Results 41 to 50 of about 4,926,805 (180)

Prognostic factors of Erdheim–Chester disease: a nationwide survey in Japan

Haematologica, 2018
Erdheim–Chester disease is a rare histiocytosis with insufficient clinical data. To clarify the clinical features and prognostic factors of Erdheim–Chester disease, we conducted a nationwide survey to collect the detailed data of 44 patients with Erdheim–
Takashi Toya, Mizuki Ogura, Kazuhiro Toyama, Akihide Yoshimi, Aya Shinozaki-Ushiku, Akira Honda, Kenjiro Honda, Noriko Hosoya, Yukako Murakami, Hiroyuki Kawashima, Yasuhito Nannya, Shunya Arai, Fumihiko Nakamura, Yusuke Shinoda, Masaomi Nangaku, Kiyoshi Miyagawa, Masashi Fukayama, Akiko Moriya-Saito, Ichiro Katayama, Takashi Ogura, Mineo Kurokawa   +20 more
doaj   +1 more source

Solving a Mystery . . . 8 Years Later

Journal of Investigative Medicine High Impact Case Reports, 2018
Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis with multisystem involvement and insidious symptoms. In this article, we describe an interesting case of Erdheim-Chester disease that was eventually diagnosed 8 years after symptoms ...
Hayan Jouni MD, Ronald S. Kuzo MD, Nandan S. Anavekar MBBCh   +2 more
doaj   +1 more source

Role of 18F-FDG PET/CT in Erdheim–Chester Disease in the Era of Multimodality Imaging

Indian Journal of Radiology and Imaging, 2021
Erdheim–Chester disease is a rare disease with systemic non-Langerhans cell histiocytosis, the diagnosis of which with conventional imaging modalities is challenging.
Bhargavi Jois, Rupa Ananthasivan, Parameswaran R. V. Sudarshan Rawat, Susmita Rakshit   +3 more
doaj   +1 more source

A case report of Erdheim-Chester disease—clinically characterized by recurrent fever, multiple bone destruction, and antinuclear antibodies

Heliyon, 2023
Background: Erdheim-Chester disease is a form of histiocytosis. It is an extremely rare illness. Since its discovery, hundreds of cases of this disease have been identified across the globe. Pathologically, the condition is characterized by proliferation
Zhong-en Gao, Jing-jing Li, Kang Sheng, Rui Liu, Feng Fan, La-mei Zhou, Hao Zhang, Dong-lin Hao   +7 more
doaj   +1 more source

Choroidal mass as the first presentation of Erdheim-Chester disease

American Journal of Ophthalmology Case Reports, 2019
Purpose: To describe a choroidal mass that proved to be histiocytic choroidal infiltration in Erdheim-Chester disease. Observations: A 54-years-old Caucasian male presented to our Retina Clinic with a suspect of choroidal melanoma in the left eye ...
Francesco Pichi
doaj   +1 more source

An unusual thoracic localizations of Erdheim- Chester disease: A case report

Respiratory Medicine Case Reports, 2017
Erdheim- Chester disease is a rare non- Langerhans cell histiocytosis that usually involves the bones, heart, central nervous system, retroperitoneum, eyes, kidneys, skin and adrenals.
C. Massaccesi, S. Colella, F. Fioretti, V. D'Emilio, G. Panella, G. Primomo, F. Barbisan, R. Pela, V. Poletti   +8 more
doaj   +1 more source

An unusual Erdheim-Chester disease with orbital involvement: a case report

Italian Journal of Medicine, 2016
Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis with multiorgan involvement and a specific tropism for perivascular and fatty connective tissue, of unclear origin, with poor response to therapy. Its identification is difficult because
Giuseppe Brunori, Aurelio Seidita, Lydia Giannitrapani, Antonietta Serruto, Francesco Bencivinni, Maurizio Soresi   +5 more
doaj   +1 more source

New Treatment Strategy and Future Research Direction for BRAF‐Mutated Cancer

Cancer Science, EarlyView.
Treatment with BRAF inhibitor plus MEK inhibitor is currently used in BRAF‐mutated various malignancies except colorectal cancer, and treatments with BRAF and/or MEK inhibitors and anti‐EGFR antibody are used in BRAF‐mutated colorectal cancer. Despite recent advances in BRAF‐targeted therapies, their efficacy is still limited.
Masanobu Takahashi, Sakura Hiraide Taniguchi, Yuya Yoshida   +2 more
wiley   +1 more source

Solitary Indeterminate Cell Histiocytosis Presenting as a Reddish Nodule on the Abdomen of a 4‐Year‐Old Boy: Clinicopathologic Correlation and Electron Microscopy Findings

Journal of Cutaneous Pathology, EarlyView.
ABSTRACT Indeterminate cell histiocytosis (ICH) is a clonal proliferative disorder of mononuclear phagocyte cells that shows features of both dendritic and histiocytic cells. Only around 100 cases of ICH were reported, and among them, only 24% of reported cases involve pediatric patients, with a mean age at diagnosis of 50 years.
Seung‐Soo Lee, Seok‐Jong Lee, Weon Ju Lee, Dae‐Lyong Ha   +3 more
wiley   +1 more source

Safety of Lowering the Platelet Transfusion Threshold Before Central Venous Catheterisation in Patients With Haematological Diseases

European Journal of Haematology, EarlyView.
ABSTRACT Introduction Central venous catheter (CVC) insertion is frequently required in patients with haematological diseases. Despite limited evidence, thrombocytopenia often prompts prophylactic platelet transfusion before catheterisation. Methods We conducted an observational before‐and‐after study including the first non‐tunnelled CVC insertion ...
Mathias Lazarevic Lindblad, Elin Pålsson, Vladimir Lazarevic, Leila Naddi, Ola Borgquist, Lars Nilsson, Maria Adrian, Björn P. Bark, Thomas Kander   +8 more
wiley   +1 more source