An unusual Erdheim-Chester disease with orbital involvement: A case report [PDF]
, 2016 Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis with multiorgan involvement and a specific tropism for perivascular and fatty connective tissue, of unclear origin, with poor response to therapy. Its identification is difficult because
Bencivinni, F. +5 more
core +2 more sources
Unmasking Rosai-Dorfman disease in a woman with cervical lymphadenopathy: a histopathological insight [PDF]
, 2023 Rosai-Dorfman disease (RDD) also called as sinus histiocytosis with massive lymphadenopathy is a rare benign proliferative self‐limiting disease of the macrophage‐histiocyte cell family.
Doshi, Anoushka A., Nelekar, Shruti B.
core +2 more sources
Purely cutaneous rosai-dorfman disease with immunohistochemistry
Indian Journal of Dermatology, 2013 Background: The cutaneous form of Rosai-Dorfman disease (RDD) is a rare entity that manifests solely with skin papules or nodules and does not present with the usual myriad of symptoms of classical RDD.
Uzma Farooq +3 more
doaj +1 more source
Autoimmune Hepatitis: Histopathological Diversity and Its Clinical Implications
Hepatology Research, Volume 56, Issue 2, Page 139-147, February 2026.ABSTRACT Autoimmune hepatitis (AIH) is a chronic inflammatory liver disease characterized by diverse clinical and histological manifestations. Accurate histopathological evaluation plays a critical role in determining disease activity, guiding treatment strategies, and predicting prognosis.
Mina Komuta, Kenichi Harada
wiley +1 more source
Disseminated histiocytoses biomarkers beyond BRAFV600E: frequent expression of PD-L1. [PDF]
, 2015 The histiocytoses are rare tumors characterized by the primary accumulation and tissue infiltration of histiocytes and dendritic cells. Identification of the activating BRAFV600E mutation in Erdheim-Chester disease (ECD) and Langerhans cell histiocytosis
Arceci, Robert J +8 more
core +3 more sources
Diagnosis of Rosai-Dorfman Disease by Fine Needle Aspiration Cytology in a Case with Cervical Lymphadenopathy and Nasal Mass [PDF]
, 2011 We report a case of Rosai-Dorfman Disease, a rare non neoplastic proliferative disorder of the cells of macrophage-histiocyte family, in a case with cervical lymphadenopathy and nasal mass diagnosed by fine needle aspiration ...
Jena, M
core +1 more source
Rare Presentation of Rosai-Dorfman Disease in Soft Tissue: Diagnostic Findings and Surgical Treatment. [PDF]
, 2022 Introduction and Importance. Rosai-Dorfman disease (RDD) is a rare, benign type II histiocytosis characterized by the infiltration of S100+ histiocytes and emperipolesis.
Betini, N. +5 more
core +1 more source
Cancer Cytopathology, Volume 134, Issue 1, January 2026.Abstract The objective of the recently published World Health Organization Reporting System for Lymph Node, Spleen, and Thymus Cytopathology (WHO system) is to standardize the diagnostic approach to fine‐needle aspiration biopsies of hematolymphoid tissues.
Mats Ehinger +4 more
wiley +1 more source
Secondary adrenal insufficiency after treatment with budesonide for autoimmune hepatitis [PDF]
, 2018 Autoimmune hepatitis (AIH) is a rare cause of chronic liver disease. The backbone of treatment is immunosuppressive medication, typically prednisolone as induction therapy and azathioprine as a maintenance therapy.
De Maeyer, Filip +5 more
core +2 more sources