presented of a woman who was thought to have atypical carcinoma of the lung but in whom a diagnosis of Rosai ...
Ali, A, Mackay, D
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Progress in diagnosis and treatment of osseous Rosai-Dorfman disease
Zhongguo aizheng zazhi, 2019 Sinus histiocytosis with massive lymphadenopathy, also known eponymously as Rosai-Dorfman disease, is a rare disease that is defined as a self-limiting proliferation of non-Langerhans histiocytes.
卫愉轩, 董 扬
doaj
Rosai-Dorfman disease with pulmonary involvement mimicking bronchogenic carcinoma
Journal of Cardiothoracic Surgery, 2020 Background Rosai-Dorfman disease is a histiocytic lesion that affects lung rarely. Case presentation We present a 52-year-old female diagnosed with right intrabronchial mass invading the bronchial wall and the extrabronchial tissues with lymphadenopathy.
Haneen Al-Maghrabi +4 more
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